{"symbol":"ECHS1","synonyms":["SCEH","ECHS1D"],"name":"enoyl CoA hydratase, short chain, 1, mitochondrial","description":"The protein encoded by this gene functions in the second step of the mitochondrial fatty acid beta-oxidation pathway. It catalyzes the hydration of 2-trans-enoyl-coenzyme A (CoA) intermediates to L-3-hydroxyacyl-CoAs. The gene product is a member of the hydratase/isomerase superfamily. It localizes to the mitochondrial matrix. Transcript variants utilizing alternative transcription initiation sites have been described in the literature. [provided by RefSeq, Jul 2008]","ncbiEntrezGeneId":1892,"ncbiEntrezGeneUrl":"http://www.ncbi.nlm.nih.gov/gene/1892","proteins":[{"symbol":"ECHM_HUMAN","href":"/api/1.0/protein/ECHM_HUMAN"}],"hgncRootFamilies":[]}