Leucine isoleucine and valine metabolism Gene Set

Dataset WikiPathways Pathways 2024
Category structural or functional annotations
Type pathway
External Link https://www.wikipathways.org/pathways/WP4686.html
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Genes

24 proteins participating in the Leucine isoleucine and valine metabolism pathway from the WikiPathways Pathways 2024 dataset.

Symbol Name
ACAD8 acyl-CoA dehydrogenase family, member 8
ACADSB acyl-CoA dehydrogenase, short/branched chain
ACAT1 acetyl-CoA acetyltransferase 1
ACSF3 acyl-CoA synthetase family member 3
ALDH6A1 aldehyde dehydrogenase 6 family, member A1
AUH AU RNA binding protein/enoyl-CoA hydratase
BCAT1 branched chain amino-acid transaminase 1, cytosolic
BCAT2 branched chain amino-acid transaminase 2, mitochondrial
BCKDHA branched chain keto acid dehydrogenase E1, alpha polypeptide
BCKDHB branched chain keto acid dehydrogenase E1, beta polypeptide
DBT dihydrolipoamide branched chain transacylase E2
DLD dihydrolipoamide dehydrogenase
ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial
HIBADH 3-hydroxyisobutyrate dehydrogenase
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
HMGCLL1 3-hydroxymethyl-3-methylglutaryl-CoA lyase-like 1
HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10
IVD isovaleryl-CoA dehydrogenase
MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha)
MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta)
MLYCD malonyl-CoA decarboxylase
MMUT methylmalonyl-CoA mutase
PCCA propionyl CoA carboxylase, alpha polypeptide
PCCB propionyl CoA carboxylase, beta polypeptide