{"symbol":"GATB","synonyms":["PET112","HSPC199","PET112L"],"name":"glutamyl-tRNA(Gln) amidotransferase, subunit B","description":"Contributes to glutaminyl-tRNA synthase (glutamine-hydrolyzing) activity. Involved in glutaminyl-tRNAGln biosynthesis via transamidation and mitochondrial translation. Located in mitochondrion. Part of glutamyl-tRNA(Gln) amidotransferase complex. Implicated in combined oxidative phosphorylation deficiency 41. [provided by Alliance of Genome Resources, Mar 2025]","ncbiEntrezGeneId":5188,"ncbiEntrezGeneUrl":"http://www.ncbi.nlm.nih.gov/gene/5188","proteins":[{"symbol":"GATB_HUMAN","href":"/api/1.0/protein/GATB_HUMAN"}],"hgncRootFamilies":[]}