| Symbol |
Name |
|
AARS2
|
alanyl-tRNA synthetase 2, mitochondrial
|
|
AASS
|
aminoadipate-semialdehyde synthase
|
|
ABCB7
|
ATP-binding cassette, sub-family B (MDR/TAP), member 7
|
|
ACAD9
|
acyl-CoA dehydrogenase family, member 9
|
|
ACADVL
|
acyl-CoA dehydrogenase, very long chain
|
|
ACOT9
|
acyl-CoA thioesterase 9
|
|
ADCK3
|
aarF domain containing kinase 3
|
|
AFG3L2
|
AFG3-like AAA ATPase 2
|
|
AGK
|
acylglycerol kinase
|
|
AIFM1
|
apoptosis-inducing factor, mitochondrion-associated, 1
|
|
ALDH18A1
|
aldehyde dehydrogenase 18 family, member A1
|
|
ALDH1B1
|
aldehyde dehydrogenase 1 family, member B1
|
|
ALDH1L2
|
aldehyde dehydrogenase 1 family, member L2
|
|
ALDH2
|
aldehyde dehydrogenase 2 family (mitochondrial)
|
|
AP2M1
|
adaptor-related protein complex 2, mu 1 subunit
|
|
ATAD3A
|
ATPase family, AAA domain containing 3A
|
|
ATAD3B
|
ATPase family, AAA domain containing 3B
|
|
ATP5A1
|
ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle
|
|
ATP5B
|
ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide
|
|
ATP5C1
|
ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1
|
|
ATP5F1
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1
|
|
ATP5G1
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9)
|
|
ATP5H
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d
|
|
ATP5L
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G
|
|
C10ORF2
|
chromosome 10 open reading frame 2
|
|
C1QBP
|
complement component 1, q subcomponent binding protein
|
|
C6ORF203
|
chromosome 6 open reading frame 203
|
|
CECR5
|
cat eye syndrome chromosome region, candidate 5
|
|
CHCHD1
|
coiled-coil-helix-coiled-coil-helix domain containing 1
|
|
CLPX
|
caseinolytic mitochondrial matrix peptidase chaperone subunit
|
|
COQ2
|
coenzyme Q2 4-hydroxybenzoate polyprenyltransferase
|
|
COX4I1
|
cytochrome c oxidase subunit IV isoform 1
|
|
CPT2
|
carnitine palmitoyltransferase 2
|
|
DAP3
|
death associated protein 3
|
|
DBT
|
dihydrolipoamide branched chain transacylase E2
|
|
DDX28
|
DEAD (Asp-Glu-Ala-Asp) box polypeptide 28
|
|
DHX30
|
DEAH (Asp-Glu-Ala-His) box helicase 30
|
|
DLD
|
dihydrolipoamide dehydrogenase
|
|
DNAJA3
|
DnaJ (Hsp40) homolog, subfamily A, member 3
|
|
DNAJC19
|
DnaJ (Hsp40) homolog, subfamily C, member 19
|
|
ECH1
|
enoyl CoA hydratase 1, peroxisomal
|
|
ECI1
|
enoyl-CoA delta isomerase 1
|
|
ERAL1
|
Era-like 12S mitochondrial rRNA chaperone 1
|
|
ERLIN2
|
ER lipid raft associated 2
|
|
ETFA
|
electron-transfer-flavoprotein, alpha polypeptide
|
|
FARS2
|
phenylalanyl-tRNA synthetase 2, mitochondrial
|
|
FASTKD1
|
FAST kinase domains 1
|
|
FASTKD2
|
FAST kinase domains 2
|
|
FLAD1
|
flavin adenine dinucleotide synthetase 1
|
|
FXN
|
frataxin
|
|
GADD45GIP1
|
growth arrest and DNA-damage-inducible, gamma interacting protein 1
|
|
GLDC
|
glycine dehydrogenase (decarboxylating)
|
|
GLUD1
|
glutamate dehydrogenase 1
|
|
GRPEL1
|
GrpE-like 1, mitochondrial (E. coli)
|
|
GRPEL2
|
GrpE-like 2, mitochondrial (E. coli)
|
|
GRSF1
|
G-rich RNA sequence binding factor 1
|
|
GTPBP10
|
GTP-binding protein 10 (putative)
|
|
HADHA
|
hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit
|
|
HARS2
|
histidyl-tRNA synthetase 2, mitochondrial
|
|
HK1
|
hexokinase 1
|
|
HN1
|
hematological and neurological expressed 1
|
|
HNRNPDL
