| HGNC Family ID | 100 |
| Symbol | Name |
|---|---|
| ATG7 | autophagy related 7 |
| MOCS3 | molybdenum cofactor synthesis 3 |
| NAE1 | NEDD8 activating enzyme E1 subunit 1 |
| SAE1 | SUMO1 activating enzyme subunit 1 |
| UBA1 | ubiquitin-like modifier activating enzyme 1 |
| UBA2 | ubiquitin-like modifier activating enzyme 2 |
| UBA3 | ubiquitin-like modifier activating enzyme 3 |
| UBA5 | ubiquitin-like modifier activating enzyme 5 |
| UBA6 | ubiquitin-like modifier activating enzyme 6 |
| UBA7 | ubiquitin-like modifier activating enzyme 7 |