| Symbol |
Name |
|
ACAD9
|
acyl-CoA dehydrogenase family, member 9
|
|
ACAT1
|
acetyl-CoA acetyltransferase 1
|
|
ACO2
|
aconitase 2, mitochondrial
|
|
ADHFE1
|
alcohol dehydrogenase, iron containing, 1
|
|
ARMC8
|
armadillo repeat containing 8
|
|
ATP5F1A
|
ATP synthase F1 subunit alpha
|
|
ATP5F1B
|
ATP synthase F1 subunit beta
|
|
ATP5F1C
|
ATP synthase F1 subunit gamma
|
|
ATP5F1D
|
ATP synthase F1 subunit delta
|
|
ATP5F1E
|
ATP synthase F1 subunit epsilon
|
|
ATP5MC1
|
ATP synthase membrane subunit c locus 1
|
|
ATP5MC2
|
ATP synthase membrane subunit c locus 2
|
|
ATP5MC3
|
ATP synthase membrane subunit c locus 3
|
|
ATP5ME
|
ATP synthase membrane subunit e
|
|
ATP5MF
|
ATP synthase membrane subunit f
|
|
ATP5MG
|
ATP synthase membrane subunit g
|
|
ATP5MJ
|
ATP synthase membrane subunit j
|
|
ATP5MK
|
ATP synthase membrane subunit k
|
|
ATP5PB
|
ATP synthase peripheral stalk-membrane subunit b
|
|
ATP5PD
|
ATP synthase peripheral stalk subunit d
|
|
ATP5PF
|
ATP synthase peripheral stalk subunit F6
|
|
ATP5PO
|
ATP synthase peripheral stalk subunit OSCP
|
|
BCS1L
|
BC1 (ubiquinol-cytochrome c reductase) synthesis-like
|
|
CMC1
|
C-x(9)-C motif containing 1
|
|
COA1
|
cytochrome c oxidase assembly factor 1 homolog (S. cerevisiae)
|
|
COA3
|
cytochrome c oxidase assembly factor 3
|
|
COA5
|
cytochrome c oxidase assembly factor 5
|
|
COQ10A
|
coenzyme Q10 homolog A (S. cerevisiae)
|
|
COQ10B
|
coenzyme Q10 homolog B (S. cerevisiae)
|
|
COX11
|
COX11 cytochrome c oxidase copper chaperone
|
|
COX14
|
COX14 cytochrome c oxidase assembly factor
|
|
COX15
|
cytochrome c oxidase assembly homolog 15 (yeast)
|
|
COX16
|
COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)
|
|
COX17
|
COX17 cytochrome c oxidase copper chaperone
|
|
COX18
|
COX18 cytochrome c oxidase assembly factor
|
|
COX19
|
COX19 cytochrome c oxidase assembly factor
|
|
COX20
|
COX20 cytochrome c oxidase assembly factor
|
|
COX4I1
|
cytochrome c oxidase subunit IV isoform 1
|
|
COX4I2
|
cytochrome c oxidase subunit IV isoform 2 (lung)
|
|
COX5A
|
cytochrome c oxidase subunit Va
|
|
COX5B
|
cytochrome c oxidase subunit Vb
|
|
COX6A1
|
cytochrome c oxidase subunit VIa polypeptide 1
|
|
COX6A2
|
cytochrome c oxidase subunit VIa polypeptide 2
|
|
COX6B1
|
cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous)
|
|
COX6B2
|
cytochrome c oxidase subunit VIb polypeptide 2 (testis)
|
|
COX6C
|
cytochrome c oxidase subunit VIc
|
|
COX7A1
|
cytochrome c oxidase subunit VIIa polypeptide 1 (muscle)
|
|
COX7A2
|
cytochrome c oxidase subunit VIIa polypeptide 2 (liver)
|
|
COX7A2L
|
cytochrome c oxidase subunit VIIa polypeptide 2 like
|
|
COX7B
|
cytochrome c oxidase subunit VIIb
|
|
COX7C
|
cytochrome c oxidase subunit VIIc
|
|
COX8A
|
cytochrome c oxidase subunit VIIIA (ubiquitous)
|
|
COX8C
|
cytochrome c oxidase subunit VIIIC
|
|
CS
|
citrate synthase
|
|
CSKMT
|
citrate synthase lysine methyltransferase
|
|
CYC1
|
cytochrome c-1
|
|
CYCS
|
cytochrome c, somatic
|
|
D2HGDH
|
D-2-hydroxyglutarate dehydrogenase
|
|
DLAT
|
dihydrolipoamide S-acetyltransferase
|
|
DLD
|
dihydrolipoamide dehydrogenase
|
|
DLST
|
dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
|
|
DMAC1
|
distal membrane arm assembly component 1
|
|
DMAC2
|
distal membrane arm assembly component 2
|
|
DMAC2L
|
distal membrane arm assembly component 2 like
|
|
ECSIT
|
ECSIT signalling integrator
|
|
ETFA
|
electron-transfer-flavoprotein, alpha polypeptide
