| Symbol |
Name |
|
AARS2
|
alanyl-tRNA synthetase 2, mitochondrial
|
|
ACAT2
|
acetyl-CoA acetyltransferase 2
|
|
ADAMTS13
|
ADAM metallopeptidase with thrombospondin type 1 motif, 13
|
|
AGK
|
acylglycerol kinase
|
|
AIFM1
|
apoptosis-inducing factor, mitochondrion-associated, 1
|
|
ATPAF2
|
ATP synthase mitochondrial F1 complex assembly factor 2
|
|
BCS1L
|
BC1 (ubiquinol-cytochrome c reductase) synthesis-like
|
|
C10ORF2
|
chromosome 10 open reading frame 2
|
|
C12ORF65
|
chromosome 12 open reading frame 65
|
|
CA5A
|
carbonic anhydrase VA, mitochondrial
|
|
COA5
|
cytochrome c oxidase assembly factor 5
|
|
COQ9
|
coenzyme Q9
|
|
COX10
|
COX10 heme A:farnesyltransferase cytochrome c oxidase assembly factor
|
|
COX14
|
COX14 cytochrome c oxidase assembly factor
|
|
COX15
|
cytochrome c oxidase assembly homolog 15 (yeast)
|
|
COX20
|
COX20 cytochrome c oxidase assembly factor
|
|
COX6B1
|
cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous)
|
|
CYC1
|
cytochrome c-1
|
|
EARS2
|
glutamyl-tRNA synthetase 2, mitochondrial
|
|
FARS2
|
phenylalanyl-tRNA synthetase 2, mitochondrial
|
|
FASTKD2
|
FAST kinase domains 2
|
|
FBXL4
|
F-box and leucine-rich repeat protein 4
|
|
FOXRED1
|
FAD-dependent oxidoreductase domain containing 1
|
|
GFM1
|
G elongation factor, mitochondrial 1
|
|
GYS2
|
glycogen synthase 2 (liver)
|
|
ISCU
|
iron-sulfur cluster assembly enzyme
|
|
LDHA
|
lactate dehydrogenase A
|
|
LIAS
|
lipoic acid synthetase
|
|
LRPPRC
|
leucine-rich pentatricopeptide repeat containing
|
|
LYRM7
|
LYR motif containing 7
|
|
MPC1
|
mitochondrial pyruvate carrier 1
|
|
MRPL3
|
mitochondrial ribosomal protein L3
|
|
MRPL44
|
mitochondrial ribosomal protein L44
|
|
MRPS16
|
mitochondrial ribosomal protein S16
|
|
MRPS22
|
mitochondrial ribosomal protein S22
|
|
MTFMT
|
mitochondrial methionyl-tRNA formyltransferase
|
|
MTO1
|
mitochondrial tRNA translation optimization 1
|
|
NDUFA10
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
|
|
NDUFA12
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12
|
|
NDUFA2
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
|
|
NDUFA9
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
|
|
NDUFAF2
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 2
|
|
NDUFAF6
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 6
|
|
NDUFS3
|
NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
|
|
NDUFS4
|
NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
|
|
NDUFS7
|
NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
|
|
NDUFS8
|
NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
|
|
OGDH
|
oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
|
|
PC
|
pyruvate carboxylase
|
|
PDHA1
|
pyruvate dehydrogenase (lipoamide) alpha 1
|
|
PDSS1
|
prenyl (decaprenyl) diphosphate synthase, subunit 1
|
|
PDSS2
|
prenyl (decaprenyl) diphosphate synthase, subunit 2
|
|
PET100
|
PET100 homolog (S. cerevisiae)
|
|
PNPO
|
pyridoxamine 5'-phosphate oxidase
|
|
POLG
|
polymerase (DNA directed), gamma
|
|
POLG2
|
polymerase (DNA directed), gamma 2, accessory subunit
|
|
PUS1
|
pseudouridylate synthase 1
|
|
RARS2
|
arginyl-tRNA synthetase 2, mitochondrial
|
|
RMND1
|
required for meiotic nuclear division 1 homolog (S. cerevisiae)
|
|
SCO2
|
SCO2 cytochrome c oxidase assembly protein
|
|
SDHA
|
succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
|
|
SDHAF1
|
succinate dehydrogenase complex assembly factor 1
|
|
SERAC1
|
serine active site containing 1
|
|
SFXN4
|
sideroflexin 4
|
|
SURF1
|
surfeit 1
|
|
TACO1
|
translational activator of mitochondrially encoded cytochrome c oxidase I
|
|
TARS2
|
threonyl-tRNA synthetase 2, mitochondrial (putative)
|
|
TMEM70
|
transmembrane protein 70
|
|
TRMU
|
tRNA 5-methylaminomethyl-2-thiouridylate methyltransferase
|
|
TSFM
|
Ts translation elongation factor, mitochondrial
|
|
UQCRC2
|
ubiquinol-cytochrome c reductase core protein II
|
|
UQCRQ
|
ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa
|
|
YARS2
|
tyrosyl-tRNA synthetase 2, mitochondrial
|
