Respirasome Gene Set

Dataset COMPARTMENTS Curated Protein Localization Evidence Scores 2025
Category structural or functional annotations
Type cellular component
External Link http://amigo.geneontology.org/amigo/term/GO:0070469
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65 proteins localized to the Respirasome cellular component from the COMPARTMENTS Curated Protein Localization Evidence Scores 2025 dataset.

Symbol Name Standardized Value
NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 5.0
NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 5.0
NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 5.0
UQCRC2 ubiquinol-cytochrome c reductase core protein II 5.0
UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 5.0
NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 5.0
NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 5.0
NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 5.0
NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 5.0
NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 5.0
NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5 5.0
NDUFA4 NDUFA4, mitochondrial complex associated 5.0
NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 5.0
NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 5.0
NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 5.0
NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 5.0
NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 5.0
NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 5.0
NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 5.0
NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 5.0
NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 5.0
NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 5.0
COX7C cytochrome c oxidase subunit VIIc 5.0
NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 5.0
NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 5.0
NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 5.0
NDUFA7 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDa 5.0
NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 5.0
NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 5.0
SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 5.0
SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 5.0
SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 5.0
SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 5.0
NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 5.0
NDUFA13 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13 5.0
NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 5.0
NDUFA11 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa 5.0
NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 5.0
COX5A cytochrome c oxidase subunit Va 5.0
NDUFV2 NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa 5.0
NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 5.0
NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 5.0
NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 5.0
NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 5.0
NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 5.0
NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 5.0
BCS1L BC1 (ubiquinol-cytochrome c reductase) synthesis-like 4.0
COX4I1 cytochrome c oxidase subunit IV isoform 1 4.0
COX7B2 cytochrome c oxidase subunit VIIb2 3.0
COX6A1 cytochrome c oxidase subunit VIa polypeptide 1 3.0
COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 3.0
WDR93 WD repeat domain 93 3.0
COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 3.0
COX8C cytochrome c oxidase subunit VIIIC 3.0
COX4I2 cytochrome c oxidase subunit IV isoform 2 (lung) 3.0
NDUFC2-KCTD14 NDUFC2-KCTD14 readthrough 3.0
UQCRHL ubiquinol-cytochrome c reductase hinge protein-like 3.0
UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 3.0
COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 3.0
NDUFA4L2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4-like 2 3.0
UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 3.0
UQCRH ubiquinol-cytochrome c reductase hinge protein 3.0
UQCRB ubiquinol-cytochrome c reductase binding protein 3.0
CCNI cyclin I 3.0
COX7B cytochrome c oxidase subunit VIIb 3.0