| Symbol |
Name |
Standardized Value |
|
SURF1
|
surfeit 1
|
3.39303
|
|
NPTX2
|
neuronal pentraxin II
|
2.12319
|
|
NDUFS8
|
NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
|
2.08962
|
|
SCO2
|
SCO2 cytochrome c oxidase assembly protein
|
2.05315
|
|
LRPPRC
|
leucine-rich pentatricopeptide repeat containing
|
2.00286
|
|
NDUFA1
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
|
1.95911
|
|
NDUFV1
|
NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa
|
1.86689
|
|
COX10
|
COX10 heme A:farnesyltransferase cytochrome c oxidase assembly factor
|
1.86186
|
|
TACO1
|
translational activator of mitochondrially encoded cytochrome c oxidase I
|
1.80698
|
|
COX15
|
cytochrome c oxidase assembly homolog 15 (yeast)
|
1.78308
|
|
NDUFAF6
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 6
|
1.77767
|
|
PDHA1
|
pyruvate dehydrogenase (lipoamide) alpha 1
|
1.73094
|
|
NDUFS1
|
NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
|
1.72593
|
|
NDUFAF5
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 5
|
1.67864
|
|
SDHAF1
|
succinate dehydrogenase complex assembly factor 1
|
1.66465
|
|
SLC19A3
|
solute carrier family 19 (thiamine transporter), member 3
|
1.57111
|
|
SCO1
|
SCO1 cytochrome c oxidase assembly protein
|
1.53877
|
|
GATB
|
glutamyl-tRNA(Gln) amidotransferase, subunit B
|
1.52468
|
|
PTCD1
|
pentatricopeptide repeat domain 1
|
1.5216
|
|
MTFMT
|
mitochondrial methionyl-tRNA formyltransferase
|
1.51325
|
|
NDUFA8
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
|
1.49964
|
|
PDHB
|
pyruvate dehydrogenase (lipoamide) beta
|
1.41753
|
|
COX7A2L
|
cytochrome c oxidase subunit VIIa polypeptide 2 like
|
1.41095
|
|
NDUFS2
|
NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
|
1.40658
|
|
NDUFS4
|
NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
|
1.34897
|
|
BOLA3
|
bolA family member 3
|
1.34548
|
|
NDUFAF2
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 2
|
1.32585
|
|
NDUFS7
|
NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
|
1.32236
|
|
NDUFA12
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12
|
1.31581
|
|
PC
|
pyruvate carboxylase
|
1.30576
|
|
GYG2
|
glycogenin 2
|
1.30357
|
|
PDHX
|
pyruvate dehydrogenase complex, component X
|
1.27257
|
|
COX17
|
COX17 cytochrome c oxidase copper chaperone
|
1.25341
|
|
NDUFB3
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa
|
1.22952
|
|
NDUFA2
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
|
1.22518
|
|
C12ORF65
|
chromosome 12 open reading frame 65
|
1.21738
|
|
MTRF1
|
mitochondrial translational release factor 1
|
1.21565
|
|
MTRF1L
|
mitochondrial translational release factor 1-like
|
1.21565
|
|
COQ2
|
coenzyme Q2 4-hydroxybenzoate polyprenyltransferase
|
1.20396
|
|
DLD
|
dihydrolipoamide dehydrogenase
|
1.19704
|
|
AARS2
|
alanyl-tRNA synthetase 2, mitochondrial
|
1.19618
|
|
POLG
|
polymerase (DNA directed), gamma
|
1.19359
|
|
SERAC1
|
serine active site containing 1
|
1.19014
|
|
NDUFS6
|
NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)
|
1.17808
|
|
ATP5E
|
ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit
|
1.17249
|
|
SDHA
|
succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
|
1.16606
|
|
NDUFA10
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
|
1.15453
|
|
COX11
|
COX11 cytochrome c oxidase copper chaperone
|
1.13416
|
|
LIAS
|
lipoic acid synthetase
|
1.08202
|
|
RMND1
|
required for meiotic nuclear division 1 homolog (S. cerevisiae)
|
1.05009
|
|
IARS2
|
isoleucyl-tRNA synthetase 2, mitochondrial
|
1.04714
|
|
TMEM70
|
transmembrane protein 70
|
1.0463
|
|
PDP2
|
pyruvate dehyrogenase phosphatase catalytic subunit 2
|
1.0362
|
|
TTC19
|
tetratricopeptide repeat domain 19
|
1.02777
|
|
DARS2
|
aspartyl-tRNA synthetase 2, mitochondrial
|
1.02692
|
|
CRLS1
|
cardiolipin synthase 1
|
1.02608
|
|
NDUFA9
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
|
1.01807
|
|
NDUFAF1
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 1
|
1.01427
|
|
MARS2
|
methionyl-tRNA synthetase 2, mitochondrial
|
1.00794
|
|
THTPA
|
thiamine triphosphatase
|
0.996127
|
|
HIBCH
|
3-hydroxyisobutyryl-CoA hydrolase
|
0.988535
|
|
LIPT1
|
lipoyltransferase 1
|
0.982215
|
|
SUCLG1
|
succinate-CoA ligase, alpha subunit
|
0.965405
|
|
NDUFB6
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa
