LETM1 Gene Set

Dataset Pathway Commons Protein-Protein Interactions
Category physical interactions
Type interacting protein
Description leucine zipper-EF-hand containing transmembrane protein 1|This gene encodes a protein that is localized to the inner mitochondrial membrane. The protein functions to maintain the mitochondrial tubular shapes and is required for normal mitochondrial morphology and cellular viability. Mutations in this gene cause Wolf-Hirschhorn syndrome, a complex malformation syndrome caused by the deletion of parts of the distal short arm of chromosome 4. Related pseudogenes have been identified on chromosomes 8, 15 and 19. [provided by RefSeq, Oct 2009] (NCBI Entrez Gene Database, 3954)
External Link http://www.ncbi.nlm.nih.gov/gene/3954
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Genes

752 interacting proteins for LETM1 from the Pathway Commons Protein-Protein Interactions dataset.

Symbol Name
AARS2 alanyl-tRNA synthetase 2, mitochondrial
AASS aminoadipate-semialdehyde synthase
ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7
ABHD12 abhydrolase domain containing 12
ACAD9 acyl-CoA dehydrogenase family, member 9
ACADVL acyl-CoA dehydrogenase, very long chain
ACOT8 acyl-CoA thioesterase 8
ACOT9 acyl-CoA thioesterase 9
ACSL1 acyl-CoA synthetase long-chain family member 1
ACSL3 acyl-CoA synthetase long-chain family member 3
ACSL4 acyl-CoA synthetase long-chain family member 4
ACTB actin, beta
ADCK3 aarF domain containing kinase 3
ADRM1 adhesion regulating molecule 1
AFG3L2 AFG3-like AAA ATPase 2
AGK acylglycerol kinase
AGO2 argonaute RISC catalytic component 2
AGPAT6 1-acylglycerol-3-phosphate O-acyltransferase 6
AGPS alkylglycerone phosphate synthase
AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1
AKAP8L A kinase (PRKA) anchor protein 8-like
ALDH18A1 aldehyde dehydrogenase 18 family, member A1
ALDH1B1 aldehyde dehydrogenase 1 family, member B1
ALDH1L2 aldehyde dehydrogenase 1 family, member L2
ALDH2 aldehyde dehydrogenase 2 family (mitochondrial)
ALDH3A2 aldehyde dehydrogenase 3 family, member A2
ALG1 ALG1, chitobiosyldiphosphodolichol beta-mannosyltransferase
ALYREF Aly/REF export factor
AMOTL1 angiomotin like 1
ANAPC1 anaphase promoting complex subunit 1
ANAPC5 anaphase promoting complex subunit 5
AP1G1 adaptor-related protein complex 1, gamma 1 subunit
AP2M1 adaptor-related protein complex 2, mu 1 subunit
APMAP adipocyte plasma membrane associated protein
ARCN1 archain 1
ARFGEF1 ADP-ribosylation factor guanine nucleotide-exchange factor 1 (brefeldin A-inhibited)
ARFGEF2 ADP-ribosylation factor guanine nucleotide-exchange factor 2 (brefeldin A-inhibited)
ARL8A ADP-ribosylation factor-like 8A
ARL8B ADP-ribosylation factor-like 8B
ASPH aspartate beta-hydroxylase
ATAD3A ATPase family, AAA domain containing 3A
ATAD3B ATPase family, AAA domain containing 3B
ATG9A autophagy related 9A
ATP1A1 ATPase, Na+/K+ transporting, alpha 1 polypeptide
ATP1B3 ATPase, Na+/K+ transporting, beta 3 polypeptide
ATP2A2 ATPase, Ca++ transporting, cardiac muscle, slow twitch 2
ATP2B4 ATPase, Ca++ transporting, plasma membrane 4
ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle
ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide
ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1
ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit
ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1
ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d
ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6
ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2
ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G
ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit
ATR ATR serine/threonine kinase
ATXN10 ataxin 10
ATXN2L ataxin 2-like
AUP1 ancient ubiquitous protein 1
AURKB aurora kinase B
AZI2 5-azacytidine induced 2
B3GNT1
BAG2 BCL2-associated athanogene 2
BAX BCL2-associated X protein
BCAP31 B-cell receptor-associated protein 31
BCS1L BC1 (ubiquinol-cytochrome c reductase) synthesis-like
BSG basigin (Ok blood group)
BZW1 basic leucine zipper and W2 domains 1
C10ORF2 chromosome 10 open reading frame 2
C12ORF57 chromosome 12 open reading frame 57
C19ORF70 chromosome 19 open reading frame 70
C1QBP complement component 1, q subcomponent binding protein
C2ORF47 chromosome 2 open reading frame 47
