An autosomal dominant disease that is characterized by the association of diffuse mesangial sclerosis (DMS), male pseudohermaphroditism with a 46,XY karyotype, and nephroblastoma that derives_from an abnormality in the WT1 gene (Wilms' tumor suppressor gene). (Human Disease Ontology, DOID_3764)
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1 genes involed in the disease denys-drash syndrome from the DISEASES Curated Gene-Disease Assocation Evidence Scores dataset.