|
|
ETFB
|
electron-transfer-flavoprotein, beta polypeptide
|
|
ETFDH
|
electron-transferring-flavoprotein dehydrogenase
|
|
FAHD1
|
fumarylacetoacetate hydrolase domain containing 1
|
|
FH
|
fumarate hydratase
|
|
FOXRED1
|
FAD-dependent oxidoreductase domain containing 1
|
|
FXN
|
frataxin
|
|
GID4
|
GID complex subunit 4
|
|
GID8
|
GID complex subunit 8
|
|
GLO1
|
glyoxalase I
|
|
GOT1
|
glutamic-oxaloacetic transaminase 1, soluble
|
|
GOT2
|
glutamic-oxaloacetic transaminase 2, mitochondrial
|
|
GPT
|
glutamic-pyruvate transaminase (alanine aminotransferase)
|
|
GSTZ1
|
glutathione S-transferase zeta 1
|
|
HAGH
|
hydroxyacylglutathione hydrolase
|
|
HCCS
|
holocytochrome c synthase
|
|
HIGD1A
|
HIG1 hypoxia inducible domain family, member 1A
|
|
HIGD1C
|
HIG1 hypoxia inducible domain family, member 1C
|
|
HIGD2A
|
HIG1 hypoxia inducible domain family, member 2A
|
|
HSCB
|
HscB mitochondrial iron-sulfur cluster co-chaperone
|
|
HSPA9
|
heat shock 70kDa protein 9 (mortalin)
|
|
IDH2
|
isocitrate dehydrogenase 2 (NADP+), mitochondrial
|
|
IDH3A
|
isocitrate dehydrogenase 3 (NAD+) alpha
|
|
IDH3B
|
isocitrate dehydrogenase 3 (NAD+) beta
|
|
IDH3G
|
isocitrate dehydrogenase 3 (NAD+) gamma
|
|
ISCA1
|
iron-sulfur cluster assembly 1
|
|
ISCA2
|
iron-sulfur cluster assembly 2
|
|
ISCU
|
iron-sulfur cluster assembly enzyme
|
|
L2HGDH
|
L-2-hydroxyglutarate dehydrogenase
|
|
LDHA
|
lactate dehydrogenase A
|
|
LDHAL6A
|
lactate dehydrogenase A-like 6A
|
|
LDHAL6B
|
lactate dehydrogenase A-like 6B
|
|
LDHB
|
lactate dehydrogenase B
|
|
LDHC
|
lactate dehydrogenase C
|
|
LETM1
|
leucine zipper-EF-hand containing transmembrane protein 1
|
|
LYRM2
|
LYR motif containing 2
|
|
LYRM4
|
LYR motif containing 4
|
|
LYRM7
|
LYR motif containing 7
|
|
MAEA
|
macrophage erythroblast attacher
|
|
MDH1
|
malate dehydrogenase 1, NAD (soluble)
|
|
MDH2
|
malate dehydrogenase 2, NAD (mitochondrial)
|
|
ME1
|
malic enzyme 1, NADP(+)-dependent, cytosolic
|
|
ME2
|
malic enzyme 2, NAD(+)-dependent, mitochondrial
|
|
ME3
|
malic enzyme 3, NADP(+)-dependent, mitochondrial
|
|
MKLN1
|
muskelin 1, intracellular mediator containing kelch motifs
|
|
MPC1
|
mitochondrial pyruvate carrier 1
|
|
MPC1L
|
mitochondrial pyruvate carrier 1-like
|
|
MPC2
|
mitochondrial pyruvate carrier 2
|
|
MRPS36
|
mitochondrial ribosomal protein S36
|
|
NDUFA1
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
|
|
NDUFA10
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
|
|
NDUFA11
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa
|
|
NDUFA12
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12
|
|
NDUFA13
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
|
|
NDUFA2
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
|
|
NDUFA3
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa
|
|
NDUFA4
|
NDUFA4, mitochondrial complex associated
|
|
NDUFA5
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5
|
|
NDUFA6
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa
|
|
NDUFA7
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDa
|
|
NDUFA8
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
|
|
NDUFA9
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
|
|
NDUFAB1
|
NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
|
|
NDUFAF1
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 1
|
|
NDUFAF2
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 2
|
|
NDUFAF3
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 3
