| Symbol |
Name |
|
AADAT
|
aminoadipate aminotransferase
|
|
AASS
|
aminoadipate-semialdehyde synthase
|
|
ABAT
|
4-aminobutyrate aminotransferase
|
|
ACAD8
|
acyl-CoA dehydrogenase family, member 8
|
|
ACADSB
|
acyl-CoA dehydrogenase, short/branched chain
|
|
ACAT1
|
acetyl-CoA acetyltransferase 1
|
|
ACMSD
|
aminocarboxymuconate semialdehyde decarboxylase
|
|
AFMID
|
arylformamidase
|
|
AGXT
|
alanine-glyoxylate aminotransferase
|
|
AGXT2
|
alanine--glyoxylate aminotransferase 2
|
|
AHCY
|
adenosylhomocysteinase
|
|
ALDH1L1
|
aldehyde dehydrogenase 1 family, member L1
|
|
ALDH1L2
|
aldehyde dehydrogenase 1 family, member L2
|
|
ALDH4A1
|
aldehyde dehydrogenase 4 family, member A1
|
|
ALDH5A1
|
aldehyde dehydrogenase 5 family, member A1
|
|
ALDH6A1
|
aldehyde dehydrogenase 6 family, member A1
|
|
ALDH7A1
|
aldehyde dehydrogenase 7 family, member A1
|
|
AMDHD1
|
amidohydrolase domain containing 1
|
|
AMT
|
aminomethyltransferase
|
|
ARG1
|
arginase 1
|
|
ASL
|
argininosuccinate lyase
|
|
ASPA
|
aspartoacylase
|
|
ASRGL1
|
asparaginase like 1
|
|
AUH
|
AU RNA binding protein/enoyl-CoA hydratase
|
|
BCAT1
|
branched chain amino-acid transaminase 1, cytosolic
|
|
BCAT2
|
branched chain amino-acid transaminase 2, mitochondrial
|
|
BCKDHA
|
branched chain keto acid dehydrogenase E1, alpha polypeptide
|
|
BCKDHB
|
branched chain keto acid dehydrogenase E1, beta polypeptide
|
|
BCKDK
|
branched chain ketoacid dehydrogenase kinase
|
|
CAD
|
carbamoyl-phosphate synthetase 2, aspartate transcarbamylase, and dihydroorotase
|
|
CCBL1
|
cysteine conjugate-beta lyase, cytoplasmic
|
|
CCBL2
|
cysteine conjugate-beta lyase 2
|
|
CDO1
|
cysteine dioxygenase type 1
|
|
CPS1
|
carbamoyl-phosphate synthase 1, mitochondrial
|
|
CSAD
|
cysteine sulfinic acid decarboxylase
|
|
CTH
|
cystathionine gamma-lyase
|
|
DAO
|
D-amino-acid oxidase
|
|
DBT
|
dihydrolipoamide branched chain transacylase E2
|
|
DDAH1
|
dimethylarginine dimethylaminohydrolase 1
|
|
DDAH2
|
dimethylarginine dimethylaminohydrolase 2
|
|
DDO
|
D-aspartate oxidase
|
|
DLD
|
dihydrolipoamide dehydrogenase
|
|
DLST
|
dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
|
|
DTD1
|
D-tyrosyl-tRNA deacylase 1
|
|
DTD2
|
D-tyrosyl-tRNA deacylase 2 (putative)
|
|
ENOSF1
|
enolase superfamily member 1
|
|
ETHE1
|
ethylmalonic encephalopathy 1
|
|
FAH
|
fumarylacetoacetate hydrolase (fumarylacetoacetase)
|
|
FTCD
|
formimidoyltransferase cyclodeaminase
|
|
GAD1
|
glutamate decarboxylase 1 (brain, 67kDa)
|
|
GAD2
|
glutamate decarboxylase 2 (pancreatic islets and brain, 65kDa)
|
|
GCAT
|
glycine C-acetyltransferase
|
|
GCDH
|
glutaryl-CoA dehydrogenase
|
|