C3 complement component 3
C6ORF203 chromosome 6 open reading frame 203
CAD carbamoyl-phosphate synthetase 2, aspartate transcarbamylase, and dihydroorotase
CALCOCO2 calcium binding and coiled-coil domain 2
CALM1 calmodulin 1 (phosphorylase kinase, delta)
CANX calnexin
CAPRIN1 cell cycle associated protein 1
CBWD6 COBW domain containing 6
CCDC124 coiled-coil domain containing 124
CCDC47 coiled-coil domain containing 47
CCDC85C coiled-coil domain containing 85C
CCNC cyclin C
CCT2 chaperonin containing TCP1, subunit 2 (beta)
CCT3 chaperonin containing TCP1, subunit 3 (gamma)
CCT4 chaperonin containing TCP1, subunit 4 (delta)
CCT5 chaperonin containing TCP1, subunit 5 (epsilon)
CCT6A chaperonin containing TCP1, subunit 6A (zeta 1)
CCT7 chaperonin containing TCP1, subunit 7 (eta)
CDC42BPG CDC42 binding protein kinase gamma (DMPK-like)
CDC42EP1 CDC42 effector protein (Rho GTPase binding) 1
CDIPT CDP-diacylglycerol--inositol 3-phosphatidyltransferase
CDK19 cyclin-dependent kinase 19
CECR5 cat eye syndrome chromosome region, candidate 5
CEPT1 choline/ethanolamine phosphotransferase 1
CERS1 ceramide synthase 1
CFL1 cofilin 1 (non-muscle)
CHCHD1 coiled-coil-helix-coiled-coil-helix domain containing 1
CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3
CHCHD6 coiled-coil-helix-coiled-coil-helix domain containing 6
CHD4 chromodomain helicase DNA binding protein 4
CHP1 calcineurin-like EF-hand protein 1
CLCC1 chloride channel CLIC-like 1
CLN6 ceroid-lipofuscinosis, neuronal 6, late infantile, variant
CLPB ClpB homolog, mitochondrial AAA ATPase chaperonin
CLPP caseinolytic mitochondrial matrix peptidase proteolytic subunit
CLPTM1 cleft lip and palate associated transmembrane protein 1
CLPX caseinolytic mitochondrial matrix peptidase chaperone subunit
CLTA clathrin, light chain A
COMT catechol-O-methyltransferase
COPA coatomer protein complex, subunit alpha
COPB1 coatomer protein complex, subunit beta 1
COPB2 coatomer protein complex, subunit beta 2 (beta prime)
COPG2 coatomer protein complex, subunit gamma 2
COX17 COX17 cytochrome c oxidase copper chaperone
COX4I1 cytochrome c oxidase subunit IV isoform 1
COX5A cytochrome c oxidase subunit Va
COX6C cytochrome c oxidase subunit VIc
CPT2 carnitine palmitoyltransferase 2
CPVL carboxypeptidase, vitellogenic-like
CSE1L CSE1 chromosome segregation 1-like (yeast)
CSTF1 cleavage stimulation factor, 3' pre-RNA, subunit 1, 50kDa
CUL7 cullin 7
CYB5B cytochrome b5 type B (outer mitochondrial membrane)
CYB5R3 cytochrome b5 reductase 3
CYP51A1 cytochrome P450, family 51, subfamily A, polypeptide 1
DAD1 defender against cell death 1
DAP3 death associated protein 3
DARS aspartyl-tRNA synthetase
DBT dihydrolipoamide branched chain transacylase E2
DCAF7 DDB1 and CUL4 associated factor 7
DDB1 damage-specific DNA binding protein 1, 127kDa
DDOST dolichyl-diphosphooligosaccharide--protein glycosyltransferase subunit (non-catalytic)
DDX20 DEAD (Asp-Glu-Ala-Asp) box polypeptide 20
DDX28 DEAD (Asp-Glu-Ala-Asp) box polypeptide 28
DDX6 DEAD (Asp-Glu-Ala-Asp) box helicase 6
DHCR7 7-dehydrocholesterol reductase
DHRS7 dehydrogenase/reductase (SDR family) member 7
DHRS7B dehydrogenase/reductase (SDR family) member 7B
DHX30 DEAH (Asp-Glu-Ala-His) box helicase 30
DLD dihydrolipoamide dehydrogenase
DNAJA1 DnaJ (Hsp40) homolog, subfamily A, member 1
DNAJA2 DnaJ (Hsp40) homolog, subfamily A, member 2
DNAJA3 DnaJ (Hsp40) homolog, subfamily A, member 3
DNAJA4 DnaJ (Hsp40) homolog, subfamily A, member 4
DNAJB1 DnaJ (Hsp40) homolog, subfamily B, member 1
DNAJB11 DnaJ (Hsp40) homolog, subfamily B, member 11
DNAJB12 DnaJ (Hsp40) homolog, subfamily B, member 12
DNAJC11 DnaJ (Hsp40) homolog, subfamily C, member 11
DNAJC7 DnaJ (Hsp40) homolog, subfamily C, member 7
DPM1 dolichyl-phosphate mannosyltransferase polypeptide 1, catalytic subunit
DYNC1H1 dynein, cytoplasmic 1, heavy chain 1
DYNC1I2 dynein, cytoplasmic 1, intermediate chain 2
DYNC1LI1 dynein, cytoplasmic 1, light intermediate chain 1
DYNC1LI2 dynein, cytoplasmic 1, light intermediate chain 2
ECH1 enoyl CoA hydratase 1, peroxisomal
ECI1 enoyl-CoA delta isomerase 1
EEF1B2 eukaryotic translation elongation factor 1 beta 2
EEF1G eukaryotic translation elongation factor 1 gamma
EEF2 eukaryotic translation elongation factor 2
