Spliceosome Gene Set

Dataset KEGG Pathways 2026
Category structural or functional annotations
Type pathway
Description After transcription, eukaryotic mRNA precursors contain protein-coding exons and noncoding introns. In the following splicing, introns are excised and exons are joined by a macromolecular complex, the spliceosome. The standard spliceosome is made up of five small nuclear ribonucleoproteins (snRNPs), U1, U2, U4, U5, and U6 snRNPs, and several spliceosome-associated proteins (SAPs). Spliceosomes are not a simple stable complex, but a dynamic family of particles that assemble on the mRNA precursor and help fold it into a conformation that allows transesterification to proceed. Various spliceosome forms (e.g. A-, B- and C-complexes) have been identified. (Kyoto Encyclopedia of Genes and Genomes, hsa03040)
External Link https://www.kegg.jp/entry/hsa03040
Similar Terms
Downloads & Tools

Genes

144 proteins participating in the Spliceosome pathway from the KEGG Pathways 2026 dataset.

Symbol Name
ACIN1 apoptotic chromatin condensation inducer 1
ALYREF Aly/REF export factor
AQR aquarius intron-binding spliceosomal factor
BCAS2 breast carcinoma amplified sequence 2
BUD13 BUD13 homolog (S. cerevisiae)
BUD31 BUD31 homolog (S. cerevisiae)
CASC3 cancer susceptibility candidate 3
CCDC12 coiled-coil domain containing 12
CDC40 cell division cycle 40
CDC5L cell division cycle 5-like
CHERP calcium homeostasis endoplasmic reticulum protein
CRNKL1 crooked neck pre-mRNA splicing factor 1
CTNNBL1 catenin, beta like 1
CWC15 CWC15 spliceosome-associated protein
CWC25 CWC25 spliceosome-associated protein homolog (S. cerevisiae)
DDX23 DEAD (Asp-Glu-Ala-Asp) box polypeptide 23
DDX39B DEAD (Asp-Glu-Ala-Asp) box polypeptide 39B
DDX42 DEAD (Asp-Glu-Ala-Asp) box helicase 42
DDX46 DEAD (Asp-Glu-Ala-Asp) box polypeptide 46
DDX5 DEAD (Asp-Glu-Ala-Asp) box helicase 5
DHX15 DEAH (Asp-Glu-Ala-His) box helicase 15
DHX16 DEAH (Asp-Glu-Ala-His) box polypeptide 16
DHX38 DEAH (Asp-Glu-Ala-His) box polypeptide 38
DHX8 DEAH (Asp-Glu-Ala-His) box polypeptide 8
EFTUD2 elongation factor Tu GTP binding domain containing 2
EIF4A3 eukaryotic translation initiation factor 4A3
FUS FUS RNA binding protein
GPKOW G patch domain and KOW motifs
HNRNPA1 heterogeneous nuclear ribonucleoprotein A1
HNRNPA1L2 heterogeneous nuclear ribonucleoprotein A1-like 2
HNRNPA1L3 heterogeneous nuclear ribonucleoprotein A1 like 3
HNRNPA3 heterogeneous nuclear ribonucleoprotein A3
HNRNPC heterogeneous nuclear ribonucleoprotein C (C1/C2)
HNRNPCL1 heterogeneous nuclear ribonucleoprotein C-like 1
HNRNPCL3 heterogeneous nuclear ribonucleoprotein C-like 3
HNRNPCL4 heterogeneous nuclear ribonucleoprotein C-like 4
HNRNPK heterogeneous nuclear ribonucleoprotein K
HNRNPM heterogeneous nuclear ribonucleoprotein M
HNRNPU heterogeneous nuclear ribonucleoprotein U (scaffold attachment factor A)
HSPA1A heat shock 70kDa protein 1A
HSPA1B heat shock 70kDa protein 1B
HSPA1L heat shock 70kDa protein 1-like
HSPA6 heat shock 70kDa protein 6 (HSP70B')
HSPA8 heat shock 70kDa protein 8
ISY1-RAB43 ISY1-RAB43 readthrough
LOC102724594 splicing factor U2AF 35 kDa subunit
LSM2 LSM2 homolog, U6 small nuclear RNA associated (S. cerevisiae)
LSM3 LSM3 homolog, U6 small nuclear RNA associated (S. cerevisiae)
LSM4 LSM4 homolog, U6 small nuclear RNA associated (S. cerevisiae)
LSM5 LSM5 homolog, U6 small nuclear RNA associated (S. cerevisiae)
LSM6 LSM6 homolog, U6 small nuclear RNA associated (S. cerevisiae)
LSM7 LSM7 homolog, U6 small nuclear RNA associated (S. cerevisiae)
LSM8 LSM8 homolog, U6 small nuclear RNA associated (S. cerevisiae)
MAGOHB mago-nashi homolog B (Drosophila)
NCBP1 nuclear cap binding protein subunit 1, 80kDa
NCBP2 nuclear cap binding protein subunit 2, 20kDa
