Valine, leucine and isoleucine degradation Gene Set

Dataset KEGG Pathways 2026
Category structural or functional annotations
Type pathway
Description (Kyoto Encyclopedia of Genes and Genomes, hsa00280)
External Link https://www.kegg.jp/entry/hsa00280
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Genes

48 proteins participating in the Valine, leucine and isoleucine degradation pathway from the KEGG Pathways 2026 dataset.

Symbol Name
AACS acetoacetyl-CoA synthetase
ABAT 4-aminobutyrate aminotransferase
ACAA1 acetyl-CoA acyltransferase 1
ACAA2 acetyl-CoA acyltransferase 2
ACAD8 acyl-CoA dehydrogenase family, member 8
ACADM acyl-CoA dehydrogenase, C-4 to C-12 straight chain
ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain
ACADSB acyl-CoA dehydrogenase, short/branched chain
ACSF3 acyl-CoA synthetase family member 3
AGXT2 alanine--glyoxylate aminotransferase 2
ALDH1B1 aldehyde dehydrogenase 1 family, member B1
ALDH2 aldehyde dehydrogenase 2 family (mitochondrial)
ALDH3A2 aldehyde dehydrogenase 3 family, member A2
ALDH6A1 aldehyde dehydrogenase 6 family, member A1
ALDH7A1 aldehyde dehydrogenase 7 family, member A1
ALDH9A1 aldehyde dehydrogenase 9 family, member A1
AOX1 aldehyde oxidase 1
AUH AU RNA binding protein/enoyl-CoA hydratase
BCAT1 branched chain amino-acid transaminase 1, cytosolic
BCAT2 branched chain amino-acid transaminase 2, mitochondrial
BCKDHA branched chain keto acid dehydrogenase E1, alpha polypeptide
BCKDHB branched chain keto acid dehydrogenase E1, beta polypeptide
DBT dihydrolipoamide branched chain transacylase E2
ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial
EHHADH enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase
HADH hydroxyacyl-CoA dehydrogenase
HADHA hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit
HADHB hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit
HIBADH 3-hydroxyisobutyrate dehydrogenase
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
HMGCL 3-hydroxymethyl-3-methylglutaryl-CoA lyase
HMGCLL1 3-hydroxymethyl-3-methylglutaryl-CoA lyase-like 1
HMGCS1 3-hydroxy-3-methylglutaryl-CoA synthase 1 (soluble)
HMGCS2 3-hydroxy-3-methylglutaryl-CoA synthase 2 (mitochondrial)
HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10
IL4I1 interleukin 4 induced 1
IVD isovaleryl-CoA dehydrogenase
LDHD lactate dehydrogenase D
MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha)
MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta)
MCEE methylmalonyl CoA epimerase
MMUT methylmalonyl-CoA mutase
OXCT1 3-oxoacid CoA transferase 1
OXCT2 3-oxoacid CoA transferase 2
PCCA propionyl CoA carboxylase, alpha polypeptide
PCCB propionyl CoA carboxylase, beta polypeptide
SOAT1 sterol O-acyltransferase 1
SOAT2 sterol O-acyltransferase 2