|
|
NDUFAF4
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 4
|
|
NDUFAF5
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 5
|
|
NDUFAF6
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 6
|
|
NDUFAF7
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 7
|
|
NDUFAF8
|
NADH:ubiquinone oxidoreductase complex assembly factor 8
|
|
NDUFB1
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa
|
|
NDUFB10
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa
|
|
NDUFB11
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa
|
|
NDUFB2
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa
|
|
NDUFB3
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa
|
|
NDUFB4
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa
|
|
NDUFB5
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa
|
|
NDUFB6
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa
|
|
NDUFB7
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa
|
|
NDUFB8
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa
|
|
NDUFB9
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa
|
|
NDUFC1
|
NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa
|
|
NDUFC2
|
NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa
|
|
NDUFS1
|
NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
|
|
NDUFS2
|
NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
|
|
NDUFS3
|
NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
|
|
NDUFS4
|
NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
|
|
NDUFS5
|
NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)
|
|
NDUFS6
|
NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)
|
|
NDUFS7
|
NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
|
|
NDUFS8
|
NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
|
|
NDUFV1
|
NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa
|
|
NDUFV2
|
NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa
|
|
NDUFV3
|
NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa
|
|
NEK1
|
NIMA-related kinase 1
|
|
NFS1
|
NFS1 cysteine desulfurase
|
|
NNT
|
nicotinamide nucleotide transhydrogenase
|
|
NUBPL
|
nucleotide binding protein-like
|
|
OGDH
|
oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
|
|
OXA1L
|
oxidase (cytochrome c) assembly 1-like
|
|
PC
|
pyruvate carboxylase
|
|
PDHA1
|
pyruvate dehydrogenase (lipoamide) alpha 1
|
|
PDHA2
|
pyruvate dehydrogenase (lipoamide) alpha 2
|
|
PDHB
|
pyruvate dehydrogenase (lipoamide) beta
|
|
PDHX
|
pyruvate dehydrogenase complex, component X
|
|
PDK1
|
pyruvate dehydrogenase kinase, isozyme 1
|
|
PDK2
|
pyruvate dehydrogenase kinase, isozyme 2
|
|
PDK3
|
pyruvate dehydrogenase kinase, isozyme 3
|
|
PDK4
|
pyruvate dehydrogenase kinase, isozyme 4
|
|
PDP1
|
pyruvate dehyrogenase phosphatase catalytic subunit 1
|
|
PDP2
|
pyruvate dehyrogenase phosphatase catalytic subunit 2
|
|
PDPR
|
pyruvate dehydrogenase phosphatase regulatory subunit
|
|
PET100
|
PET100 homolog (S. cerevisiae)
|
|
PET117
|
PET117 homolog (S. cerevisiae)
|
|
PGAM5
|
phosphoglycerate mutase family member 5
|
|
PKLR
|
pyruvate kinase, liver and RBC
|
|
PKM
|
pyruvate kinase, muscle
|
|
PM20D1
|
peptidase M20 domain containing 1
|
|
PNKD
|
paroxysmal nonkinesigenic dyskinesia
|
|
PYURF
|
PIGY upstream reading frame
|
|
RAB5IF
|
RAB5 interacting factor
|
|
RANBP9
|
RAN binding protein 9
|
|
RMND5A
|
required for meiotic nuclear division 5 homolog A (S. cerevisiae)
|
|
RMND5B
|
