PCCA Gene Set

Dataset Pathway Commons Protein-Protein Interactions
Category physical interactions
Type interacting protein
Description propionyl CoA carboxylase, alpha polypeptide|The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, May 2010] (NCBI Entrez Gene Database, 5095)
External Link http://www.ncbi.nlm.nih.gov/gene/5095
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Genes

354 interacting proteins for PCCA from the Pathway Commons Protein-Protein Interactions dataset.

Symbol Name
ACACA acetyl-CoA carboxylase alpha
ACACB acetyl-CoA carboxylase beta
ACTA2 actin, alpha 2, smooth muscle, aorta
ACTB actin, beta
ACTG2 actin, gamma 2, smooth muscle, enteric
AKAP8L A kinase (PRKA) anchor protein 8-like
ALB albumin
ANXA2 annexin A2
ATF2 activating transcription factor 2
ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle
ATXN2L ataxin 2-like
BAG2 BCL2-associated athanogene 2
C1QBP complement component 1, q subcomponent binding protein
CAD carbamoyl-phosphate synthetase 2, aspartate transcarbamylase, and dihydroorotase
CALM1 calmodulin 1 (phosphorylase kinase, delta)
CAPZA1 capping protein (actin filament) muscle Z-line, alpha 1
CAPZB capping protein (actin filament) muscle Z-line, beta
CCT2 chaperonin containing TCP1, subunit 2 (beta)
CCT3 chaperonin containing TCP1, subunit 3 (gamma)
CCT4 chaperonin containing TCP1, subunit 4 (delta)
CCT5 chaperonin containing TCP1, subunit 5 (epsilon)
CCT6A chaperonin containing TCP1, subunit 6A (zeta 1)
CCT7 chaperonin containing TCP1, subunit 7 (eta)
CCT8 chaperonin containing TCP1, subunit 8 (theta)
CDC42 cell division cycle 42
CDCA4 cell division cycle associated 4
CDK1 cyclin-dependent kinase 1
CEBPB CCAAT/enhancer binding protein (C/EBP), beta
CEBPG CCAAT/enhancer binding protein (C/EBP), gamma
CKB creatine kinase, brain
CLPX caseinolytic mitochondrial matrix peptidase chaperone subunit
CLTC clathrin, heavy chain (Hc)
CSE1L CSE1 chromosome segregation 1-like (yeast)
DARS aspartyl-tRNA synthetase
DAZAP1 DAZ associated protein 1
DCD dermcidin
DDX17 DEAD (Asp-Glu-Ala-Asp) box helicase 17
DDX21 DEAD (Asp-Glu-Ala-Asp) box helicase 21
DDX3X DEAD (Asp-Glu-Ala-Asp) box helicase 3, X-linked
DDX5 DEAD (Asp-Glu-Ala-Asp) box helicase 5
DDX6 DEAD (Asp-Glu-Ala-Asp) box helicase 6
DHX9 DEAH (Asp-Glu-Ala-His) box helicase 9
DNAJB1 DnaJ (Hsp40) homolog, subfamily B, member 1
DNAJB5 DnaJ (Hsp40) homolog, subfamily B, member 5
DNAJB6 DnaJ (Hsp40) homolog, subfamily B, member 6
DSP desmoplakin
DYNC2H1 dynein, cytoplasmic 2, heavy chain 1
E2F1 E2F transcription factor 1
E2F4 E2F transcription factor 4, p107/p130-binding
ECH1 enoyl CoA hydratase 1, peroxisomal
EEF1A1 eukaryotic translation elongation factor 1 alpha 1
EEF1A1P5 eukaryotic translation elongation factor 1 alpha 1 pseudogene 5
EEF1B2 eukaryotic translation elongation factor 1 beta 2
EIF3B eukaryotic translation initiation factor 3, subunit B
ENO1 enolase 1, (alpha)
EPRS glutamyl-prolyl-tRNA synthetase