GCSH
|
glycine cleavage system protein H (aminomethyl carrier)
|
|
GLDC
|
glycine dehydrogenase (decarboxylating)
|
|
GLS
|
glutaminase
|
|
GLUD1
|
glutamate dehydrogenase 1
|
|
GLUD2
|
glutamate dehydrogenase 2
|
|
GLUL
|
glutamate-ammonia ligase
|
|
GOT1
|
glutamic-oxaloacetic transaminase 1, soluble
|
|
GOT2
|
glutamic-oxaloacetic transaminase 2, mitochondrial
|
|
GPT
|
glutamic-pyruvate transaminase (alanine aminotransferase)
|
|
GPT2
|
glutamic pyruvate transaminase (alanine aminotransferase) 2
|
|
GSTZ1
|
glutathione S-transferase zeta 1
|
|
HAAO
|
3-hydroxyanthranilate 3,4-dioxygenase
|
|
HAL
|
histidine ammonia-lyase
|
|
HDC
|
histidine decarboxylase
|
|
HGD
|
homogentisate 1,2-dioxygenase
|
|
HIBADH
|
3-hydroxyisobutyrate dehydrogenase
|
|
HIBCH
|
3-hydroxyisobutyryl-CoA hydrolase
|
|
HMGCL
|
3-hydroxymethyl-3-methylglutaryl-CoA lyase
|
|
HOGA1
|
4-hydroxy-2-oxoglutarate aldolase 1
|
|
HPD
|
4-hydroxyphenylpyruvate dioxygenase
|
|
HSD17B10
|
hydroxysteroid (17-beta) dehydrogenase 10
|
|
IDO1
|
indoleamine 2,3-dioxygenase 1
|
|
IDO2
|
indoleamine 2,3-dioxygenase 2
|
|
IVD
|
isovaleryl-CoA dehydrogenase
|
|
KMO
|
kynurenine 3-monooxygenase (kynurenine 3-hydroxylase)
|
|
KYNU
|
kynureninase
|
|
MCCC1
|
methylcrotonoyl-CoA carboxylase 1 (alpha)
|
|
MCCC2
|
methylcrotonoyl-CoA carboxylase 2 (beta)
|
|
MTRR
|
5-methyltetrahydrofolate-homocysteine methyltransferase reductase
|
|
NOS1
|
nitric oxide synthase 1 (neuronal)
|
|
NOS2
|
nitric oxide synthase 2, inducible
|
|
NOS3
|
nitric oxide synthase 3 (endothelial cell)
|
|
OGDH
|
oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
|
|
OTC
|
ornithine carbamoyltransferase
|
|
PAH
|
phenylalanine hydroxylase
|
|
PCBD1
|
pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha
|
|
PCYOX1
|
prenylcysteine oxidase 1
|
|
PCYOX1L
|
prenylcysteine oxidase 1 like
|
|
PIPOX
|
pipecolic acid oxidase
|
|
PPAT
|
phosphoribosyl pyrophosphate amidotransferase
|
|
PRODH
|
proline dehydrogenase (oxidase) 1
|
|
PRODH2
|
proline dehydrogenase (oxidase) 2
|
|
QDPR
|
quinoid dihydropteridine reductase
|
|
SDS
|
serine dehydratase
|
|
SDSL
|
serine dehydratase-like
|
|
SHMT1
|
serine hydroxymethyltransferase 1 (soluble)
|
|
SLC25A10
|
solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10
|
|
SLC25A21
|
solute carrier family 25 (mitochondrial oxoadipate carrier), member 21
|
|
SQRDL
|
sulfide quinone reductase-like (yeast)
|
|
SUOX
|
sulfite oxidase
|
|
TAT
|
tyrosine aminotransferase
|
|
TDO2
|
tryptophan 2,3-dioxygenase
|
|
THNSL2
|
threonine synthase-like 2 (S. cerevisiae)
|
|
TST
|
thiosulfate sulfurtransferase (rhodanese)
|
|
UROC1
|
urocanate hydratase 1
|