EIF2S1 eukaryotic translation initiation factor 2, subunit 1 alpha, 35kDa
EIF3B eukaryotic translation initiation factor 3, subunit B
EIF3H eukaryotic translation initiation factor 3, subunit H
EIF3I eukaryotic translation initiation factor 3, subunit I
EIF4A1 eukaryotic translation initiation factor 4A1
EMD emerin
EPHX1 epoxide hydrolase 1, microsomal (xenobiotic)
EPRS glutamyl-prolyl-tRNA synthetase
ERAL1 Era-like 12S mitochondrial rRNA chaperone 1
ERLIN2 ER lipid raft associated 2
ERP44 endoplasmic reticulum protein 44
ESYT1 extended synaptotagmin-like protein 1
ESYT2 extended synaptotagmin-like protein 2
ETFA electron-transfer-flavoprotein, alpha polypeptide
FAF2 Fas associated factor family member 2
FAM162A family with sequence similarity 162, member A
FAM186B family with sequence similarity 186, member B
FANCD2 Fanconi anemia, complementation group D2
FANCI Fanconi anemia, complementation group I
FAR1 fatty acyl CoA reductase 1
FARS2 phenylalanyl-tRNA synthetase 2, mitochondrial
FASTKD1 FAST kinase domains 1
FASTKD2 FAST kinase domains 2
FBXL16 F-box and leucine-rich repeat protein 16
FDFT1 farnesyl-diphosphate farnesyltransferase 1
FKBP8 FK506 binding protein 8, 38kDa
FLAD1 flavin adenine dinucleotide synthetase 1
FMR1 fragile X mental retardation 1
FOXK1 forkhead box K1
FOXK2 forkhead box K2
FXR2 fragile X mental retardation, autosomal homolog 2
GADD45GIP1 growth arrest and DNA-damage-inducible, gamma interacting protein 1
GANAB glucosidase, alpha; neutral AB
GATAD2A GATA zinc finger domain containing 2A
GCDH glutaryl-CoA dehydrogenase
GCN1L1 GCN1 general control of amino-acid synthesis 1-like 1 (yeast)
GDPD1 glycerophosphodiester phosphodiesterase domain containing 1
GID8 GID complex subunit 8
GIGYF1 GRB10 interacting GYF protein 1
GLDC glycine dehydrogenase (decarboxylating)
GLUD1 glutamate dehydrogenase 1
GNB3 guanine nucleotide binding protein (G protein), beta polypeptide 3
GNPAT glyceronephosphate O-acyltransferase
GOLGA2 golgin A2
GRPEL1 GrpE-like 1, mitochondrial (E. coli)
GRSF1 G-rich RNA sequence binding factor 1
GTF3C1 general transcription factor IIIC, polypeptide 1, alpha 220kDa
GTF3C3 general transcription factor IIIC, polypeptide 3, 102kDa
GTF3C5 general transcription factor IIIC, polypeptide 5, 63kDa
GTF3C6 general transcription factor IIIC, polypeptide 6, alpha 35kDa
GTPBP10 GTP-binding protein 10 (putative)
HACD3 3-hydroxyacyl-CoA dehydratase 3
HADHA hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit
HADHB hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit
HARS2 histidyl-tRNA synthetase 2, mitochondrial
HAX1 HCLS1 associated protein X-1
HEATR1 HEAT repeat containing 1
HECTD1 HECT domain containing E3 ubiquitin protein ligase 1
HIGD1A HIG1 hypoxia inducible domain family, member 1A
HK1 hexokinase 1
HLA-C major histocompatibility complex, class I, C
HM13 histocompatibility (minor) 13
HMMR hyaluronan-mediated motility receptor (RHAMM)
HNRNPD heterogeneous nuclear ribonucleoprotein D (AU-rich element RNA binding protein 1, 37kDa)
HNRNPDL heterogeneous nuclear ribonucleoprotein D-like
HNRNPF heterogeneous nuclear ribonucleoprotein F
HNRNPH1 heterogeneous nuclear ribonucleoprotein H1 (H)
HNRNPK heterogeneous nuclear ribonucleoprotein K
HNRNPM heterogeneous nuclear ribonucleoprotein M
HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10
HSD17B12 hydroxysteroid (17-beta) dehydrogenase 12
HSP90AA1 heat shock protein 90kDa alpha (cytosolic), class A member 1
HSP90AB1 heat shock protein 90kDa alpha (cytosolic), class B member 1
HSPA1B heat shock 70kDa protein 1B
HSPA4 heat shock 70kDa protein 4
HSPA4L heat shock 70kDa protein 4-like
HSPA6 heat shock 70kDa protein 6 (HSP70B')
HSPA8 heat shock 70kDa protein 8
HSPA9 heat shock 70kDa protein 9 (mortalin)
HSPBP1 HSPA (heat shock 70kDa) binding protein, cytoplasmic cochaperone 1
HSPD1 heat shock 60kDa protein 1 (chaperonin)
HSPH1 heat shock 105kDa/110kDa protein 1
HUWE1 HECT, UBA and WWE domain containing 1, E3 ubiquitin protein ligase
HYOU1 hypoxia up-regulated 1
IARS isoleucyl-tRNA synthetase
ICT1 immature colon carcinoma transcript 1
IFIH1 interferon induced with helicase C domain 1
IGF2BP2 insulin-like growth factor 2 mRNA binding protein 2
IKBKE inhibitor of kappa light polypeptide gene enhancer in B-cells, kinase epsilon