FAU Finkel-Biskis-Reilly murine sarcoma virus (FBR-MuSV) ubiquitously expressed
FLNC filamin C, gamma
GAPDH glyceraldehyde-3-phosphate dehydrogenase
GBAS glioblastoma amplified sequence
GCN1L1 GCN1 general control of amino-acid synthesis 1-like 1 (yeast)
GLUD1 glutamate dehydrogenase 1
GRPEL1 GrpE-like 1, mitochondrial (E. coli)
H1FX H1 histone family, member X
H2AFJ H2A histone family, member J
H2BFS H2B histone family, member S (pseudogene)
H3F3A H3 histone, family 3A
HAX1 HCLS1 associated protein X-1
HCFC1 host cell factor C1
HCFC2 host cell factor C2
HIST1H1D histone cluster 1, H1d
HIST1H1E histone cluster 1, H1e
HIST1H2AB histone cluster 1, H2ab
HIST1H2AC histone cluster 1, H2ac
HIST1H2AD histone cluster 1, H2ad
HIST1H2AH histone cluster 1, H2ah
HIST1H2AI histone cluster 1, H2ai
HIST1H2AJ histone cluster 1, H2aj
HIST1H2BB histone cluster 1, H2bb
HIST1H2BD histone cluster 1, H2bd
HIST1H2BF histone cluster 1, H2bf
HIST1H2BH histone cluster 1, H2bh
HIST1H2BJ histone cluster 1, H2bj
HIST1H2BK histone cluster 1, H2bk
HIST1H2BL histone cluster 1, H2bl
HIST1H2BM histone cluster 1, H2bm
HIST1H2BN histone cluster 1, H2bn
HIST1H2BO histone cluster 1, H2bo
HIST1H3B histone cluster 1, H3b
HIST1H4F histone cluster 1, H4f
HIST2H2AA4 histone cluster 2, H2aa4
HIST2H2AC histone cluster 2, H2ac
HIST2H2BE histone cluster 2, H2be
HIST2H2BF histone cluster 2, H2bf
HIST2H3A histone cluster 2, H3a
HIST3H2A histone cluster 3, H2a
HIST3H2BB histone cluster 3, H2bb
HIST3H3 histone cluster 3, H3
HLCS holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)
HNRNPA0 heterogeneous nuclear ribonucleoprotein A0
HNRNPA1 heterogeneous nuclear ribonucleoprotein A1
HNRNPA2B1 heterogeneous nuclear ribonucleoprotein A2/B1
HNRNPAB heterogeneous nuclear ribonucleoprotein A/B
HNRNPC heterogeneous nuclear ribonucleoprotein C (C1/C2)
HNRNPCL1 heterogeneous nuclear ribonucleoprotein C-like 1
HNRNPD heterogeneous nuclear ribonucleoprotein D (AU-rich element RNA binding protein 1, 37kDa)
HNRNPF heterogeneous nuclear ribonucleoprotein F
HNRNPH1 heterogeneous nuclear ribonucleoprotein H1 (H)
HNRNPH2 heterogeneous nuclear ribonucleoprotein H2 (H')
HNRNPK heterogeneous nuclear ribonucleoprotein K
HNRNPL heterogeneous nuclear ribonucleoprotein L
HNRNPM heterogeneous nuclear ribonucleoprotein M
HNRNPR heterogeneous nuclear ribonucleoprotein R
HNRNPU heterogeneous nuclear ribonucleoprotein U (scaffold attachment factor A)
HSP90AA1 heat shock protein 90kDa alpha (cytosolic), class A member 1
HSP90AB1 heat shock protein 90kDa alpha (cytosolic), class B member 1
HSPA1B heat shock 70kDa protein 1B
HSPA5 heat shock 70kDa protein 5 (glucose-regulated protein, 78kDa)
HSPA8 heat shock 70kDa protein 8
HSPA9 heat shock 70kDa protein 9 (mortalin)
HSPB1 heat shock 27kDa protein 1
HSPD1 heat shock 60kDa protein 1 (chaperonin)
IARS isoleucyl-tRNA synthetase
IFIT1 interferon-induced protein with tetratricopeptide repeats 1
IFIT1B interferon-induced protein with tetratricopeptide repeats 1B
