| Symbol |
Name |
Standardized Value |
|
FXN
|
frataxin
|
4.42748
|
|
ACO2
|
aconitase 2, mitochondrial
|
2.09571
|
|
ISCU
|
iron-sulfur cluster assembly enzyme
|
2.04955
|
|
TTPA
|
tocopherol (alpha) transfer protein
|
2.02703
|
|
C21ORF2
|
chromosome 21 open reading frame 2
|
1.9267
|
|
GPAA1
|
glycosylphosphatidylinositol anchor attachment 1
|
1.92529
|
|
SACS
|
sacsin molecular chaperone
|
1.61396
|
|
ATXN3
|
ataxin 3
|
1.58582
|
|
PIP5K1B
|
phosphatidylinositol-4-phosphate 5-kinase, type I, beta
|
1.57289
|
|
NFS1
|
NFS1 cysteine desulfurase
|
1.55424
|
|
APTX
|
aprataxin
|
1.5238
|
|
FTMT
|
ferritin mitochondrial
|
1.49087
|
|
C10ORF2
|
chromosome 10 open reading frame 2
|
1.40351
|
|
FTH1
|
ferritin, heavy polypeptide 1
|
1.22388
|
|
FTL
|
ferritin, light polypeptide
|
1.22388
|
|
HSCB
|
HscB mitochondrial iron-sulfur cluster co-chaperone
|
1.21522
|
|
SETX
|
senataxin
|
1.19532
|
|
SLC25A28
|
solute carrier family 25 (mitochondrial iron transporter), member 28
|
1.13459
|
|
ABCB7
|
ATP-binding cassette, sub-family B (MDR/TAP), member 7
|
1.10594
|
|
IREB2
|
iron-responsive element binding protein 2
|
1.04251
|
|
FECH
|
ferrochelatase
|
1.02945
|
|
SPTBN2
|
spectrin, beta, non-erythrocytic 2
|
0.964986
|
|
BCS1L
|
BC1 (ubiquinol-cytochrome c reductase) synthesis-like
|
0.942858
|
|
MIPEP
|
mitochondrial intermediate peptidase
|
0.941611
|
|
PANK2
|
pantothenate kinase 2
|
0.931656
|
|
ATCAY
|
ataxia, cerebellar, Cayman type
|
0.892948
|
|
GLRX5
|
glutaredoxin 5
|
0.885569
|
|
HDAC9
|
histone deacetylase 9
|
0.874919
|
|
PDYN
|
prodynorphin
|
0.857724
|
|
SFXN1
|
sideroflexin 1
|
0.849536
|
|
PMPCB
|
peptidase (mitochondrial processing) beta
|
0.848716
|
|
CS
|
citrate synthase
|
0.811821
|
|
ACO1
|
aconitase 1, soluble
|
0.804436
|
|
MSH3
|
mutS homolog 3
|
0.803205
|
|
AFF2
|
AF4/FMR2 family, member 2
|
0.802795
|
|
POLG
|
polymerase (DNA directed), gamma
|
0.800333
|
|
PRKACG
|
protein kinase, cAMP-dependent, catalytic, gamma
|
0.792131
|
|
HDAC3
|
histone deacetylase 3
|
0.789672
|
|
CRIPT
|
cysteine-rich PDZ-binding protein
|
0.779432
|
|
TFR2
|
transferrin receptor 2
|
0.758193
|
|
HEPH
|
hephaestin
|
0.75412
|
|
EXOC6
|
exocyst complex component 6
|
0.753306
|
|
SLC40A1
|
solute carrier family 40 (iron-regulated transporter), member 1
|
0.746798
|
|
KLHL1
|
kelch-like family member 1
|
0.72329
|
|
TIMM44
|
translocase of inner mitochondrial membrane 44 homolog (yeast)
|
0.694702
|
|
SLC11A2
|
solute carrier family 11 (proton-coupled divalent metal ion transporter), member 2
|
0.6939
|
|
SYNE1
|
spectrin repeat containing, nuclear envelope 1
|
0.67312
|
|
TFRC
|
transferrin receptor
|
0.669936
|
|
TF
|
transferrin
|
0.668345
|
|
FMR1
|
fragile X mental retardation 1
|
0.663578
|
|
MTCP1
|
mature T-cell proliferation 1
|
0.620617
|
|
CDSN
|
corneodesmosin
|
0.615529
|
|
ADCK3
|
aarF domain containing kinase 3
|
0.584719
|
|
PANK1
|
pantothenate kinase 1
|
0.581217
|
|
OPA3
|
optic atrophy 3 (autosomal recessive, with chorea and spastic paraplegia)
|
0.576939
|
|
HFE
|
hemochromatosis
|
0.56722
|
|
MTHFD2
|
methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase
|
0.562558
|
|
OGDH
|
oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
|
0.558674
|
|
SOD2
|
superoxide dismutase 2, mitochondrial
|
0.552075
|
|
NDUFA1
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
|
0.550522
|
|
GPX1
|
glutathione peroxidase 1
|
0.548583
|
|
NPTX2
|
neuronal pentraxin II
|
0.546256
|
|
CP
|
ceruloplasmin (ferroxidase)
|
0.545481
|
|
KCNC3
|
potassium channel, voltage gated Shaw related subfamily C, member 3
|
0.529994
|
|
MT4
|
metallothionein 4
|
0.524974
|
|
GPX5
|
glutathione peroxidase 5
|
0.517649
|
|
GPX4
|
glutathione peroxidase 4
|
0.514571
|
|
SLC25A37
|
solute carrier family 25 (mitochondrial iron transporter), member 37
|
0.509959
|
|
FGF13
|
fibroblast growth factor 13
|
0.509576
|
|
HIST2H3PS2
|