ILF3 interleukin enhancer binding factor 3, 90kDa
IMMT inner membrane protein, mitochondrial
IMPDH2 IMP (inosine 5'-monophosphate) dehydrogenase 2
INADL InaD-like (Drosophila)
IPO7 importin 7
IPO8 importin 8
IRAK1 interleukin-1 receptor-associated kinase 1
IRF3 interferon regulatory factor 3
IRS4 insulin receptor substrate 4
ISCA1 iron-sulfur cluster assembly 1
KARS lysyl-tRNA synthetase
KDELR2 KDEL (Lys-Asp-Glu-Leu) endoplasmic reticulum protein retention receptor 2
KIAA0368 KIAA0368
KIAA0391 KIAA0391
KIAA1524 KIAA1524
KLHDC2 kelch domain containing 2
KPNA2 karyopherin alpha 2 (RAG cohort 1, importin alpha 1)
KPNB1 karyopherin (importin) beta 1
KRTCAP2 keratinocyte associated protein 2
LAGE3 L antigen family, member 3
LAMP1 lysosomal-associated membrane protein 1
LARS leucyl-tRNA synthetase
LATS2 large tumor suppressor kinase 2
LMAN1 lectin, mannose-binding, 1
LMAN2 lectin, mannose-binding 2
LMBR1 limb development membrane protein 1
LNX2 ligand of numb-protein X 2
LONP1 lon peptidase 1, mitochondrial
LPCAT1 lysophosphatidylcholine acyltransferase 1
LRPPRC leucine-rich pentatricopeptide repeat containing
LRRC59 leucine rich repeat containing 59
LYPLAL1 lysophospholipase-like 1
LZTR1 leucine-zipper-like transcription regulator 1
M6PR mannose-6-phosphate receptor (cation dependent)
MAD2L1 MAD2 mitotic arrest deficient-like 1 (yeast)
MAGED1 melanoma antigen family D1
MAGED2 melanoma antigen family D2
MALSU1 mitochondrial assembly of ribosomal large subunit 1
MARS methionyl-tRNA synthetase
MAT2A methionine adenosyltransferase II, alpha
MAVS mitochondrial antiviral signaling protein
MBD3 methyl-CpG binding domain protein 3
MCAT malonyl CoA:ACP acyltransferase (mitochondrial)
MCC mutated in colorectal cancers
MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta)
MCU mitochondrial calcium uniporter
MDN1 MDN1, midasin homolog (yeast)
ME2 malic enzyme 2, NAD(+)-dependent, mitochondrial
MED12 mediator complex subunit 12
MED13 mediator complex subunit 13
MED13L mediator complex subunit 13-like
MED14 mediator complex subunit 14
MED15 mediator complex subunit 15
MED16 mediator complex subunit 16
MED17 mediator complex subunit 17
MED20 mediator complex subunit 20
MED23 mediator complex subunit 23
MED24 mediator complex subunit 24
MED25 mediator complex subunit 25
MED26 mediator complex subunit 26
MED27 mediator complex subunit 27
MED29 mediator complex subunit 29
MED4 mediator complex subunit 4
MED8 mediator complex subunit 8
MED9 mediator complex subunit 9
METTL17 methyltransferase like 17
MGME1 mitochondrial genome maintenance exonuclease 1
MIB1 mindbomb E3 ubiquitin protein ligase 1
MLF2 myeloid leukemia factor 2
MLLT11 myeloid/lymphoid or mixed-lineage leukemia (trithorax homolog, Drosophila); translocated to, 11
MLLT4 myeloid/lymphoid or mixed-lineage leukemia (trithorax homolog, Drosophila); translocated to, 4
MMAB methylmalonic aciduria (cobalamin deficiency) cblB type
MMS19 MMS19 nucleotide excision repair homolog (S. cerevisiae)
MOB1A MOB kinase activator 1A
MOGS mannosyl-oligosaccharide glucosidase
MON2 MON2 homolog (S. cerevisiae)
MOV10 Mov10 RISC complex RNA helicase
MPDZ multiple PDZ domain protein
MPP5 membrane protein, palmitoylated 5 (MAGUK p55 subfamily member 5)
MRM1 mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae)
MRPL1 mitochondrial ribosomal protein L1
MRPL10 mitochondrial ribosomal protein L10
MRPL11 mitochondrial ribosomal protein L11
MRPL12 mitochondrial ribosomal protein L12
MRPL13 mitochondrial ribosomal protein L13
MRPL14 mitochondrial ribosomal protein L14
MRPL15 mitochondrial ribosomal protein L15
MRPL16 mitochondrial ribosomal protein L16
MRPL17 mitochondrial ribosomal protein L17
MRPL18 mitochondrial ribosomal protein L18
MRPL19 mitochondrial ribosomal protein L19
MRPL2 mitochondrial ribosomal protein L2
MRPL20 mitochondrial ribosomal protein L20
MRPL21 mitochondrial ribosomal protein L21
MRPL22 mitochondrial ribosomal protein L22
MRPL24 mitochondrial ribosomal protein L24
MRPL27 mitochondrial ribosomal protein L27
MRPL28 mitochondrial ribosomal protein L28
MRPL3 mitochondrial ribosomal protein L3
MRPL32 mitochondrial ribosomal protein L32
MRPL37 mitochondrial ribosomal protein L37
MRPL39 mitochondrial ribosomal protein L39
MRPL4 mitochondrial ribosomal protein L4
MRPL40 mitochondrial ribosomal protein L40
