| Symbol |
Name |
|
AADAT
|
aminoadipate aminotransferase
|
|
AASS
|
aminoadipate-semialdehyde synthase
|
|
ACAT1
|
acetyl-CoA acetyltransferase 1
|
|
ACO1
|
aconitase 1, soluble
|
|
ALDH7A1
|
aldehyde dehydrogenase 7 family, member A1
|
|
ALDOA
|
aldolase A, fructose-bisphosphate
|
|
ALDOB
|
aldolase B, fructose-bisphosphate
|
|
ALDOC
|
aldolase C, fructose-bisphosphate
|
|
AMT
|
aminomethyltransferase
|
|
ARG1
|
arginase 1
|
|
ASL
|
argininosuccinate lyase
|
|
ASS1
|
argininosuccinate synthase 1
|
|
BTD
|
biotinidase
|
|
CBS
|
cystathionine-beta-synthase
|
|
CDO1
|
cysteine dioxygenase type 1
|
|
CPS1
|
carbamoyl-phosphate synthase 1, mitochondrial
|
|
CTH
|
cystathionine gamma-lyase
|
|
DHTKD1
|
dehydrogenase E1 and transketolase domain containing 1
|
|
DLAT
|
dihydrolipoamide S-acetyltransferase
|
|
DLD
|
dihydrolipoamide dehydrogenase
|
|
ECHS1
|
enoyl CoA hydratase, short chain, 1, mitochondrial
|
|
ENO1
|
enolase 1, (alpha)
|
|
ENO2
|
enolase 2 (gamma, neuronal)
|
|
ENO3
|
enolase 3 (beta, muscle)
|
|
ETHE1
|
ethylmalonic encephalopathy 1
|
|
FBP1
|
fructose-1,6-bisphosphatase 1
|
|
FBP2
|
fructose-1,6-bisphosphatase 2
|
|
G6PC1
|
glucose-6-phosphatase catalytic subunit 1
|
|
GAMT
|
guanidinoacetate N-methyltransferase
|
|
GAPDH
|
glyceraldehyde-3-phosphate dehydrogenase
|
|
GATM
|
glycine amidinotransferase (L-arginine:glycine amidinotransferase)
|
|
GCDH
|
glutaryl-CoA dehydrogenase
|
|
GCK
|
glucokinase (hexokinase 4)
|
|
GLDC
|
glycine dehydrogenase (decarboxylating)
|
|
GLS2
|
glutaminase 2 (liver, mitochondrial)
|
|
GLUD1
|
glutamate dehydrogenase 1
|
|
GOT1
|
glutamic-oxaloacetic transaminase 1, soluble
|
|
GOT2
|
glutamic-oxaloacetic transaminase 2, mitochondrial
|
|
GPHN
|
gephyrin
|
|
GPI
|
glucose-6-phosphate isomerase
|
|
GPT
|
glutamic-pyruvate transaminase (alanine aminotransferase)
|
|
HADH
|
hydroxyacyl-CoA dehydrogenase
|
|
HK1
|
hexokinase 1
|
|
HK2
|
hexokinase 2
|
|
HK3
|
hexokinase 3 (white cell)
|
|
HLCS
|
holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)
|
|
LDHA
|
lactate dehydrogenase A
|
|
LDHAL6B
|
lactate dehydrogenase A-like 6B
|
|
LDHB
|
lactate dehydrogenase B
|
|
LDHC
|
lactate dehydrogenase C
|
|
LOC102724560
|
cystathionine beta-synthase
|
|
MDH1
|
malate dehydrogenase 1, NAD (soluble)
|
|
MDH2
|
malate dehydrogenase 2, NAD (mitochondrial)
|
|
MOCS1
|
molybdenum cofactor synthesis 1
|
|
MOCS2
|
molybdenum cofactor synthesis 2
|
|
MOCS3
|
molybdenum cofactor synthesis 3
|
|
MPC1
|
mitochondrial pyruvate carrier 1
|
|
MPC2
|
mitochondrial pyruvate carrier 2
|
|
OTC
|
ornithine carbamoyltransferase
|
|
PC
|
pyruvate carboxylase
|
|
PCK1
|
phosphoenolpyruvate carboxykinase 1 (soluble)
|
|
PDHA1
|
pyruvate dehydrogenase (lipoamide) alpha 1
|
|
PFKL
|
phosphofructokinase, liver
|
|
PFKM
|
phosphofructokinase, muscle
|
|
PFKP
|
phosphofructokinase, platelet
|
|
PGAM1
|
phosphoglycerate mutase 1 (brain)
|
|
PGAM2
|
phosphoglycerate mutase 2 (muscle)
|
|
PGK1
|
phosphoglycerate kinase 1
|
|
PGK2
|
phosphoglycerate kinase 2
|
|
PHGDH
|
phosphoglycerate dehydrogenase
|
|
PKLR
|
pyruvate kinase, liver and RBC
|
|
PKM
|
pyruvate kinase, muscle
|
|
PSAT1
|
phosphoserine aminotransferase 1
|
|
PSPH
|
phosphoserine phosphatase
|
|
SFXN1
|
sideroflexin 1
|
|
SHMT1
|
serine hydroxymethyltransferase 1 (soluble)
|
|
SHMT2
|
serine hydroxymethyltransferase 2 (mitochondrial)
|
|
SLC1A5
|
solute carrier family 1 (neutral amino acid transporter), member 5
|
|
SLC25A1
|
solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1
|
|
SLC25A15
|
solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15
|
|
SLC25A5
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5
|
|
SLC2A1
|
solute carrier family 2 (facilitated glucose transporter), member 1
|
|
SLC2A2
|
solute carrier family 2 (facilitated glucose transporter), member 2
|
|
SLC2A3
|
solute carrier family 2 (facilitated glucose transporter), member 3
|
|
SLC2A4
|
solute carrier family 2 (facilitated glucose transporter), member 4
|
|
SLC2A5
|
solute carrier family 2 (facilitated glucose/fructose transporter), member 5
|
|
SLC7A2
|
solute carrier family 7 (cationic amino acid transporter, y+ system), member 2
|
|
SPCS1
|
signal peptidase complex subunit 1 homolog (S. cerevisiae)
|
|
SQOR
|
sulfide quinone oxidoreductase
|
|
SUOX
|
sulfite oxidase
|
|
TPI1
|
triosephosphate isomerase 1
|
|
XDH
|
xanthine dehydrogenase
|