dicarboxylic acid metabolic process Gene Set

Dataset GO Biological Process Annotations 2025
Category structural or functional annotations
Type biological process
Description The chemical reactions and pathways involving dicarboxylic acids, any organic acid containing two carboxyl (COOH) groups or anions (COO-). (Gene Ontology, GO_0043648)
External Link http://amigo.geneontology.org/amigo/term/GO:0043648
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Genes

56 genes participating in the dicarboxylic acid metabolic process biological process from the curated GO Biological Process Annotations 2025 dataset.

Symbol Name
AADAT aminoadipate aminotransferase
ACLY ATP citrate lyase
ACOT4 acyl-CoA thioesterase 4
ACOT8 acyl-CoA thioesterase 8
ADHFE1 alcohol dehydrogenase, iron containing, 1
ALDH18A1 aldehyde dehydrogenase 18 family, member A1
ALDH5A1 aldehyde dehydrogenase 5 family, member A1
ASS1 argininosuccinate synthase 1
ATAT1 alpha tubulin acetyltransferase 1
D2HGDH D-2-hydroxyglutarate dehydrogenase
DGLUCY D-glutamate cyclase
DHFR dihydrofolate reductase
DHFR2 dihydrofolate reductase 2
DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
FAHD1 fumarylacetoacetate hydrolase domain containing 1
FAHD2A fumarylacetoacetate hydrolase domain containing 2A
FAHD2B fumarylacetoacetate hydrolase domain containing 2B
FPGS folylpolyglutamate synthase
GCLC glutamate-cysteine ligase, catalytic subunit
GCLM glutamate-cysteine ligase, modifier subunit
GGT1 gamma-glutamyltransferase 1
GOLT1A golgi transport 1A
GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial
GPT2 glutamic pyruvate transaminase (alanine aminotransferase) 2
GRID2 glutamate receptor, ionotropic, delta 2
HAAO 3-hydroxyanthranilate 3,4-dioxygenase
HOGA1 4-hydroxy-2-oxoglutarate aldolase 1
IDH1 isocitrate dehydrogenase 1 (NADP+), soluble
IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial
L2HGDH L-2-hydroxyglutarate dehydrogenase
LDHD lactate dehydrogenase D
LDLR low density lipoprotein receptor
MDH1 malate dehydrogenase 1, NAD (soluble)
MDH1B malate dehydrogenase 1B, NAD (soluble)
MDH2 malate dehydrogenase 2, NAD (mitochondrial)
MRPS36 mitochondrial ribosomal protein S36
MTHFD2 methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase
MTHFD2L methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2-like
MTRR 5-methyltetrahydrofolate-homocysteine methyltransferase reductase
NAGS N-acetylglutamate synthase
NIT2 nitrilase family, member 2
OGDH oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
OGDHL oxoglutarate dehydrogenase-like
PCDHB11 protocadherin beta 11
PCDHB16 protocadherin beta 16
PCDHGA5 protocadherin gamma subfamily A, 5
PCK1 phosphoenolpyruvate carboxykinase 1 (soluble)
PCK2 phosphoenolpyruvate carboxykinase 2 (mitochondrial)
PHYH phytanoyl-CoA 2-hydroxylase
SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
SDHAF3 succinate dehydrogenase complex assembly factor 3
SHMT1 serine hydroxymethyltransferase 1 (soluble)
SLC19A1 solute carrier family 19 (folate transporter), member 1
SLC25A32 solute carrier family 25 (mitochondrial folate carrier), member 32
SLC46A1 solute carrier family 46 (folate transporter), member 1
ST20-MTHFS ST20-MTHFS readthrough