Symbol |
Name |
ACO2
|
aconitase 2, mitochondrial
|
ADHFE1
|
alcohol dehydrogenase, iron containing, 1
|
ATP5A1
|
ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle
|
ATP5B
|
ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide
|
ATP5C1
|
ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1
|
ATP5D
|
ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit
|
ATP5E
|
ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit
|
ATP5F1
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1
|
ATP5G1
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9)
|
ATP5G2
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9)
|
ATP5G3
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9)
|
ATP5H
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d
|
ATP5I
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E
|
ATP5J
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6
|
ATP5J2
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2
|
ATP5L
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G
|
ATP5O
|
ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit
|
ATP5S
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit s (factor B)
|
BSG
|
basigin (Ok blood group)
|
COX11
|
COX11 cytochrome c oxidase copper chaperone
|
COX14
|
COX14 cytochrome c oxidase assembly factor
|
COX16
|
COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)
|
COX18
|
COX18 cytochrome c oxidase assembly factor
|
COX19
|
COX19 cytochrome c oxidase assembly factor
|
COX20
|
COX20 cytochrome c oxidase assembly factor
|
COX4I1
|
cytochrome c oxidase subunit IV isoform 1
|
COX5A
|
cytochrome c oxidase subunit Va
|
COX5B
|
cytochrome c oxidase subunit Vb
|
COX6A1
|
cytochrome c oxidase subunit VIa polypeptide 1
|
COX6B1
|
cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous)
|
COX6C
|
cytochrome c oxidase subunit VIc
|
COX7A2L
|
cytochrome c oxidase subunit VIIa polypeptide 2 like
|
COX7B
|
cytochrome c oxidase subunit VIIb
|
COX7C
|
cytochrome c oxidase subunit VIIc
|
COX8A
|
cytochrome c oxidase subunit VIIIA (ubiquitous)
|
CS
|
citrate synthase
|
CYC1
|
cytochrome c-1
|
CYCS
|
cytochrome c, somatic
|
D2HGDH
|
D-2-hydroxyglutarate dehydrogenase
|
DLAT
|
dihydrolipoamide S-acetyltransferase
|
DLD
|
dihydrolipoamide dehydrogenase
|
DLST
|
dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
|
ETFA
|
electron-transfer-flavoprotein, alpha polypeptide
|
ETFB
|
electron-transfer-flavoprotein, beta polypeptide
|
ETFDH
|
electron-transferring-flavoprotein dehydrogenase
|
FH
|
fumarate hydratase
|
IDH2
|
isocitrate dehydrogenase 2 (NADP+), mitochondrial
|
IDH3A
|
isocitrate dehydrogenase 3 (NAD+) alpha
|
IDH3B
|
isocitrate dehydrogenase 3 (NAD+) beta
|
IDH3G
|
isocitrate dehydrogenase 3 (NAD+) gamma
|
L2HGDH
|
L-2-hydroxyglutarate dehydrogenase
|
LDHA
|
lactate dehydrogenase A
|
LDHB
|
lactate dehydrogenase B
|
LRPPRC
|
leucine-rich pentatricopeptide repeat containing
|
MDH2
|
malate dehydrogenase 2, NAD (mitochondrial)
|
MPC1
|
mitochondrial pyruvate carrier 1
|
MPC2
|
mitochondrial pyruvate carrier 2
|
NDUFA1
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
|
NDUFA10
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
|
NDUFA11
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa
|
NDUFA12
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12
|
NDUFA13
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
|
NDUFA2
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
|
NDUFA3
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa
|
NDUFA4
|
NDUFA4, mitochondrial complex associated
|
NDUFA5
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5
|
NDUFA6
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa
|
NDUFA7
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDa
|
NDUFA8
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
|
NDUFA9
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
|
NDUFAB1
|
NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
|
NDUFB1
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa
|
NDUFB10
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa
|
NDUFB11
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa
|
NDUFB2
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa
|
NDUFB3
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa
|
NDUFB4
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa
|
NDUFB5
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa
|
NDUFB6
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa
|
NDUFB7
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa
|
NDUFB8
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa
|
NDUFB9
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa
|
NDUFC1
|
NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa
|
NDUFC2
|
NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa
|
NDUFS1
|
NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
|
NDUFS2
|
NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
|
NDUFS3
|
NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
|
NDUFS4
|
NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
|
NDUFS5
|
NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)
|
NDUFS6
|
NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)
|
NDUFS7
|
NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
|
NDUFS8
|
NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
|
NDUFV1
|
NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa
|
NDUFV2
|
NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa
|
NDUFV3
|
NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa
|
NNT
|
nicotinamide nucleotide transhydrogenase
|
OGDH
|
oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
|
PDHA1
|
pyruvate dehydrogenase (lipoamide) alpha 1
|
PDHB
|
pyruvate dehydrogenase (lipoamide) beta
|
PDHX
|
pyruvate dehydrogenase complex, component X
|
PDK1
|
pyruvate dehydrogenase kinase, isozyme 1
|
PDK2
|
pyruvate dehydrogenase kinase, isozyme 2
|
PDK3
|
pyruvate dehydrogenase kinase, isozyme 3
|
PDK4
|
pyruvate dehydrogenase kinase, isozyme 4
|
PDP1
|
pyruvate dehyrogenase phosphatase catalytic subunit 1
|
PDP2
|
pyruvate dehyrogenase phosphatase catalytic subunit 2
|
PDPR
|
pyruvate dehydrogenase phosphatase regulatory subunit
|
PPARD
|
peroxisome proliferator-activated receptor delta
|
RXRA
|
retinoid X receptor, alpha
|
SCO1
|
SCO1 cytochrome c oxidase assembly protein
|
SCO2
|
SCO2 cytochrome c oxidase assembly protein
|
SDHA
|
succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
|
SDHB
|
succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
|
SDHC
|
succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa
|
SDHD
|
succinate dehydrogenase complex, subunit D, integral membrane protein
|
SLC16A1
|
solute carrier family 16 (monocarboxylate transporter), member 1
|
SLC16A3
|
solute carrier family 16 (monocarboxylate transporter), member 3
|
SLC16A8
|
solute carrier family 16 (monocarboxylate transporter), member 8
|
SUCLA2
|
succinate-CoA ligase, ADP-forming, beta subunit
|
SUCLG1
|
succinate-CoA ligase, alpha subunit
|
SUCLG2
|
succinate-CoA ligase, GDP-forming, beta subunit
|
SURF1
|
surfeit 1
|
TACO1
|
translational activator of mitochondrially encoded cytochrome c oxidase I
|
UCP1
|
uncoupling protein 1 (mitochondrial, proton carrier)
|
UCP2
|
uncoupling protein 2 (mitochondrial, proton carrier)
|
UCP3
|
uncoupling protein 3 (mitochondrial, proton carrier)
|
UQCR10
|
ubiquinol-cytochrome c reductase, complex III subunit X
|
UQCR11
|
ubiquinol-cytochrome c reductase, complex III subunit XI
|
UQCRB
|
ubiquinol-cytochrome c reductase binding protein
|
UQCRC1
|
ubiquinol-cytochrome c reductase core protein I
|
UQCRC2
|
ubiquinol-cytochrome c reductase core protein II
|
UQCRFS1
|
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
|
UQCRH
|
ubiquinol-cytochrome c reductase hinge protein
|
UQCRQ
|
ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa
|