IFIT2 interferon-induced protein with tetratricopeptide repeats 2
IFIT3 interferon-induced protein with tetratricopeptide repeats 3
IGF2BP1 insulin-like growth factor 2 mRNA binding protein 1
ILF2 interleukin enhancer binding factor 2
ILF3 interleukin enhancer binding factor 3, 90kDa
IQGAP1 IQ motif containing GTPase activating protein 1
IQGAP2 IQ motif containing GTPase activating protein 2
IRS4 insulin receptor substrate 4
JUN jun proto-oncogene
JUP junction plakoglobin
KHDRBS1 KH domain containing, RNA binding, signal transduction associated 1
KPNB1 karyopherin (importin) beta 1
KRT1 keratin 1, type II
KRT10 keratin 10, type I
KRT14 keratin 14, type I
KRT16 keratin 16, type I
KRT2 keratin 2, type II
KRT31 keratin 31, type I
KRT32 keratin 32, type I
KRT33B keratin 33B, type I
KRT5 keratin 5, type II
KRT6B keratin 6B, type II
KRT78 keratin 78, type II
KRT81 keratin 81, type II
KRT85 keratin 85, type II
KRT9 keratin 9, type I
LDHA lactate dehydrogenase A
LDHB lactate dehydrogenase B
LRPPRC leucine-rich pentatricopeptide repeat containing
LSM12 LSM12 homolog (S. cerevisiae)
MAGED1 melanoma antigen family D1
MAP7 microtubule-associated protein 7
MATR3 matrin 3
MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha)
MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta)
MCM5 minichromosome maintenance complex component 5
MKI67 marker of proliferation Ki-67
MLF2 myeloid leukemia factor 2
MOV10 Mov10 RISC complex RNA helicase
MRPL12 mitochondrial ribosomal protein L12
MRPS27 mitochondrial ribosomal protein S27
MYBBP1A MYB binding protein (P160) 1a
MYC v-myc avian myelocytomatosis viral oncogene homolog
MYL6 myosin, light chain 6, alkali, smooth muscle and non-muscle
NIPSNAP1 nipsnap homolog 1 (C. elegans)
NONO non-POU domain containing, octamer-binding
NPM1 nucleophosmin (nucleolar phosphoprotein B23, numatrin)
NRF1 nuclear respiratory factor 1
NUCLEOLIN nucleolin multifunctional protein
NUFIP2 nuclear fragile X mental retardation protein interacting protein 2
NUP93 nucleoporin 93kDa
OGT O-linked N-acetylglucosamine (GlcNAc) transferase
P4HA2 prolyl 4-hydroxylase, alpha polypeptide II
PABPC1 poly(A) binding protein, cytoplasmic 1
PABPC4 poly(A) binding protein, cytoplasmic 4 (inducible form)
PARK2 parkin RBR E3 ubiquitin protein ligase
PARP2 poly (ADP-ribose) polymerase 2
PC pyruvate carboxylase
PCBP2 poly(rC) binding protein 2
PCCB propionyl CoA carboxylase, beta polypeptide
PCMT1 protein-L-isoaspartate (D-aspartate) O-methyltransferase
PHB2 prohibitin 2
POLR2A polymerase (RNA) II (DNA directed) polypeptide A, 220kDa
POTEE POTE ankyrin domain family, member E
POTEF POTE ankyrin domain family, member F
PPIA peptidylprolyl isomerase A (cyclophilin A)
PPP2CA protein phosphatase 2, catalytic subunit, alpha isozyme
PPP2CB protein phosphatase 2, catalytic subunit, beta isozyme
PPP2R1A protein phosphatase 2, regulatory subunit A, alpha
PPP2R1B protein phosphatase 2, regulatory subunit A, beta
PPP2R2B protein phosphatase 2, regulatory subunit B, beta
