Porphyrin metabolism Gene Set

Dataset KEGG Pathways 2026
Category structural or functional annotations
Type pathway
Description Porphyrins are a group of chemical compounds with the backbone ring structure consisting of four linked pyrrole units. Metal complexes of porphyrins, as well as those of corrinoids with the one-carbon shorter ring structure, play important biological roles. They include iron-containing heme, magnesium-containing chlorophyll, nickel-containing coenzyme F430 and cobalt-containing cobamide (such as vitamin B12 coenzyme) as shown in this map. (Kyoto Encyclopedia of Genes and Genomes, hsa00860)
External Link https://www.kegg.jp/entry/hsa00860
Similar Terms
Downloads & Tools

Genes

46 proteins participating in the Porphyrin metabolism pathway from the KEGG Pathways 2026 dataset.

Symbol Name
ALAD aminolevulinate dehydratase
ALAS1 5'-aminolevulinate synthase 1
ALAS2 5'-aminolevulinate synthase 2
BLVRA biliverdin reductase A
BLVRB biliverdin reductase B
COX10 COX10 heme A:farnesyltransferase cytochrome c oxidase assembly factor
COX15 cytochrome c oxidase assembly homolog 15 (yeast)
CP ceruloplasmin (ferroxidase)
CPOX coproporphyrinogen oxidase
EARS2 glutamyl-tRNA synthetase 2, mitochondrial
EPRS1 glutamyl-prolyl-tRNA synthetase 1
FECH ferrochelatase
FTH1 ferritin, heavy polypeptide 1
FTL ferritin, light polypeptide
FTMT ferritin mitochondrial
FXN frataxin
GUSB glucuronidase, beta
HCCS holocytochrome c synthase
HEPH hephaestin
HEPHL1 hephaestin-like 1
HMBS hydroxymethylbilane synthase
HMOX1 heme oxygenase 1
HMOX2 heme oxygenase 2
MMAB methylmalonic aciduria (cobalamin deficiency) cblB type
PPOX protoporphyrinogen oxidase
UGT1A1 UDP glucuronosyltransferase 1 family, polypeptide A1
UGT1A10 UDP glucuronosyltransferase 1 family, polypeptide A10
UGT1A3 UDP glucuronosyltransferase 1 family, polypeptide A3
UGT1A4 UDP glucuronosyltransferase 1 family, polypeptide A4
UGT1A5 UDP glucuronosyltransferase 1 family, polypeptide A5
UGT1A6 UDP glucuronosyltransferase 1 family, polypeptide A6
UGT1A7 UDP glucuronosyltransferase 1 family, polypeptide A7
UGT1A8 UDP glucuronosyltransferase 1 family, polypeptide A8
UGT1A9 UDP glucuronosyltransferase 1 family, polypeptide A9
UGT2A1 UDP glucuronosyltransferase 2 family, polypeptide A1, complex locus
UGT2A2 UDP glucuronosyltransferase 2 family, polypeptide A2
UGT2A3 UDP glucuronosyltransferase 2 family, polypeptide A3
UGT2B10 UDP glucuronosyltransferase 2 family, polypeptide B10
UGT2B11 UDP glucuronosyltransferase 2 family, polypeptide B11
UGT2B15 UDP glucuronosyltransferase 2 family, polypeptide B15
UGT2B17 UDP glucuronosyltransferase 2 family, polypeptide B17
UGT2B28 UDP glucuronosyltransferase 2 family, polypeptide B28
UGT2B4 UDP glucuronosyltransferase 2 family, polypeptide B4
UGT2B7 UDP glucuronosyltransferase 2 family, polypeptide B7
UROD uroporphyrinogen decarboxylase
UROS uroporphyrinogen III synthase