| Symbol |
Name |
|
ABAT
|
4-aminobutyrate aminotransferase
|
|
ABCE1
|
ATP-binding cassette, sub-family E (OABP), member 1
|
|
ACO1
|
aconitase 1, soluble
|
|
ACO2
|
aconitase 2, mitochondrial
|
|
AIFM3
|
apoptosis-inducing factor, mitochondrion-associated, 3
|
|
AOX1
|
aldehyde oxidase 1
|
|
BRIP1
|
BRCA1 interacting protein C-terminal helicase 1
|
|
CDK5RAP1
|
CDK5 regulatory subunit associated protein 1
|
|
CDKAL1
|
CDK5 regulatory subunit associated protein 1-like 1
|
|
CIAPIN1
|
cytokine induced apoptosis inhibitor 1
|
|
CISD1
|
CDGSH iron sulfur domain 1
|
|
CISD2
|
CDGSH iron sulfur domain 2
|
|
CISD3
|
CDGSH iron sulfur domain 3
|
|
DDX11
|
DEAD/H (Asp-Glu-Ala-Asp/His) box helicase 11
|
|
DNA2
|
DNA replication helicase/nuclease 2
|
|
DPYD
|
dihydropyrimidine dehydrogenase
|
|
ELP3
|
elongator acetyltransferase complex subunit 3
|
|
ERCC2
|
excision repair cross-complementation group 2
|
|
ETFDH
|
electron-transferring-flavoprotein dehydrogenase
|
|
EXO5
|
exonuclease 5
|
|
FDX1
|
ferredoxin 1
|
|
FDX1L
|
ferredoxin 1-like
|
|
FECH
|
ferrochelatase
|
|
FXN
|
frataxin
|
|
GLRX2
|
glutaredoxin 2
|
|
GLRX3
|
glutaredoxin 3
|
|
GLRX5
|
glutaredoxin 5
|
|
IREB2
|
iron-responsive element binding protein 2
|
|
ISCA1
|
iron-sulfur cluster assembly 1
|
|
ISCA2
|
iron-sulfur cluster assembly 2
|
|
ISCU
|
iron-sulfur cluster assembly enzyme
|
|
LIAS
|
lipoic acid synthetase
|
|
MOCS1
|
molybdenum cofactor synthesis 1
|
|
MUTYH
|
mutY homolog
|
|
NARFL
|
nuclear prelamin A recognition factor-like
|
|
NDUFS1
|
NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
|
|
NDUFS2
|
NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
|
|
NDUFS7
|
NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
|
|
NDUFS8
|
NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
|
|
NDUFV1
|
NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa
|
|
NDUFV2
|
NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa
|
|
NFS1
|
NFS1 cysteine desulfurase
|
|
NFU1
|
NFU1 iron-sulfur cluster scaffold
|
|
NTHL1
|
nth endonuclease III-like 1 (E. coli)
|
|
NUBP1
|
nucleotide binding protein 1
|
|
NUBP2
|
nucleotide binding protein 2
|
|
NUBPL
|
nucleotide binding protein-like
|
|
POLA1
|
polymerase (DNA directed), alpha 1, catalytic subunit
|
|
POLD1
|
polymerase (DNA directed), delta 1, catalytic subunit
|
|
POLE
|
polymerase (DNA directed), epsilon, catalytic subunit
|
|
PPAT
|
phosphoribosyl pyrophosphate amidotransferase
|
|
PRIM2
|
primase, DNA, polypeptide 2 (58kDa)
|
|
REV3L
|
REV3-like, polymerase (DNA directed), zeta, catalytic subunit
|
|
RFESD
|
Rieske (Fe-S) domain containing
|
|
RPS3
|
ribosomal protein S3
|
|
RSAD1
|
radical S-adenosyl methionine domain containing 1
|
|
RSAD2
|
radical S-adenosyl methionine domain containing 2
|
|
RTEL1
|
regulator of telomere elongation helicase 1
|
|
SDHB
|
succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
|
|
TYW1
|
tRNA-yW synthesizing protein 1 homolog (S. cerevisiae)
|
|
TYW1B
|
tRNA-yW synthesizing protein 1 homolog B (S. cerevisiae)
|
|
UQCRFS1
|
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
|
|
XDH
|
xanthine dehydrogenase
|