MRPL41 mitochondrial ribosomal protein L41
MRPL43 mitochondrial ribosomal protein L43
MRPL44 mitochondrial ribosomal protein L44
MRPL46 mitochondrial ribosomal protein L46
MRPL47 mitochondrial ribosomal protein L47
MRPL48 mitochondrial ribosomal protein L48
MRPL49 mitochondrial ribosomal protein L49
MRPL50 mitochondrial ribosomal protein L50
MRPL51 mitochondrial ribosomal protein L51
MRPL54 mitochondrial ribosomal protein L54
MRPL55 mitochondrial ribosomal protein L55
MRPL9 mitochondrial ribosomal protein L9
MRPS10 mitochondrial ribosomal protein S10
MRPS11 mitochondrial ribosomal protein S11
MRPS14 mitochondrial ribosomal protein S14
MRPS15 mitochondrial ribosomal protein S15
MRPS16 mitochondrial ribosomal protein S16
MRPS17 mitochondrial ribosomal protein S17
MRPS18A mitochondrial ribosomal protein S18A
MRPS18B mitochondrial ribosomal protein S18B
MRPS2 mitochondrial ribosomal protein S2
MRPS21 mitochondrial ribosomal protein S21
MRPS22 mitochondrial ribosomal protein S22
MRPS23 mitochondrial ribosomal protein S23
MRPS24 mitochondrial ribosomal protein S24
MRPS25 mitochondrial ribosomal protein S25
MRPS26 mitochondrial ribosomal protein S26
MRPS27 mitochondrial ribosomal protein S27
MRPS28 mitochondrial ribosomal protein S28
MRPS30 mitochondrial ribosomal protein S30
MRPS31 mitochondrial ribosomal protein S31
MRPS34 mitochondrial ribosomal protein S34
MRPS35 mitochondrial ribosomal protein S35
MRPS5 mitochondrial ribosomal protein S5
MRPS6 mitochondrial ribosomal protein S6
MRPS7 mitochondrial ribosomal protein S7
MRPS9 mitochondrial ribosomal protein S9
MRRF mitochondrial ribosome recycling factor
MTA1 metastasis associated 1
MTA2 metastasis associated 1 family, member 2
MTDH metadherin
MTG1 mitochondrial ribosome-associated GTPase 1
MTHFD2 methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase
MTIF2 mitochondrial translational initiation factor 2
MTPAP mitochondrial poly(A) polymerase
MTX1 metaxin 1
MUT methylmalonyl CoA mutase
NAP1L1 nucleosome assembly protein 1-like 1
NCLN nicalin
NDUFA13 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
NDUFA4 NDUFA4, mitochondrial complex associated
NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5
NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3
NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4
NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa
NGRN neugrin, neurite outgrowth associated
NIPSNAP1 nipsnap homolog 1 (C. elegans)
NLRX1 NLR family member X1
NME4 NME/NM23 nucleoside diphosphate kinase 4
NOA1 nitric oxide associated 1
NOMO1 NODAL modulator 1
NOMO3 NODAL modulator 3
NOP58 NOP58 ribonucleoprotein
NRF1 nuclear respiratory factor 1
NSDHL NAD(P) dependent steroid dehydrogenase-like
NSUN4 NOP2/Sun domain family, member 4
NUCLEOLIN nucleolin multifunctional protein
NUP205 nucleoporin 205kDa
NUP210 nucleoporin 210kDa
NUP93 nucleoporin 93kDa
OAT ornithine aminotransferase
OPTN optineurin
OSBPL8 oxysterol binding protein-like 8
OSGEP O-sialoglycoprotein endopeptidase
OXA1L oxidase (cytochrome c) assembly 1-like
PABPC1 poly(A) binding protein, cytoplasmic 1
PARD3 par-3 family cell polarity regulator
PARP1 poly (ADP-ribose) polymerase 1
PARS2 prolyl-tRNA synthetase 2, mitochondrial (putative)
PCBP1 poly(rC) binding protein 1
PCBP2 poly(rC) binding protein 2
PCCB propionyl CoA carboxylase, beta polypeptide
PCNA proliferating cell nuclear antigen
PCYOX1 prenylcysteine oxidase 1
PDK3 pyruvate dehydrogenase kinase, isozyme 3
PELO pelota homolog (Drosophila)
PGAM5 phosphoglycerate mutase family member 5
PGRMC1 progesterone receptor membrane component 1
PGRMC2 progesterone receptor membrane component 2
PHB prohibitin
PHB2 prohibitin 2
PHGDH phosphoglycerate dehydrogenase
PI4KA phosphatidylinositol 4-kinase, catalytic, alpha
PIKFYVE phosphoinositide kinase, FYVE finger containing
PLOD1 procollagen-lysine, 2-oxoglutarate 5-dioxygenase 1
PMPCA peptidase (mitochondrial processing) alpha
PMPCB peptidase (mitochondrial processing) beta
PNKD paroxysmal nonkinesigenic dyskinesia
PNMA2 paraneoplastic Ma antigen 2
PNPT1 polyribonucleotide nucleotidyltransferase 1
POLDIP2 polymerase (DNA-directed), delta interacting protein 2
POLR2A polymerase (RNA) II (DNA directed) polypeptide A, 220kDa
POLR2B polymerase (RNA) II (DNA directed) polypeptide B, 140kDa