|
heterogeneous nuclear ribonucleoprotein D-like
|
|
HSCB
|
HscB mitochondrial iron-sulfur cluster co-chaperone
|
|
HSD17B10
|
hydroxysteroid (17-beta) dehydrogenase 10
|
|
HSPA1B
|
heat shock 70kDa protein 1B
|
|
HSPA9
|
heat shock 70kDa protein 9 (mortalin)
|
|
HSPD1
|
heat shock 60kDa protein 1 (chaperonin)
|
|
ICT1
|
immature colon carcinoma transcript 1
|
|
IGF2BP2
|
insulin-like growth factor 2 mRNA binding protein 2
|
|
IMMT
|
inner membrane protein, mitochondrial
|
|
ISCA1
|
iron-sulfur cluster assembly 1
|
|
KARS
|
lysyl-tRNA synthetase
|
|
KIAA0391
|
KIAA0391
|
|
LDHD
|
lactate dehydrogenase D
|
|
LETM1
|
leucine zipper-EF-hand containing transmembrane protein 1
|
|
LONP1
|
lon peptidase 1, mitochondrial
|
|
LRPPRC
|
leucine-rich pentatricopeptide repeat containing
|
|
MALSU1
|
mitochondrial assembly of ribosomal large subunit 1
|
|
MARK3
|
MAP/microtubule affinity-regulating kinase 3
|
|
MAX
|
MYC associated factor X
|
|
MCAT
|
malonyl CoA:ACP acyltransferase (mitochondrial)
|
|
MCCC2
|
methylcrotonoyl-CoA carboxylase 2 (beta)
|
|
MCU
|
mitochondrial calcium uniporter
|
|
MDM2
|
MDM2 proto-oncogene, E3 ubiquitin protein ligase
|
|
ME2
|
malic enzyme 2, NAD(+)-dependent, mitochondrial
|
|
METTL17
|
methyltransferase like 17
|
|
MMAB
|
methylmalonic aciduria (cobalamin deficiency) cblB type
|
|
MOV10
|
Mov10 RISC complex RNA helicase
|
|
MRM1
|
mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae)
|
|
MRPL1
|
mitochondrial ribosomal protein L1
|
|
MRPL10
|
mitochondrial ribosomal protein L10
|
|
MRPL11
|
mitochondrial ribosomal protein L11
|
|
MRPL12
|
mitochondrial ribosomal protein L12
|
|
MRPL13
|
mitochondrial ribosomal protein L13
|
|
MRPL14
|
mitochondrial ribosomal protein L14
|
|
MRPL15
|
mitochondrial ribosomal protein L15
|
|
MRPL16
|
mitochondrial ribosomal protein L16
|
|
MRPL17
|
mitochondrial ribosomal protein L17
|
|
MRPL18
|
mitochondrial ribosomal protein L18
|
|
MRPL19
|
mitochondrial ribosomal protein L19
|
|
MRPL2
|
mitochondrial ribosomal protein L2
|
|
MRPL20
|
mitochondrial ribosomal protein L20
|
|
MRPL21
|
mitochondrial ribosomal protein L21
|
|
MRPL22
|
mitochondrial ribosomal protein L22
|
|
MRPL24
|
mitochondrial ribosomal protein L24
|
|
MRPL27
|
mitochondrial ribosomal protein L27
|
|
MRPL28
|
mitochondrial ribosomal protein L28
|
|
MRPL3
|
mitochondrial ribosomal protein L3
|
|
MRPL32
|
mitochondrial ribosomal protein L32
|
|
MRPL37
|
mitochondrial ribosomal protein L37
|
|
MRPL39
|
mitochondrial ribosomal protein L39
|
|
MRPL4
|
mitochondrial ribosomal protein L4
|
|
MRPL40
|
mitochondrial ribosomal protein L40
|
|
MRPL41
|
mitochondrial ribosomal protein L41
|
|
MRPL43
|
mitochondrial ribosomal protein L43
|
|
MRPL44
|
mitochondrial ribosomal protein L44
|
|
MRPL46
|
mitochondrial ribosomal protein L46
|
|
MRPL47
|
mitochondrial ribosomal protein L47
|
|
MRPL48
|
mitochondrial ribosomal protein L48
|
|
MRPL49
|
mitochondrial ribosomal protein L49
|
|
MRPL50
|
mitochondrial ribosomal protein L50
|
|
MRPL51
|
mitochondrial ribosomal protein L51
|
|
MRPL54
|
mitochondrial ribosomal protein L54
|
|
MRPL55
|
mitochondrial ribosomal protein L55
|
|
MRPL9
|
mitochondrial ribosomal protein L9
|
|
MRPS10
|
mitochondrial ribosomal protein S10
|
|
MRPS11
|
mitochondrial ribosomal protein S11