NCBP2L nuclear cap binding protein subunit 2-like
PCBP1 poly(rC) binding protein 1
PHF5A PHD finger protein 5A
PLRG1 pleiotropic regulator 1
PPIE peptidylprolyl isomerase E (cyclophilin E)
PPIH peptidylprolyl isomerase H (cyclophilin H)
PPIL1 peptidylprolyl isomerase (cyclophilin)-like 1
PQBP1 polyglutamine binding protein 1
PRPF18 pre-mRNA processing factor 18
PRPF19 pre-mRNA processing factor 19
PRPF3 pre-mRNA processing factor 3
PRPF31 pre-mRNA processing factor 31
PRPF38A pre-mRNA processing factor 38A
PRPF38B pre-mRNA processing factor 38B
PRPF4 pre-mRNA processing factor 4
PRPF40A PRP40 pre-mRNA processing factor 40 homolog A (S. cerevisiae)
PRPF40B PRP40 pre-mRNA processing factor 40 homolog B (S. cerevisiae)
PRPF6 pre-mRNA processing factor 6
PRPF8 pre-mRNA processing factor 8
PUF60 poly-U binding splicing factor 60KDa
RBM17 RNA binding motif protein 17
RBM22 RNA binding motif protein 22
RBM25 RNA binding motif protein 25
RBM8A RNA binding motif protein 8A
RBMX RNA binding motif protein, X-linked
RBMX2 RNA binding motif protein, X-linked 2
RBMXL1 RNA binding motif protein, X-linked-like 1
RP9 retinitis pigmentosa 9 (autosomal dominant)
SART1 squamous cell carcinoma antigen recognized by T cells
SF1 splicing factor 1
SF3A1 splicing factor 3a, subunit 1, 120kDa
SF3A2 splicing factor 3a, subunit 2, 66kDa
SF3A3 splicing factor 3a, subunit 3, 60kDa
SF3B1 splicing factor 3b, subunit 1, 155kDa
SF3B2 splicing factor 3b, subunit 2, 145kDa
SF3B3 splicing factor 3b, subunit 3, 130kDa
SF3B4 splicing factor 3b, subunit 4, 49kDa
SF3B5 splicing factor 3b, subunit 5, 10kDa
SF3B6 splicing factor 3b, subunit 6, 14kDa
SLU7 SLU7 splicing factor homolog (S. cerevisiae)
SMNDC1 survival motor neuron domain containing 1
SNIP1 Smad nuclear interacting protein 1
SNRNP200 small nuclear ribonucleoprotein 200kDa (U5)
SNRNP27 small nuclear ribonucleoprotein 27kDa (U4/U6.U5)
SNRNP40 small nuclear ribonucleoprotein 40kDa (U5)
SNRNP70 small nuclear ribonucleoprotein 70kDa (U1)
SNRPA small nuclear ribonucleoprotein polypeptide A
SNRPA1 small nuclear ribonucleoprotein polypeptide A'
SNRPB small nuclear ribonucleoprotein polypeptides B and B1
SNRPB2 small nuclear ribonucleoprotein polypeptide B
SNRPC small nuclear ribonucleoprotein polypeptide C
SNRPD2 small nuclear ribonucleoprotein D2 polypeptide 16.5kDa
SNRPD3 small nuclear ribonucleoprotein D3 polypeptide 18kDa
SNRPE small nuclear ribonucleoprotein polypeptide E
SNRPF small nuclear ribonucleoprotein polypeptide F
SNRPG small nuclear ribonucleoprotein polypeptide G
SNU13 small nuclear ribonucleoprotein 13
SNW1 SNW domain containing 1
SRSF1 serine/arginine-rich splicing factor 1
SRSF10 serine/arginine-rich splicing factor 10
SRSF2 serine/arginine-rich splicing factor 2
SRSF3 serine/arginine-rich splicing factor 3
SRSF4 serine/arginine-rich splicing factor 4
SRSF5 serine/arginine-rich splicing factor 5
SRSF6 serine/arginine-rich splicing factor 6
SRSF7 serine/arginine-rich splicing factor 7
SRSF8 serine/arginine-rich splicing factor 8
SRSF9 serine/arginine-rich splicing factor 9
SYF2 SYF2 pre-mRNA-splicing factor
TCERG1 transcription elongation regulator 1
THOC1 THO complex 1
THOC2 THO complex 2
THOC3 THO complex 3
THOC5 THO complex 5
THOC6 THO complex 6
THOC7 THO complex 7
TRA2A transformer 2 alpha homolog (Drosophila)
TRA2B transformer 2 beta homolog (Drosophila)
TXNL4A thioredoxin-like 4A
U2AF1 U2 small nuclear RNA auxiliary factor 1
U2AF1L4 U2 small nuclear RNA auxiliary factor 1-like 4
U2AF2 U2 small nuclear RNA auxiliary factor 2
U2SURP U2 snRNP-associated SURP domain containing
USP39 ubiquitin specific peptidase 39
WBP11 WW domain binding protein 11
XAB2 XPA binding protein 2
YJU2 YJU2 splicing factor homolog
ZMAT2 zinc finger, matrin-type 2