POLR2H polymerase (RNA) II (DNA directed) polypeptide H
POLRMT polymerase (RNA) mitochondrial (DNA directed)
PPP2CA protein phosphatase 2, catalytic subunit, alpha isozyme
PPP2CB protein phosphatase 2, catalytic subunit, beta isozyme
PPP2R1A protein phosphatase 2, regulatory subunit A, alpha
PPP2R1B protein phosphatase 2, regulatory subunit A, beta
PPP2R2A protein phosphatase 2, regulatory subunit B, alpha
PPP2R5C protein phosphatase 2, regulatory subunit B', gamma
PPP2R5E protein phosphatase 2, regulatory subunit B', epsilon isoform
PPP6C protein phosphatase 6, catalytic subunit
PPP6R3 protein phosphatase 6, regulatory subunit 3
PPT1 palmitoyl-protein thioesterase 1
PRDX4 peroxiredoxin 4
PRDX5 peroxiredoxin 5
PRKAR2A protein kinase, cAMP-dependent, regulatory, type II, alpha
PRKDC protein kinase, DNA-activated, catalytic polypeptide
PRPF8 pre-mRNA processing factor 8
PSMC2 proteasome (prosome, macropain) 26S subunit, ATPase, 2
PSMC5 proteasome (prosome, macropain) 26S subunit, ATPase, 5
PSMC6 proteasome (prosome, macropain) 26S subunit, ATPase, 6
PSMD2 proteasome (prosome, macropain) 26S subunit, non-ATPase, 2
PSMD3 proteasome (prosome, macropain) 26S subunit, non-ATPase, 3
PSMD6 proteasome (prosome, macropain) 26S subunit, non-ATPase, 6
PTCD1 pentatricopeptide repeat domain 1
PTCD3 pentatricopeptide repeat domain 3
PTGES2 prostaglandin E synthase 2
PTOV1 prostate tumor overexpressed 1
PTPN1 protein tyrosine phosphatase, non-receptor type 1
PTPN13 protein tyrosine phosphatase, non-receptor type 13 (APO-1/CD95 (Fas)-associated phosphatase)
PTRH2 peptidyl-tRNA hydrolase 2
PUS1 pseudouridylate synthase 1
PUSL1 pseudouridylate synthase-like 1
PYCR2 pyrroline-5-carboxylate reductase family, member 2
RAB10 RAB10, member RAS oncogene family
RAB11A RAB11A, member RAS oncogene family
RAB14 RAB14, member RAS oncogene family
RAB1B RAB1B, member RAS oncogene family
RAB21 RAB21, member RAS oncogene family
RAB2A RAB2A, member RAS oncogene family
RAB4A RAB4A, member RAS oncogene family
RAB5B RAB5B, member RAS oncogene family
RAB5C RAB5C, member RAS oncogene family
RAB6A RAB6A, member RAS oncogene family
RAB7A RAB7A, member RAS oncogene family
RAB8A RAB8A, member RAS oncogene family
RAD23A RAD23 homolog A (S. cerevisiae)
RAD23B RAD23 homolog B (S. cerevisiae)
RAI14 retinoic acid induced 14
RANBP1 RAN binding protein 1
RANBP9 RAN binding protein 9
RARS arginyl-tRNA synthetase
RARS2 arginyl-tRNA synthetase 2, mitochondrial
RBBP4 retinoblastoma binding protein 4
RBBP5 retinoblastoma binding protein 5
RBBP7 retinoblastoma binding protein 7
RBFA ribosome binding factor A (putative)
RCN2 reticulocalbin 2, EF-hand calcium binding domain
RDH11 retinol dehydrogenase 11 (all-trans/9-cis/11-cis)
RDH13 retinol dehydrogenase 13 (all-trans/9-cis)
RFC3 replication factor C (activator 1) 3, 38kDa
RFT1 RFT1 homolog (S. cerevisiae)
RHBDD2 rhomboid domain containing 2
RNMTL1 RNA methyltransferase like 1
RPL12 ribosomal protein L12
RPL13 ribosomal protein L13
RPL14 ribosomal protein L14
RPL15 ribosomal protein L15
RPL17 ribosomal protein L17
RPL18 ribosomal protein L18
RPL19 ribosomal protein L19
RPL21 ribosomal protein L21
RPL22 ribosomal protein L22
RPL23 ribosomal protein L23
RPL23A ribosomal protein L23a
RPL24 ribosomal protein L24
RPL26 ribosomal protein L26
RPL27 ribosomal protein L27
RPL29 ribosomal protein L29
RPL3 ribosomal protein L3
RPL31 ribosomal protein L31
RPL35 ribosomal protein L35
RPL36 ribosomal protein L36
RPL4 ribosomal protein L4
RPL5 ribosomal protein L5
RPL6 ribosomal protein L6
RPL7 ribosomal protein L7
RPL8 ribosomal protein L8
RPLP0 ribosomal protein, large, P0
RPLP1 ribosomal protein, large, P1
RPLP2 ribosomal protein, large, P2
RPN1 ribophorin I
RPN2 ribophorin II
RPS14 ribosomal protein S14
RPS27 ribosomal protein S27
RPS28 ribosomal protein S28
RPS3A ribosomal protein S3A
RPS4X ribosomal protein S4, X-linked
RPS6 ribosomal protein S6
RPS7 ribosomal protein S7
RPSA ribosomal protein SA
RPUSD3 RNA pseudouridylate synthase domain containing 3
RPUSD4 RNA pseudouridylate synthase domain containing 4
RTN4 reticulon 4
RUVBL1 RuvB-like AAA ATPase 1
RUVBL2 RuvB-like AAA ATPase 2
S100A11 S100 calcium binding protein A11
SACM1L SAC1 suppressor of actin mutations 1-like (yeast)
SARS2 seryl-tRNA synthetase 2, mitochondrial