required for meiotic nuclear division 5 homolog B (S. cerevisiae)
|
|
RPS27A
|
ribosomal protein S27a
|
|
SCO1
|
SCO1 cytochrome c oxidase assembly protein
|
|
SCO2
|
SCO2 cytochrome c oxidase assembly protein
|
|
SDHA
|
succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
|
|
SDHAF1
|
succinate dehydrogenase complex assembly factor 1
|
|
SDHAF2
|
succinate dehydrogenase complex assembly factor 2
|
|
SDHAF3
|
succinate dehydrogenase complex assembly factor 3
|
|
SDHAF4
|
succinate dehydrogenase complex assembly factor 4
|
|
SDHB
|
succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
|
|
SDHC
|
succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa
|
|
SDHD
|
succinate dehydrogenase complex, subunit D, integral membrane protein
|
|
SFXN4
|
sideroflexin 4
|
|
SIRT3
|
sirtuin 3
|
|
SIRT4
|
sirtuin 4
|
|
SLC25A11
|
solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11
|
|
SLC25A12
|
solute carrier family 25 (aspartate/glutamate carrier), member 12
|
|
SLC25A13
|
solute carrier family 25 (aspartate/glutamate carrier), member 13
|
|
SLC25A14
|
solute carrier family 25 (mitochondrial carrier, brain), member 14
|
|
SLC25A18
|
solute carrier family 25 (glutamate carrier), member 18
|
|
SLC25A22
|
solute carrier family 25 (mitochondrial carrier: glutamate), member 22
|
|
SLC25A27
|
solute carrier family 25, member 27
|
|
SLC25A4
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
|
|
SMIM20
|
small integral membrane protein 20
|
|
SUCLA2
|
succinate-CoA ligase, ADP-forming, beta subunit
|
|
SUCLG1
|
succinate-CoA ligase, alpha subunit
|
|
SUCLG2
|
succinate-CoA ligase, GDP-forming, beta subunit
|
|
SURF1
|
surfeit 1
|
|
TACO1
|
translational activator of mitochondrially encoded cytochrome c oxidase I
|
|
TIMM21
|
translocase of inner mitochondrial membrane 21 homolog (yeast)
|
|
TIMMDC1
|
translocase of inner mitochondrial membrane domain containing 1
|
|
TMEM126A
|
transmembrane protein 126A
|
|
TMEM126B
|
transmembrane protein 126B
|
|
TMEM177
|
transmembrane protein 177
|
|
TMEM186
|
transmembrane protein 186
|
|
TMEM223
|
transmembrane protein 223
|
|
TRAP1
|
TNF receptor-associated protein 1
|
|
TTC19
|
tetratricopeptide repeat domain 19
|
|
UBA52
|
ubiquitin A-52 residue ribosomal protein fusion product 1
|
|
UBB
|
ubiquitin B
|
|
UBC
|
ubiquitin C
|
|
UCP1
|
uncoupling protein 1 (mitochondrial, proton carrier)
|
|
UCP2
|
uncoupling protein 2 (mitochondrial, proton carrier)
|
|
UCP3
|
uncoupling protein 3 (mitochondrial, proton carrier)
|
|
UQCC1
|
ubiquinol-cytochrome c reductase complex assembly factor 1
|
|
UQCC2
|
ubiquinol-cytochrome c reductase complex assembly factor 2
|
|
UQCC3
|
ubiquinol-cytochrome c reductase complex assembly factor 3
|
|
UQCC5
|
ubiquinol-cytochrome c reductase complex assembly factor 5
|
|
UQCC6
|
ubiquinol-cytochrome c reductase complex assembly factor 6
|
|
UQCR10
|
ubiquinol-cytochrome c reductase, complex III subunit X
|
|
UQCR11
|
ubiquinol-cytochrome c reductase, complex III subunit XI
|
|
UQCRB
|
ubiquinol-cytochrome c reductase binding protein
|
|
UQCRC1
|
ubiquinol-cytochrome c reductase core protein I
|
|
UQCRC2
|
ubiquinol-cytochrome c reductase core protein II
|
|
UQCRFS1
|
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
|
|
UQCRH
|
ubiquinol-cytochrome c reductase hinge protein
|
|
UQCRQ
|
ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa
|
|
VDAC1
|
voltage-dependent anion channel 1
|
|
WDR26
|
WD repeat domain 26
|
