glycosphingolipid metabolic process Gene Set

Dataset GO Biological Process Annotations 2025
Category structural or functional annotations
Type biological process
Description The chemical reactions and pathways involving glycosphingolipids, any compound with residues of sphingoid and at least one monosaccharide. (Gene Ontology, GO_0006687)
External Link http://amigo.geneontology.org/amigo/term/GO:0006687
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Genes

40 genes participating in the glycosphingolipid metabolic process biological process from the curated GO Biological Process Annotations 2025 dataset.

Symbol Name
A4GALT alpha 1,4-galactosyltransferase
ABCA2 ATP-binding cassette, sub-family A (ABC1), member 2
B3GALNT1 beta-1,3-N-acetylgalactosaminyltransferase 1 (globoside blood group)
B3GALT4 UDP-Gal:betaGlcNAc beta 1,3-galactosyltransferase, polypeptide 4
B3GNT5 UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 5
B4GALNT1 beta-1,4-N-acetyl-galactosaminyl transferase 1
B4GALT6 UDP-Gal:betaGlcNAc beta 1,4- galactosyltransferase, polypeptide 6
CERK ceramide kinase
CLN6 ceroid-lipofuscinosis, neuronal 6, late infantile, variant
ENPP7 ectonucleotide pyrophosphatase/phosphodiesterase 7
FUT1 fucosyltransferase 1 (galactoside 2-alpha-L-fucosyltransferase, H blood group)
FUT2 fucosyltransferase 2 (secretor status included)
FUT4 fucosyltransferase 4 (alpha (1,3) fucosyltransferase, myeloid-specific)
FUT6 fucosyltransferase 6 (alpha (1,3) fucosyltransferase)
FUT9 fucosyltransferase 9 (alpha (1,3) fucosyltransferase)
GAL3ST1 galactose-3-O-sulfotransferase 1
GALC galactosylceramidase
GBA2 glucosidase, beta (bile acid) 2
GBA3 glucosidase, beta, acid 3 (gene/pseudogene)
GLB1 galactosidase, beta 1
GM2A GM2 ganglioside activator
LARGE1 LARGE xylosyl- and glucuronyltransferase 1
M6PR mannose-6-phosphate receptor (cation dependent)
NAT8 N-acetyltransferase 8 (GCN5-related, putative)
NEU2 sialidase 2 (cytosolic sialidase)
NEU3 sialidase 3 (membrane sialidase)
SMPD1 sphingomyelin phosphodiesterase 1, acid lysosomal
ST3GAL2 ST3 beta-galactoside alpha-2,3-sialyltransferase 2
ST3GAL3 ST3 beta-galactoside alpha-2,3-sialyltransferase 3
ST3GAL5 ST3 beta-galactoside alpha-2,3-sialyltransferase 5
ST6GALNAC3 ST6 (alpha-N-acetyl-neuraminyl-2,3-beta-galactosyl-1,3)-N-acetylgalactosaminide alpha-2,6-sialyltransferase 3
ST6GALNAC5 ST6 (alpha-N-acetyl-neuraminyl-2,3-beta-galactosyl-1,3)-N-acetylgalactosaminide alpha-2,6-sialyltransferase 5
ST6GALNAC6 ST6 (alpha-N-acetyl-neuraminyl-2,3-beta-galactosyl-1,3)-N-acetylgalactosaminide alpha-2,6-sialyltransferase 6
ST8SIA1 ST8 alpha-N-acetyl-neuraminide alpha-2,8-sialyltransferase 1
ST8SIA3 ST8 alpha-N-acetyl-neuraminide alpha-2,8-sialyltransferase 3
ST8SIA5 ST8 alpha-N-acetyl-neuraminide alpha-2,8-sialyltransferase 5
SUMF1 sulfatase modifying factor 1
TM9SF2 transmembrane 9 superfamily member 2
UGCG UDP-glucose ceramide glucosyltransferase
UGT8 UDP glycosyltransferase 8