SCAMP3 secretory carrier membrane protein 3
SCCPDH saccharopine dehydrogenase (putative)
SCFD1 sec1 family domain containing 1
SCO2 SCO2 cytochrome c oxidase assembly protein
SDF2L1 stromal cell-derived factor 2-like 1
SDF4 stromal cell derived factor 4
SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
SEC22B SEC22 vesicle trafficking protein homolog B (S. cerevisiae) (gene/pseudogene)
SEC61A1 Sec61 alpha 1 subunit (S. cerevisiae)
SEC61B Sec61 beta subunit
SERBP1 SERPINE1 mRNA binding protein 1
SF3B3 splicing factor 3b, subunit 3, 130kDa
SFXN1 sideroflexin 1
SGK1 serum/glucocorticoid regulated kinase 1
SHMT2 serine hydroxymethyltransferase 2 (mitochondrial)
SKP1 S-phase kinase-associated protein 1
SKP2 S-phase kinase-associated protein 2, E3 ubiquitin protein ligase
SLC16A1 solute carrier family 16 (monocarboxylate transporter), member 1
SLC1A5 solute carrier family 1 (neutral amino acid transporter), member 5
SLC25A1 solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1
SLC25A10 solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10
SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11
SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12
SLC25A13 solute carrier family 25 (aspartate/glutamate carrier), member 13
SLC25A18 solute carrier family 25 (glutamate carrier), member 18
SLC25A19 solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19
SLC25A21 solute carrier family 25 (mitochondrial oxoadipate carrier), member 21
SLC25A22 solute carrier family 25 (mitochondrial carrier: glutamate), member 22
SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3
SLC25A33 solute carrier family 25 (pyrimidine nucleotide carrier), member 33
SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
SLC25A5 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5
SLC25A6 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 6
SLC2A1 solute carrier family 2 (facilitated glucose transporter), member 1
SLC37A4 solute carrier family 37 (glucose-6-phosphate transporter), member 4
SLC39A7 solute carrier family 39 (zinc transporter), member 7
SLC3A2 solute carrier family 3 (amino acid transporter heavy chain), member 2
SLC7A5 solute carrier family 7 (amino acid transporter light chain, L system), member 5
SLIRP SRA stem-loop interacting RNA binding protein
SMC1A structural maintenance of chromosomes 1A
SMC3 structural maintenance of chromosomes 3
SMC4 structural maintenance of chromosomes 4
SNRPF small nuclear ribonucleoprotein polypeptide F
SPAG5 sperm associated antigen 5
SPTLC1 serine palmitoyltransferase, long chain base subunit 1
SPTLC2 serine palmitoyltransferase, long chain base subunit 2
SRP68 signal recognition particle 68kDa
SRP72 signal recognition particle 72kDa
SRPRB signal recognition particle receptor, B subunit
SRSF2 serine/arginine-rich splicing factor 2
SSBP1 single-stranded DNA binding protein 1, mitochondrial
SSR1 signal sequence receptor, alpha
SSR3 signal sequence receptor, gamma (translocon-associated protein gamma)
SSR4 signal sequence receptor, delta
ST13 suppression of tumorigenicity 13 (colon carcinoma) (Hsp70 interacting protein)
STAT1 signal transducer and activator of transcription 1, 91kDa
STAT2 signal transducer and activator of transcription 2, 113kDa
STAT3 signal transducer and activator of transcription 3 (acute-phase response factor)
STIP1 stress-induced phosphoprotein 1
STOML2 stomatin (EPB72)-like 2
STT3A STT3A, subunit of the oligosaccharyltransferase complex (catalytic)
STT3B STT3B, subunit of the oligosaccharyltransferase complex (catalytic)
STUB1 STIP1 homology and U-box containing protein 1, E3 ubiquitin protein ligase
STXBP4 syntaxin binding protein 4
SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit
SUPV3L1 suppressor of var1, 3-like 1 (S. cerevisiae)
SV2A synaptic vesicle glycoprotein 2A
SYNCRIP synaptotagmin binding, cytoplasmic RNA interacting protein
SYNGR1 synaptogyrin 1
SYNJ2BP synaptojanin 2 binding protein
TAGLN2 transgelin 2
TANK TRAF family member-associated NFKB activator
TARS2 threonyl-tRNA synthetase 2, mitochondrial (putative)
TBC1D15 TBC1 domain family, member 15
TBCD tubulin folding cofactor D
TBK1 TANK-binding kinase 1
TBKBP1 TBK1 binding protein 1
TCEB1 transcription elongation factor B (SIII), polypeptide 1 (15kDa, elongin C)
