Branched-chain amino acid catabolism Gene Set

Dataset Reactome Pathways 2024
Category structural or functional annotations
Type pathway
External Link https://reactome.org/PathwayBrowser/#/R-HSA-70895
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Genes

21 proteins participating in the Branched-chain amino acid catabolism pathway from the Reactome Pathways 2024 dataset.

Symbol Name
ACAD8 acyl-CoA dehydrogenase family, member 8
ACADSB acyl-CoA dehydrogenase, short/branched chain
ACAT1 acetyl-CoA acetyltransferase 1
ALDH6A1 aldehyde dehydrogenase 6 family, member A1
AUH AU RNA binding protein/enoyl-CoA hydratase
BCAT1 branched chain amino-acid transaminase 1, cytosolic
BCAT2 branched chain amino-acid transaminase 2, mitochondrial
BCKDHA branched chain keto acid dehydrogenase E1, alpha polypeptide
BCKDHB branched chain keto acid dehydrogenase E1, beta polypeptide
BCKDK branched chain ketoacid dehydrogenase kinase
DBT dihydrolipoamide branched chain transacylase E2
DLD dihydrolipoamide dehydrogenase
ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial
HIBADH 3-hydroxyisobutyrate dehydrogenase
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10
IVD isovaleryl-CoA dehydrogenase
MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha)
MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta)
PPM1K protein phosphatase, Mg2+/Mn2+ dependent, 1K
SLC25A44 solute carrier family 25, member 44