|
0.962891
|
|
SLIRP
|
SRA stem-loop interacting RNA binding protein
|
0.950352
|
|
DSCR8
|
Down syndrome critical region 8
|
0.929587
|
|
MT-ATP8
|
ATP synthase F0 subunit 8
|
0.910199
|
|
SDHC
|
succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa
|
0.86018
|
|
NDUFA4
|
NDUFA4, mitochondrial complex associated
|
0.857315
|
|
DNAJC19
|
DnaJ (Hsp40) homolog, subfamily C, member 19
|
0.823718
|
|
GFM1
|
G elongation factor, mitochondrial 1
|
0.807718
|
|
TSFM
|
Ts translation elongation factor, mitochondrial
|
0.804026
|
|
TRMU
|
tRNA 5-methylaminomethyl-2-thiouridylate methyltransferase
|
0.800333
|
|
OPA3
|
optic atrophy 3 (autosomal recessive, with chorea and spastic paraplegia)
|
0.792131
|
|
DNAH8
|
dynein, axonemal, heavy chain 8
|
0.757786
|
|
ECHS1
|
enoyl CoA hydratase, short chain, 1, mitochondrial
|
0.734217
|
|
CS
|
citrate synthase
|
0.724098
|
|
SDHB
|
succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
|
0.72329
|
|
NFU1
|
NFU1 iron-sulfur cluster scaffold
|
0.718039
|
|
SDHD
|
succinate dehydrogenase complex, subunit D, integral membrane protein
|
0.716828
|
|
ATCAY
|
ataxia, cerebellar, Cayman type
|
0.70434
|
|
GLRX5
|
glutaredoxin 5
|
0.697109
|
|
C10ORF2
|
chromosome 10 open reading frame 2
|
0.687491
|
|
TK2
|
thymidine kinase 2, mitochondrial
|
0.682294
|
|
SDHAF2
|
succinate dehydrogenase complex assembly factor 2
|
0.682294
|
|
NDUFV2
|
NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa
|
0.680297
|
|
SUCLA2
|
succinate-CoA ligase, ADP-forming, beta subunit
|
0.653671
|
|
GCSH
|
glycine cleavage system protein H (aminomethyl carrier)
|
0.646559
|
|
PDSS2
|
prenyl (decaprenyl) diphosphate synthase, subunit 2
|
0.615529
|
|
PDP1
|
pyruvate dehyrogenase phosphatase catalytic subunit 1
|
0.60069
|
|
TIMM8A
|
translocase of inner mitochondrial membrane 8 homolog A (yeast)
|
0.596402
|
|
MTO1
|
mitochondrial tRNA translation optimization 1
|
0.592895
|
|
BCS1L
|
BC1 (ubiquinol-cytochrome c reductase) synthesis-like
|
0.572273
|
|
NDUFS3
|
NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
|
0.563723
|
|
PAPSS1
|
3'-phosphoadenosine 5'-phosphosulfate synthase 1
|
0.556732
|
|
OGDH
|
oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
|
0.551298
|
|
ATP5O
|
ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit
|
0.521888
|
|
SLC12A6
|
solute carrier family 12 (potassium/chloride transporter), member 6
|
0.511112
|
|
RANBP2
|
RAN binding protein 2
|
0.507273
|
|
GLDC
|
glycine dehydrogenase (decarboxylating)
|
0.505356
|
|
AHSG
|
alpha-2-HS-glycoprotein
|
0.496175
|
|
SLC27A1
|
solute carrier family 27 (fatty acid transporter), member 1
|
0.495793
|
|
SLC25A4
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
|
0.486646
|
|
DLAT
|
dihydrolipoamide S-acetyltransferase
|
0.484364
|
|
UCP1
|
uncoupling protein 1 (mitochondrial, proton carrier)
|
0.470711
|
|
CDSN
|
corneodesmosin
|
0.463149
|
|
SUOX
|
sulfite oxidase
|
0.440538
|
|
LGALS4
|
lectin, galactoside-binding, soluble, 4
|
0.437906
|
|
ICT1
|
immature colon carcinoma transcript 1
|
0.436402
|
|
AK1
|
adenylate kinase 1
|
0.407919
|
|
FLAD1
|
flavin adenine dinucleotide synthetase 1
|
0.381481
|
|
PCYT1A
|
phosphate cytidylyltransferase 1, choline, alpha
|
0.371847
|
|
GDAP1
|
ganglioside induced differentiation associated protein 1
|
0.34384
|
|
COL6A3
|
collagen, type VI, alpha 3
|
0.32701
|
|
GZMM
|
granzyme M (lymphocyte met-ase 1)
|
0.302698
|
|
FXN
|
frataxin
|
0.301615
|
|
QDPR
|
quinoid dihydropteridine reductase
|
0.290821
|
|
GCDH
|
glutaryl-CoA dehydrogenase
|
0.276514
|
|
NDUFAB1
|
NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
|
0.262306
|
|
SETD1A
|
SET domain containing 1A
|
0.259477
|
|
SACS
|
sacsin molecular chaperone
|
0.254888
|
|
ATP11A
|
ATPase, class VI, type 11A
|
0.245747
|
|
MRPS7
|
mitochondrial ribosomal protein S7
|
0.228333
|
|
EEF1A1
|
eukaryotic translation elongation factor 1 alpha 1
|
0.203933
|
|
OPA1
|
optic atrophy 1 (autosomal dominant)
|
0.191408
|
|
MARS
|
methionyl-tRNA synthetase
|
0.190786
|
|
TFAM
|
transcription factor A, mitochondrial
|
0.174617
|
|
NFIC
|
nuclear factor I/C (CCAAT-binding transcription factor)
|
0.171036
|
|
TKT
|
transketolase
|
0.170544
|
|
NFIX
|
nuclear factor I/X (CCAAT-binding transcription factor)
|
0.169571
|
