Sphingolipid metabolism Gene Set

Dataset KEGG Pathways 2026
Category structural or functional annotations
Type pathway
External Link https://www.kegg.jp/entry/hsa00600
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Genes

54 proteins participating in the Sphingolipid metabolism pathway from the KEGG Pathways 2026 dataset.

Symbol Name
ACER1 alkaline ceramidase 1
ACER2 alkaline ceramidase 2
ACER3 alkaline ceramidase 3
ARSA arylsulfatase A
ASAH1 N-acylsphingosine amidohydrolase (acid ceramidase) 1
ASAH2 N-acylsphingosine amidohydrolase (non-lysosomal ceramidase) 2
B4GALNT1 beta-1,4-N-acetyl-galactosaminyl transferase 1
B4GALT5 UDP-Gal:betaGlcNAc beta 1,4- galactosyltransferase, polypeptide 5
B4GALT6 UDP-Gal:betaGlcNAc beta 1,4- galactosyltransferase, polypeptide 6
CERK ceramide kinase
CERS1 ceramide synthase 1
CERS2 ceramide synthase 2
CERS3 ceramide synthase 3
CERS4 ceramide synthase 4
CERS6 ceramide synthase 6
DEGS1 delta(4)-desaturase, sphingolipid 1
DEGS2 delta(4)-desaturase, sphingolipid 2
EGFL7 EGF-like-domain, multiple 7
ENPP7 ectonucleotide pyrophosphatase/phosphodiesterase 7
GAL3ST1 galactose-3-O-sulfotransferase 1
GALC galactosylceramidase
GBA1 glucosylceramidase beta 1
GBA2 glucosidase, beta (bile acid) 2
GLB1 galactosidase, beta 1
GM2A GM2 ganglioside activator
HEXA hexosaminidase A (alpha polypeptide)
HEXB hexosaminidase B (beta polypeptide)
KDSR 3-ketodihydrosphingosine reductase
NAT8 N-acetyltransferase 8 (GCN5-related, putative)
NEU2 sialidase 2 (cytosolic sialidase)
NEU3 sialidase 3 (membrane sialidase)
NEU4 sialidase 4
PLPP1 phospholipid phosphatase 1
PLPP2 phospholipid phosphatase 2
PLPP3 phospholipid phosphatase 3
PSAPL1 prosaposin-like 1 (gene/pseudogene)
SAMD8 sterile alpha motif domain containing 8
SFTPA2 surfactant protein A2
SGMS1 sphingomyelin synthase 1
SGMS2 sphingomyelin synthase 2
SGPL1 sphingosine-1-phosphate lyase 1
SGPP1 sphingosine-1-phosphate phosphatase 1
SGPP2 sphingosine-1-phosphate phosphatase 2
SMPD1 sphingomyelin phosphodiesterase 1, acid lysosomal
SMPD2 sphingomyelin phosphodiesterase 2, neutral membrane (neutral sphingomyelinase)
SMPD3 sphingomyelin phosphodiesterase 3, neutral membrane (neutral sphingomyelinase II)
SMPD4 sphingomyelin phosphodiesterase 4, neutral membrane (neutral sphingomyelinase-3)
SPHK1 sphingosine kinase 1
SPHK2 sphingosine kinase 2
SPTLC1 serine palmitoyltransferase, long chain base subunit 1
SPTLC2 serine palmitoyltransferase, long chain base subunit 2
SPTLC3 serine palmitoyltransferase, long chain base subunit 3
UGCG UDP-glucose ceramide glucosyltransferase
UGT8 UDP glycosyltransferase 8