TCEB2 transcription elongation factor B (SIII), polypeptide 2 (18kDa, elongin B)
TCP1 t-complex 1
TECR trans-2,3-enoyl-CoA reductase
TEFM transcription elongation factor, mitochondrial
TFAM transcription factor A, mitochondrial
TFB1M transcription factor B1, mitochondrial
TFRC transferrin receptor
THNSL1 threonine synthase-like 1 (S. cerevisiae)
THOC2 THO complex 2
TIMM10 translocase of inner mitochondrial membrane 10 homolog (yeast)
TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast)
TIMM21 translocase of inner mitochondrial membrane 21 homolog (yeast)
TIMM23 translocase of inner mitochondrial membrane 23 homolog (yeast)
TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae)
TIMMDC1 translocase of inner mitochondrial membrane domain containing 1
TM9SF2 transmembrane 9 superfamily member 2
TM9SF4 transmembrane 9 superfamily protein member 4
TMED10 transmembrane emp24-like trafficking protein 10 (yeast)
TMED2 transmembrane emp24 domain trafficking protein 2
TMED9 transmembrane emp24 protein transport domain containing 9
TMEM109 transmembrane protein 109
TMEM161A transmembrane protein 161A
TMEM205 transmembrane protein 205
TMEM33 transmembrane protein 33
TMLHE trimethyllysine hydroxylase, epsilon
TMPO thymopoietin
TMX1 thioredoxin-related transmembrane protein 1
TNPO1 transportin 1
TNPO2 transportin 2
TNPO3 transportin 3
TNS2 tensin 2
TOMM22 translocase of outer mitochondrial membrane 22 homolog (yeast)
TOMM70A translocase of outer mitochondrial membrane 70 homolog A (S. cerevisiae)
TOP1 topoisomerase (DNA) I
TOR1AIP1 torsin A interacting protein 1
TP53 tumor protein p53
TRAF2 TNF receptor-associated factor 2
TRAFD1 TRAF-type zinc finger domain containing 1
TRAP1 TNF receptor-associated protein 1
TRIM28 tripartite motif containing 28
TRIP13 thyroid hormone receptor interactor 13
TRMT10C tRNA methyltransferase 10 homolog C (S. cerevisiae)
TRUB2 TruB pseudouridine (psi) synthase family member 2
TTC1 tetratricopeptide repeat domain 1
TTI1 TELO2 interacting protein 1
TUBA1A tubulin, alpha 1a
TUBA1B tubulin, alpha 1b
TUBA1C tubulin, alpha 1c
TUBB tubulin, beta class I
TUBB2A tubulin, beta 2A class IIa
TUBB2B tubulin, beta 2B class IIb
TUBB3 tubulin, beta 3 class III
TUBB4A tubulin, beta 4A class IVa
TUBB4B tubulin, beta 4B class IVb
TUBB6 tubulin, beta 6 class V
TUFM Tu translation elongation factor, mitochondrial
TXLNA taxilin alpha
TXN thioredoxin
UBC ubiquitin C
UBE2C ubiquitin-conjugating enzyme E2C
UBE2S ubiquitin-conjugating enzyme E2S
UBE3C ubiquitin protein ligase E3C
UFL1 UFM1-specific ligase 1
UNC45A unc-45 homolog A (C. elegans)
UQCRC1 ubiquinol-cytochrome c reductase core protein I
UQCRC2 ubiquinol-cytochrome c reductase core protein II
UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse)
USP7 ubiquitin specific peptidase 7 (herpes virus-associated)
USP9X ubiquitin specific peptidase 9, X-linked
UTRN utrophin
VAC14 Vac14 homolog (S. cerevisiae)
VAMP3 vesicle-associated membrane protein 3
VAPA VAMP (vesicle-associated membrane protein)-associated protein A, 33kDa
VARS2 valyl-tRNA synthetase 2, mitochondrial
VAT1 vesicle amine transport 1
VCP valosin containing protein
VDAC1 voltage-dependent anion channel 1
VDAC2 voltage-dependent anion channel 2
VDAC3 voltage-dependent anion channel 3
VIM vimentin
WBSCR16 Williams-Beuren syndrome chromosome region 16
WDR6 WD repeat domain 6
WRNIP1 Werner helicase interacting protein 1
XPO1 exportin 1
XPO5 exportin 5
XPOT exportin, tRNA
XRCC5 X-ray repair complementing defective repair in Chinese hamster cells 5 (double-strand-break rejoining)
XRCC6 X-ray repair complementing defective repair in Chinese hamster cells 6
YARS2 tyrosyl-tRNA synthetase 2, mitochondrial
YBX1 Y box binding protein 1
YME1L1 YME1-like 1 ATPase
YWHAB tyrosine 3-monooxygenase/tryptophan 5-monooxygenase activation protein, beta
YWHAE tyrosine 3-monooxygenase/tryptophan 5-monooxygenase activation protein, epsilon
YWHAG tyrosine 3-monooxygenase/tryptophan 5-monooxygenase activation protein, gamma
YWHAH tyrosine 3-monooxygenase/tryptophan 5-monooxygenase activation protein, eta
YWHAQ tyrosine 3-monooxygenase/tryptophan 5-monooxygenase activation protein, theta
YWHAZ tyrosine 3-monooxygenase/tryptophan 5-monooxygenase activation protein, zeta
ZMPSTE24 zinc metallopeptidase STE24