Lysine degradation Gene Set

Dataset KEGG Pathways 2026
Category structural or functional annotations
Type pathway
Description (Kyoto Encyclopedia of Genes and Genomes, hsa00310)
External Link https://www.kegg.jp/entry/hsa00310
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Genes

63 proteins participating in the Lysine degradation pathway from the KEGG Pathways 2026 dataset.

Symbol Name
AADAT aminoadipate aminotransferase
AASS aminoadipate-semialdehyde synthase
ALDH1B1 aldehyde dehydrogenase 1 family, member B1
ALDH2 aldehyde dehydrogenase 2 family (mitochondrial)
ALDH3A2 aldehyde dehydrogenase 3 family, member A2
ALDH7A1 aldehyde dehydrogenase 7 family, member A1
ALDH9A1 aldehyde dehydrogenase 9 family, member A1
ASH1L ash1 (absent, small, or homeotic)-like (Drosophila)
BBOX1 butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
CAMKMT calmodulin-lysine N-methyltransferase
COLGALT1 collagen beta(1-O)galactosyltransferase 1
COLGALT2 collagen beta(1-O)galactosyltransferase 2
DHTKD1 dehydrogenase E1 and transketolase domain containing 1
DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
DOT1L DOT1-like histone H3K79 methyltransferase
ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial
EHHADH enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase
EHMT1 euchromatic histone-lysine N-methyltransferase 1
EHMT2 euchromatic histone-lysine N-methyltransferase 2
EZH1 enhancer of zeste 1 polycomb repressive complex 2 subunit
EZH2 enhancer of zeste 2 polycomb repressive complex 2 subunit
GCDH glutaryl-CoA dehydrogenase
HADH hydroxyacyl-CoA dehydrogenase
HADHA hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit
HYKK hydroxylysine kinase
KMT2A lysine (K)-specific methyltransferase 2A
KMT2B lysine (K)-specific methyltransferase 2B
KMT2C lysine (K)-specific methyltransferase 2C
KMT2D lysine (K)-specific methyltransferase 2D
KMT2E lysine (K)-specific methyltransferase 2E
KMT5A lysine methyltransferase 5A
KMT5B lysine methyltransferase 5B
KMT5C lysine methyltransferase 5C
LDHD lactate dehydrogenase D
MECOM MDS1 and EVI1 complex locus
NSD1 nuclear receptor binding SET domain protein 1
NSD2 nuclear receptor binding SET domain protein 2
NSD3 nuclear receptor binding SET domain protein 3
PHYKPL 5-phosphohydroxy-L-lysine phospho-lyase
PIPOX pipecolic acid oxidase
PLOD1 procollagen-lysine, 2-oxoglutarate 5-dioxygenase 1
PLOD2 procollagen-lysine, 2-oxoglutarate 5-dioxygenase 2
PLOD3 procollagen-lysine, 2-oxoglutarate 5-dioxygenase 3
PRDM16 PR domain containing 16
PRDM2 PR domain containing 2, with ZNF domain
PRDM6 PR domain containing 6
PRDM7 PR domain containing 7
PRDM9 PR domain containing 9
SETD1A SET domain containing 1A
SETD1B SET domain containing 1B
SETD2 SET domain containing 2
SETD7 SET domain containing (lysine methyltransferase) 7
SETDB1 SET domain, bifurcated 1
SETDB2 SET domain, bifurcated 2
SETMAR SET domain and mariner transposase fusion gene
SMYD1 SET and MYND domain containing 1
SMYD2 SET and MYND domain containing 2
SMYD3 SET and MYND domain containing 3
SOAT1 sterol O-acyltransferase 1
SOAT2 sterol O-acyltransferase 2
SUV39H1 suppressor of variegation 3-9 homolog 1 (Drosophila)
SUV39H2 suppressor of variegation 3-9 homolog 2 (Drosophila)
TMLHE trimethyllysine hydroxylase, epsilon