Glycosphingolipid metabolism Gene Set

Dataset Reactome Pathways 2024
Category structural or functional annotations
Type pathway
External Link https://reactome.org/PathwayBrowser/#/R-HSA-1660662
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Genes

58 proteins participating in the Glycosphingolipid metabolism pathway from the Reactome Pathways 2024 dataset.

Symbol Name
A4GALT alpha 1,4-galactosyltransferase
ARSA arylsulfatase A
ARSB arylsulfatase B
ARSD arylsulfatase D
ARSF arylsulfatase F
ARSG arylsulfatase G
ARSH arylsulfatase family, member H
ARSI arylsulfatase family, member I
ARSJ arylsulfatase family, member J
ARSK arylsulfatase family, member K
ARSL arylsulfatase L
ASAH1 N-acylsphingosine amidohydrolase (acid ceramidase) 1
ASAH2 N-acylsphingosine amidohydrolase (non-lysosomal ceramidase) 2
B3GALNT1 beta-1,3-N-acetylgalactosaminyltransferase 1 (globoside blood group)
B3GALT4 UDP-Gal:betaGlcNAc beta 1,3-galactosyltransferase, polypeptide 4
B3GNT5 UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 5
B4GALNT1 beta-1,4-N-acetyl-galactosaminyl transferase 1
B4GALT5 UDP-Gal:betaGlcNAc beta 1,4- galactosyltransferase, polypeptide 5
B4GALT6 UDP-Gal:betaGlcNAc beta 1,4- galactosyltransferase, polypeptide 6
CERK ceramide kinase
CTSA cathepsin A
ENPP7 ectonucleotide pyrophosphatase/phosphodiesterase 7
FUT1 fucosyltransferase 1 (galactoside 2-alpha-L-fucosyltransferase, H blood group)
FUT2 fucosyltransferase 2 (secretor status included)
GAL3ST1 galactose-3-O-sulfotransferase 1
GALC galactosylceramidase
GBA1 glucosylceramidase beta 1
GBA2 glucosidase, beta (bile acid) 2
GBA3 glucosidase, beta, acid 3 (gene/pseudogene)
GLA galactosidase, alpha
GLB1 galactosidase, beta 1
GLB1L galactosidase, beta 1-like
GLB1L2 galactosidase, beta 1-like 2
GLB1L3 galactosidase, beta 1-like 3
GM2A GM2 ganglioside activator
HEXA hexosaminidase A (alpha polypeptide)
HEXB hexosaminidase B (beta polypeptide)
M6PR mannose-6-phosphate receptor (cation dependent)
NEU1 sialidase 1 (lysosomal sialidase)
NEU2 sialidase 2 (cytosolic sialidase)
NEU3 sialidase 3 (membrane sialidase)
NEU4 sialidase 4
PSAP prosaposin
SMPD1 sphingomyelin phosphodiesterase 1, acid lysosomal
SMPD2 sphingomyelin phosphodiesterase 2, neutral membrane (neutral sphingomyelinase)
SMPD3 sphingomyelin phosphodiesterase 3, neutral membrane (neutral sphingomyelinase II)
SMPD4 sphingomyelin phosphodiesterase 4, neutral membrane (neutral sphingomyelinase-3)
ST3GAL2 ST3 beta-galactoside alpha-2,3-sialyltransferase 2
ST3GAL3 ST3 beta-galactoside alpha-2,3-sialyltransferase 3
ST3GAL5 ST3 beta-galactoside alpha-2,3-sialyltransferase 5
ST6GALNAC5 ST6 (alpha-N-acetyl-neuraminyl-2,3-beta-galactosyl-1,3)-N-acetylgalactosaminide alpha-2,6-sialyltransferase 5
ST6GALNAC6 ST6 (alpha-N-acetyl-neuraminyl-2,3-beta-galactosyl-1,3)-N-acetylgalactosaminide alpha-2,6-sialyltransferase 6
ST8SIA5 ST8 alpha-N-acetyl-neuraminide alpha-2,8-sialyltransferase 5
STS steroid sulfatase (microsomal), isozyme S
SUMF1 sulfatase modifying factor 1
SUMF2 sulfatase modifying factor 2
UGCG UDP-glucose ceramide glucosyltransferase
UGT8 UDP glycosyltransferase 8