|
|
MRPS14
|
mitochondrial ribosomal protein S14
|
|
MRPS15
|
mitochondrial ribosomal protein S15
|
|
MRPS16
|
mitochondrial ribosomal protein S16
|
|
MRPS17
|
mitochondrial ribosomal protein S17
|
|
MRPS18A
|
mitochondrial ribosomal protein S18A
|
|
MRPS18B
|
mitochondrial ribosomal protein S18B
|
|
MRPS2
|
mitochondrial ribosomal protein S2
|
|
MRPS21
|
mitochondrial ribosomal protein S21
|
|
MRPS22
|
mitochondrial ribosomal protein S22
|
|
MRPS23
|
mitochondrial ribosomal protein S23
|
|
MRPS24
|
mitochondrial ribosomal protein S24
|
|
MRPS25
|
mitochondrial ribosomal protein S25
|
|
MRPS26
|
mitochondrial ribosomal protein S26
|
|
MRPS27
|
mitochondrial ribosomal protein S27
|
|
MRPS28
|
mitochondrial ribosomal protein S28
|
|
MRPS30
|
mitochondrial ribosomal protein S30
|
|
MRPS31
|
mitochondrial ribosomal protein S31
|
|
MRPS34
|
mitochondrial ribosomal protein S34
|
|
MRPS35
|
mitochondrial ribosomal protein S35
|
|
MRPS5
|
mitochondrial ribosomal protein S5
|
|
MRPS6
|
mitochondrial ribosomal protein S6
|
|
MRPS7
|
mitochondrial ribosomal protein S7
|
|
MRPS9
|
mitochondrial ribosomal protein S9
|
|
MRRF
|
mitochondrial ribosome recycling factor
|
|
MTG1
|
mitochondrial ribosome-associated GTPase 1
|
|
MTIF2
|
mitochondrial translational initiation factor 2
|
|
MTPAP
|
mitochondrial poly(A) polymerase
|
|
MUT
|
methylmalonyl CoA mutase
|
|
MYC
|
v-myc avian myelocytomatosis viral oncogene homolog
|
|
NDUFA13
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
|
|
NDUFA9
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
|
|
NDUFAF3
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 3
|
|
NDUFS1
|
NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
|
|
NDUFS2
|
NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
|
|
NDUFS3
|
NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
|
|
NDUFS8
|
NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
|
|
NDUFV1
|
NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa
|
|
NEDD8
|
neural precursor cell expressed, developmentally down-regulated 8
|
|
NGRN
|
neugrin, neurite outgrowth associated
|
|
NIPSNAP1
|
nipsnap homolog 1 (C. elegans)
|
|
NME4
|
NME/NM23 nucleoside diphosphate kinase 4
|
|
NOA1
|
nitric oxide associated 1
|
|
NSUN4
|
NOP2/Sun domain family, member 4
|
|
OAT
|
ornithine aminotransferase
|
|
OXA1L
|
oxidase (cytochrome c) assembly 1-like
|
|
PAM16
|
presequence translocase-associated motor 16 homolog (S. cerevisiae)
|
|
PARS2
|
prolyl-tRNA synthetase 2, mitochondrial (putative)
|
|
PCCB
|
propionyl CoA carboxylase, beta polypeptide
|
|
PDK3
|
pyruvate dehydrogenase kinase, isozyme 3
|
|
PGAM5
|
phosphoglycerate mutase family member 5
|
|
PHB
|
prohibitin
|
|
PHB2
|
prohibitin 2
|
|
PMPCA
|
peptidase (mitochondrial processing) alpha
|
|
PNPT1
|
polyribonucleotide nucleotidyltransferase 1
|
|
POLDIP2
|
polymerase (DNA-directed), delta interacting protein 2
|
|
POLRMT
|
polymerase (RNA) mitochondrial (DNA directed)
|
|
PRDX4
|
peroxiredoxin 4
|
|
PRDX5
|
peroxiredoxin 5
|
|
PTCD1
|
pentatricopeptide repeat domain 1
|
|
PTCD3
|
pentatricopeptide repeat domain 3
|
|
PUS1
|
pseudouridylate synthase 1
|
|
PUSL1
|
pseudouridylate synthase-like 1
|
|
PYCR2
|
pyrroline-5-carboxylate reductase family, member 2
|
|
RARS2
|