PPP4C protein phosphatase 4, catalytic subunit
PRDX1 peroxiredoxin 1
PRDX3 peroxiredoxin 3
PRDX4 peroxiredoxin 4
PRPF40A PRP40 pre-mRNA processing factor 40 homolog A (S. cerevisiae)
PRPF8 pre-mRNA processing factor 8
PRSS1 protease, serine, 1 (trypsin 1)
PSD4 pleckstrin and Sec7 domain containing 4
PSMB6 proteasome (prosome, macropain) subunit, beta type, 6
PSMC2 proteasome (prosome, macropain) 26S subunit, ATPase, 2
PSMD2 proteasome (prosome, macropain) 26S subunit, non-ATPase, 2
PTBP1 polypyrimidine tract binding protein 1
QARS glutaminyl-tRNA synthetase
R3HCC1 R3H domain and coiled-coil containing 1
RAD50 RAD50 homolog (S. cerevisiae)
RAN RAN, member RAS oncogene family
RBL2 retinoblastoma-like 2
RBM25 RNA binding motif protein 25
RBM7 RNA binding motif protein 7
RCN1 reticulocalbin 1, EF-hand calcium binding domain
RCN2 reticulocalbin 2, EF-hand calcium binding domain
RECQL4 RecQ protein-like 4
RFC3 replication factor C (activator 1) 3, 38kDa
RPL10 ribosomal protein L10
RPL10A ribosomal protein L10a
RPL11 ribosomal protein L11
RPL12 ribosomal protein L12
RPL13 ribosomal protein L13
RPL13A ribosomal protein L13a
RPL13AP3 ribosomal protein L13a pseudogene 3
RPL14 ribosomal protein L14
RPL15 ribosomal protein L15
RPL17 ribosomal protein L17
RPL18 ribosomal protein L18
RPL18A ribosomal protein L18a
RPL19 ribosomal protein L19
RPL21 ribosomal protein L21
RPL22 ribosomal protein L22
RPL23 ribosomal protein L23
RPL23A ribosomal protein L23a
RPL24 ribosomal protein L24
RPL26 ribosomal protein L26
RPL26L1 ribosomal protein L26-like 1
RPL27 ribosomal protein L27
RPL27A ribosomal protein L27a
RPL28 ribosomal protein L28
RPL3 ribosomal protein L3
RPL30 ribosomal protein L30
RPL31 ribosomal protein L31
RPL32 ribosomal protein L32
RPL34 ribosomal protein L34
RPL35 ribosomal protein L35
RPL35A ribosomal protein L35a
RPL36 ribosomal protein L36
RPL36A ribosomal protein L36a
RPL36AL ribosomal protein L36a-like
RPL37A ribosomal protein L37a
RPL4 ribosomal protein L4
RPL5 ribosomal protein L5
RPL6 ribosomal protein L6
RPL7 ribosomal protein L7
RPL7A ribosomal protein L7a
RPL8 ribosomal protein L8
RPLP0 ribosomal protein, large, P0
RPLP1 ribosomal protein, large, P1
RPLP2 ribosomal protein, large, P2
RPS10 ribosomal protein S10
RPS11 ribosomal protein S11
RPS12 ribosomal protein S12
RPS13 ribosomal protein S13
RPS14 ribosomal protein S14
RPS15A ribosomal protein S15a
RPS16 ribosomal protein S16
RPS17 ribosomal protein S17
RPS18 ribosomal protein S18
RPS19 ribosomal protein S19
RPS2 ribosomal protein S2
RPS20 ribosomal protein S20
RPS23 ribosomal protein S23
RPS24 ribosomal protein S24
RPS26 ribosomal protein S26
RPS27L ribosomal protein S27-like
RPS3 ribosomal protein S3
RPS3A ribosomal protein S3A
RPS4X ribosomal protein S4, X-linked
RPS5 ribosomal protein S5
RPS6 ribosomal protein S6
RPS7 ribosomal protein S7
RPS8 ribosomal protein S8
RPS9 ribosomal protein S9
RPSA ribosomal protein SA
RSL1D1 ribosomal L1 domain containing 1