histone cluster 2, H3, pseudogene 2
|
0.495793
|
|
SPG7
|
spastic paraplegia 7 (pure and complicated autosomal recessive)
|
0.495411
|
|
H3F3B
|
H3 histone, family 3B (H3.3B)
|
0.48893
|
|
H3F3A
|
H3 histone, family 3A
|
0.48893
|
|
AMPD1
|
adenosine monophosphate deaminase 1
|
0.485885
|
|
MFN2
|
mitofusin 2
|
0.485125
|
|
PNKP
|
polynucleotide kinase 3'-phosphatase
|
0.479047
|
|
SCAI
|
suppressor of cancer cell invasion
|
0.47753
|
|
CPOX
|
coproporphyrinogen oxidase
|
0.476772
|
|
HELT
|
helt bHLH transcription factor
|
0.474877
|
|
SIL1
|
SIL1 nucleotide exchange factor
|
0.455601
|
|
MDH1
|
malate dehydrogenase 1, NAD (soluble)
|
0.451831
|
|
DARS2
|
aspartyl-tRNA synthetase 2, mitochondrial
|
0.427015
|
|
MSH2
|
mutS homolog 2
|
0.418394
|
|
CLPP
|
caseinolytic mitochondrial matrix peptidase proteolytic subunit
|
0.412405
|
|
TIMM8A
|
translocase of inner mitochondrial membrane 8 homolog A (yeast)
|
0.407172
|
|
PMS2
|
PMS2 postmeiotic segregation increased 2 (S. cerevisiae)
|
0.407172
|
|
SLC39A14
|
solute carrier family 39 (zinc transporter), member 14
|
0.393746
|
|
CTCF
|
CCCTC-binding factor (zinc finger protein)
|
0.391885
|
|
HMOX1
|
heme oxygenase 1
|
0.389281
|
|
POLG2
|
polymerase (DNA directed), gamma 2, accessory subunit
|
0.381852
|
|
ZFYVE26
|
zinc finger, FYVE domain containing 26
|
0.378885
|
|
JPH3
|
junctophilin 3
|
0.377773
|
|
DLST
|
dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
|
0.364824
|
|
FEN1
|
flap structure-specific endonuclease 1
|
0.363347
|
|
AGK
|
acylglycerol kinase
|
0.35892
|
|
FA2H
|
fatty acid 2-hydroxylase
|
0.355604
|
|
PPAT
|
phosphoribosyl pyrophosphate amidotransferase
|
0.351923
|
|
FOXH1
|
forkhead box H1
|
0.349717
|
|
CNBP
|
CCHC-type zinc finger, nucleic acid binding protein
|
0.344207
|
|
MED1
|
mediator complex subunit 1
|
0.339073
|
|
ATP5B
|
ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide
|
0.334681
|
|
SIRT3
|
sirtuin 3
|
0.332487
|
|
GAD2
|
glutamate decarboxylase 2 (pancreatic islets and brain, 65kDa)
|
0.32774
|
|
SLC25A19
|
solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19
|
0.321545
|
|
HTT
|
huntingtin
|
0.304864
|
|
INS
|
insulin
|
0.300894
|
|
HFE2
|
hemochromatosis type 2 (juvenile)
|
0.299452
|
|
MSH6
|
mutS homolog 6
|
0.291898
|
|
CKM
|
creatine kinase, muscle
|
0.290821
|
|
HMGCL
|
3-hydroxymethyl-3-methylglutaryl-CoA lyase
|
0.289386
|
|
SERPINA3
|
serpin peptidase inhibitor, clade A (alpha-1 antiproteinase, antitrypsin), member 3
|
0.286519
|
|
MDH2
|
malate dehydrogenase 2, NAD (mitochondrial)
|
0.265849
|
|
MRE11A
|
MRE11 meiotic recombination 11 homolog A (S. cerevisiae)
|
0.264431
|
|
AFP
|
alpha-fetoprotein
|
0.263368
|
|
TST
|
thiosulfate sulfurtransferase (rhodanese)
|
0.240497
|
|
PLEKHG4
|
pleckstrin homology domain containing, family G (with RhoGef domain) member 4
|
0.222479
|
|
PRDX5
|
peroxiredoxin 5
|
0.220081
|
|
DLD
|
dihydrolipoamide dehydrogenase
|
0.218034
|
|
COX4I1
|
cytochrome c oxidase subunit IV isoform 1
|
0.214297
|
|
DNM1
|
dynamin 1
|
0.213959
|
|
ATL1
|
atlastin GTPase 1
|
0.209248
|
|
CLN6
|
ceroid-lipofuscinosis, neuronal 6, late infantile, variant
|
0.197742
|
|
SPG11
|
spastic paraplegia 11 (autosomal recessive)
|
0.195183
|
|
NRF1
|
nuclear respiratory factor 1
|
0.192031
|
|
C9ORF72
|
chromosome 9 open reading frame 72
|
0.190786
|
|
SIX4
|
SIX homeobox 4
|
0.188326
|
|
FDX1
|
ferredoxin 1
|
0.181222
|
|
TJP2
|
tight junction protein 2
|
0.178682
|
|
MFN1
|
mitofusin 1
|
0.175411
|
|
EGR3
|
early growth response 3
|
0.173571
|
|
SLC17A6
|
solute carrier family 17 (vesicular glutamate transporter), member 6
|
0.172544
|
|
HLCS
|
holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)
|
0.166095
|
|
KLF4
|
Kruppel-like factor 4 (gut)
|
0.165001
|
|
ASNS
|
asparagine synthetase (glutamine-hydrolyzing)
|
0.163729
|
|
PPARG
|
peroxisome proliferator-activated receptor gamma
|
0.159124
|