arginyl-tRNA synthetase 2, mitochondrial
|
|
RBFA
|
ribosome binding factor A (putative)
|
|
RNMTL1
|
RNA methyltransferase like 1
|
|
RPA2
|
replication protein A2, 32kDa
|
|
RPUSD3
|
RNA pseudouridylate synthase domain containing 3
|
|
RPUSD4
|
RNA pseudouridylate synthase domain containing 4
|
|
SARS2
|
seryl-tRNA synthetase 2, mitochondrial
|
|
SDHA
|
succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
|
|
SFXN1
|
sideroflexin 1
|
|
SHMT2
|
serine hydroxymethyltransferase 2 (mitochondrial)
|
|
SLC25A1
|
solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1
|
|
SLC25A10
|
solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10
|
|
SLC25A11
|
solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11
|
|
SLC25A12
|
solute carrier family 25 (aspartate/glutamate carrier), member 12
|
|
SLC25A13
|
solute carrier family 25 (aspartate/glutamate carrier), member 13
|
|
SLC25A18
|
solute carrier family 25 (glutamate carrier), member 18
|
|
SLC25A3
|
solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3
|
|
SLC25A4
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
|
|
SLC25A5
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5
|
|
SLC25A6
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 6
|
|
SLIRP
|
SRA stem-loop interacting RNA binding protein
|
|
SSBP1
|
single-stranded DNA binding protein 1, mitochondrial
|
|
STOML2
|
stomatin (EPB72)-like 2
|
|
SUCLA2
|
succinate-CoA ligase, ADP-forming, beta subunit
|
|
SUMO1
|
small ubiquitin-like modifier 1
|
|
SUMO2
|
small ubiquitin-like modifier 2
|
|
SUMO3
|
small ubiquitin-like modifier 3
|
|
SUPV3L1
|
suppressor of var1, 3-like 1 (S. cerevisiae)
|
|
TAF1
|
TAF1 RNA polymerase II, TATA box binding protein (TBP)-associated factor, 250kDa
|
|
TARS2
|
threonyl-tRNA synthetase 2, mitochondrial (putative)
|
|
TEFM
|
transcription elongation factor, mitochondrial
|
|
TFAM
|
transcription factor A, mitochondrial
|
|
TFB1M
|
transcription factor B1, mitochondrial
|
|
THNSL1
|
threonine synthase-like 1 (S. cerevisiae)
|
|
TIMM17A
|
translocase of inner mitochondrial membrane 17 homolog A (yeast)
|
|
TIMM17B
|
translocase of inner mitochondrial membrane 17 homolog B (yeast)
|
|
TIMM21
|
translocase of inner mitochondrial membrane 21 homolog (yeast)
|
|
TIMM23
|
translocase of inner mitochondrial membrane 23 homolog (yeast)
|
|
TIMM44
|
translocase of inner mitochondrial membrane 44 homolog (yeast)
|
|
TIMM50
|
translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae)
|
|
TMLHE
|
trimethyllysine hydroxylase, epsilon
|
|
TOP1
|
topoisomerase (DNA) I
|
|
TRMT10C
|
tRNA methyltransferase 10 homolog C (S. cerevisiae)
|
|
TRUB2
|
TruB pseudouridine (psi) synthase family member 2
|
|
TUFM
|
Tu translation elongation factor, mitochondrial
|
|
UBC
|
ubiquitin C
|
|
UQCRC1
|
ubiquinol-cytochrome c reductase core protein I
|
|
UQCRC2
|
ubiquinol-cytochrome c reductase core protein II
|
|
UQCRFS1
|
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
|
|
VARS2
|
valyl-tRNA synthetase 2, mitochondrial
|
|
VDAC1
|
voltage-dependent anion channel 1
|
|
VDAC3
|
voltage-dependent anion channel 3
|
|
WBSCR16
|
Williams-Beuren syndrome chromosome region 16
|
|
WTAP
|
Wilms tumor 1 associated protein
|
|
YARS2
|
tyrosyl-tRNA synthetase 2, mitochondrial
|
|
YME1L1
|
YME1-like 1 ATPase
|
