Mitochondrial respiratory chain complex assembly factors Gene Family

HGNC Family ID 645

Genes

Symbol Name
ACAD9 acyl-CoA dehydrogenase family, member 9
ATPAF1 ATP synthase mitochondrial F1 complex assembly factor 1
ATPAF2 ATP synthase mitochondrial F1 complex assembly factor 2
BCS1L BC1 (ubiquinol-cytochrome c reductase) synthesis-like
COA1 cytochrome c oxidase assembly factor 1 homolog (S. cerevisiae)
COA3 cytochrome c oxidase assembly factor 3
COA4 cytochrome c oxidase assembly factor 4 homolog (S. cerevisiae)
COA5 cytochrome c oxidase assembly factor 5
COA6 cytochrome c oxidase assembly factor 6
COA7 cytochrome c oxidase assembly factor 7 (putative)
COX10 COX10 heme A:farnesyltransferase cytochrome c oxidase assembly factor
COX11 COX11 cytochrome c oxidase copper chaperone
COX14 COX14 cytochrome c oxidase assembly factor
COX15 cytochrome c oxidase assembly homolog 15 (yeast)
COX17 COX17 cytochrome c oxidase copper chaperone
COX18 COX18 cytochrome c oxidase assembly factor
COX19 COX19 cytochrome c oxidase assembly factor
COX20 COX20 cytochrome c oxidase assembly factor
ECSIT ECSIT signalling integrator
NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1
NDUFAF2 NADH dehydrogenase (ubiquinone) complex I, assembly factor 2
NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3
NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4
NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5
NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6
NDUFAF7 NADH dehydrogenase (ubiquinone) complex I, assembly factor 7
NUBPL nucleotide binding protein-like
SCO1 SCO1 cytochrome c oxidase assembly protein
SCO2 SCO2 cytochrome c oxidase assembly protein
SDHAF1 succinate dehydrogenase complex assembly factor 1
SDHAF2 succinate dehydrogenase complex assembly factor 2
SDHAF3 succinate dehydrogenase complex assembly factor 3
SDHAF4 succinate dehydrogenase complex assembly factor 4
SURF1 surfeit 1
TMEM126B transmembrane protein 126B
UQCC1 ubiquinol-cytochrome c reductase complex assembly factor 1
UQCC2 ubiquinol-cytochrome c reductase complex assembly factor 2
UQCC3 ubiquinol-cytochrome c reductase complex assembly factor 3