RUVBL1 RuvB-like AAA ATPase 1
RUVBL2 RuvB-like AAA ATPase 2
S100A7 S100 calcium binding protein A7
S100A8 S100 calcium binding protein A8
S100A9 S100 calcium binding protein A9
SEC13 SEC13 homolog (S. cerevisiae)
SEC16A SEC16 homolog A (S. cerevisiae)
SERBP1 SERPINE1 mRNA binding protein 1
SERTAD4 SERTA domain containing 4
SET SET nuclear proto-oncogene
SF3B1 splicing factor 3b, subunit 1, 155kDa
SF3B2 splicing factor 3b, subunit 2, 145kDa
SFPQ splicing factor proline/glutamine-rich
SGOL2 shugoshin-like 2 (S. pombe)
SIK2 salt-inducible kinase 2
SKA1 spindle and kinetochore associated complex subunit 1
SKA2 spindle and kinetochore associated complex subunit 2
SKA3 spindle and kinetochore associated complex subunit 3
SKIV2L2 superkiller viralicidic activity 2-like 2 (S. cerevisiae)
SLC25A6 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 6
SMC4 structural maintenance of chromosomes 4
SNRNP200 small nuclear ribonucleoprotein 200kDa (U5)
SNRNP70 small nuclear ribonucleoprotein 70kDa (U1)
SNRPA small nuclear ribonucleoprotein polypeptide A
SNRPA1 small nuclear ribonucleoprotein polypeptide A'
SNRPB small nuclear ribonucleoprotein polypeptides B and B1
SNRPB2 small nuclear ribonucleoprotein polypeptide B
SNRPC small nuclear ribonucleoprotein polypeptide C
SNRPD1 small nuclear ribonucleoprotein D1 polypeptide 16kDa
SNRPD2 small nuclear ribonucleoprotein D2 polypeptide 16.5kDa
SNRPD3 small nuclear ribonucleoprotein D3 polypeptide 18kDa
SNRPE small nuclear ribonucleoprotein polypeptide E
SNRPF small nuclear ribonucleoprotein polypeptide F
SRP9 signal recognition particle 9kDa
SRSF1 serine/arginine-rich splicing factor 1
SRSF4 serine/arginine-rich splicing factor 4
SRSF5 serine/arginine-rich splicing factor 5
SRSF6 serine/arginine-rich splicing factor 6
SSBP1 single-stranded DNA binding protein 1, mitochondrial
STAU1 staufen double-stranded RNA binding protein 1
SUGP2 SURP and G patch domain containing 2
SYNCRIP synaptotagmin binding, cytoplasmic RNA interacting protein
TAF1 TAF1 RNA polymerase II, TATA box binding protein (TBP)-associated factor, 250kDa
TCP1 t-complex 1
TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae)
TMPO thymopoietin
TOE1 target of EGR1, member 1 (nuclear)
TRIM28 tripartite motif containing 28
TUBA1A tubulin, alpha 1a
TUBA1B tubulin, alpha 1b
TUBA1C tubulin, alpha 1c
TUBB tubulin, beta class I
TUBB4B tubulin, beta 4B class IVb
TUFM Tu translation elongation factor, mitochondrial
UBC ubiquitin C
UBE2N ubiquitin-conjugating enzyme E2N
UBR5 ubiquitin protein ligase E3 component n-recognin 5
VIM vimentin
WDR77 WD repeat domain 77
XPOT exportin, tRNA
XRCC5 X-ray repair complementing defective repair in Chinese hamster cells 5 (double-strand-break rejoining)
YBX1 Y box binding protein 1
YBX3 Y box binding protein 3
YWHAE tyrosine 3-monooxygenase/tryptophan 5-monooxygenase activation protein, epsilon
ZC3HAV1 zinc finger CCCH-type, antiviral 1
ZCCHC8 zinc finger, CCHC domain containing 8