mitochondrial envelope Gene Set

Dataset GO Cellular Component Annotations 2023
Category structural or functional annotations
Type biological process
Description The double lipid bilayer enclosing the mitochondrion and separating its contents from the cell cytoplasm; includes the intermembrane space. (Gene Ontology, GO_0005740)
External Link http://amigo.geneontology.org/amigo/term/GO:0005740
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Genes

147 proteins localized to the mitochondrial envelope cellular component from the curated GO Cellular Component Annotations 2023 dataset.

Symbol Name
ABCB10 ATP-binding cassette, sub-family B (MDR/TAP), member 10
ABCB6 ATP-binding cassette, sub-family B (MDR/TAP), member 6 (Langereis blood group)
ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8
ABCD1 ATP-binding cassette, sub-family D (ALD), member 1
ACAD11 acyl-CoA dehydrogenase family, member 11
ACAD9 acyl-CoA dehydrogenase family, member 9
ACADM acyl-CoA dehydrogenase, C-4 to C-12 straight chain
ACADVL acyl-CoA dehydrogenase, very long chain
ADAP2 ArfGAP with dual PH domains 2
AFG1L AFG1 like ATPase
AGK acylglycerol kinase
AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1
AK2 adenylate kinase 2
ALPL alkaline phosphatase, liver/bone/kidney
AQP8 aquaporin 8
ARL2 ADP-ribosylation factor-like 2
ARL2BP ADP-ribosylation factor-like 2 binding protein
ASPNAT aspartate N-acetyltransferase
ATCAY ataxia, cerebellar, Cayman type
ATP5F1B ATP synthase F1 subunit beta
ATXN3 ataxin 3
BLOC1S1 biogenesis of lysosomal organelles complex-1, subunit 1
BNIP1 BCL2/adenovirus E1B 19kDa interacting protein 1
BNIP3 BCL2/adenovirus E1B 19kDa interacting protein 3
BOK BCL2-related ovarian killer
C19ORF12 chromosome 19 open reading frame 12
C7ORF73 chromosome 7 open reading frame 73
CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10
CHCHD2 coiled-coil-helix-coiled-coil-helix domain containing 2
CHCHD4 coiled-coil-helix-coiled-coil-helix domain containing 4
CHCHD5 coiled-coil-helix-coiled-coil-helix domain containing 5
CIDEA cell death-inducing DFFA-like effector a
CLPB ClpB homolog, mitochondrial AAA ATPase chaperonin
CMC4 C-x(9)-C motif containing 4
COA4 cytochrome c oxidase assembly factor 4 homolog (S. cerevisiae)
COA6 cytochrome c oxidase assembly factor 6
COA7 cytochrome c oxidase assembly factor 7 (putative)
COX17 COX17 cytochrome c oxidase copper chaperone
COX19 COX19 cytochrome c oxidase assembly factor
CPOX coproporphyrinogen oxidase
CYB5R3 cytochrome b5 reductase 3
CYCS cytochrome c, somatic
DIABLO diablo, IAP-binding mitochondrial protein
ETFDH electron-transferring-flavoprotein dehydrogenase
FBXL4 F-box and leucine-rich repeat protein 4
FKBP8 FK506 binding protein 8, 38kDa
FLVCR2 feline leukemia virus subgroup C cellular receptor family, member 2
FZD9 frizzled class receptor 9
GATM glycine amidinotransferase (L-arginine:glycine amidinotransferase)
GNPAT glyceronephosphate O-acyltransferase
GPAM glycerol-3-phosphate acyltransferase, mitochondrial
GPAT2 glycerol-3-phosphate acyltransferase 2, mitochondrial
GPER1 G protein-coupled estrogen receptor 1
GUCY2C guanylate cyclase 2C
HADHB hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit
HAX1 HCLS1 associated protein X-1
HCRT hypocretin (orexin) neuropeptide precursor
HSD3B1 hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 1
HSD3B2 hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 2
HSP90B2P heat shock protein 90kDa beta (Grp94), member 2, pseudogene
HTRA2 HtrA serine peptidase 2
IFI27 interferon, alpha-inducible protein 27
IFI27L2 interferon, alpha-inducible protein 27-like 2
IFI6 interferon, alpha-inducible protein 6
IKBKE inhibitor of kappa light polypeptide gene enhancer in B-cells, kinase epsilon
IRGM immunity-related GTPase family, M
KIF28P kinesin family member 28, pseudogene
LRRK2 leucine-rich repeat kinase 2
LYRM7 LYR motif containing 7
MAOB monoamine oxidase B
MAVS mitochondrial antiviral signaling protein
MFF mitochondrial fission factor
MICU1 mitochondrial calcium uptake 1
MICU2 mitochondrial calcium uptake 2
MYOC myocilin, trabecular meshwork inducible glucocorticoid response
NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
NDUFA13 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa
NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4
NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa
NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa
NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
NGRN neugrin, neurite outgrowth associated
NLN neurolysin (metallopeptidase M3 family)
NME4 NME/NM23 nucleoside diphosphate kinase 4
OGDH oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
OMA1 OMA1 zinc metallopeptidase
OPA1 optic atrophy 1 (autosomal dominant)
OXA1L oxidase (cytochrome c) assembly 1-like
PANK2 pantothenate kinase 2
PINK1 PTEN induced putative kinase 1
PLA2G4C phospholipase A2, group IVC (cytosolic, calcium-independent)
PLEKHN1 pleckstrin homology domain containing, family N member 1
PNPT1 polyribonucleotide nucleotidyltransferase 1
PRELID1 PRELI domain containing 1
PRELID2 PRELI domain containing 2
PRELID3B PRELI domain containing 3B
RCC1L RCC1 like
REXO2 RNA exonuclease 2
RNF144B ring finger protein 144B
SDHAF3 succinate dehydrogenase complex assembly factor 3
SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
SDHD succinate dehydrogenase complex, subunit D, integral membrane protein
SIRT5 sirtuin 5
SLC22A3 solute carrier family 22 (organic cation transporter), member 3
SLC25A20 solute carrier family 25 (carnitine/acylcarnitine translocase), member 20
SLC25A27 solute carrier family 25, member 27
SLC25A28 solute carrier family 25 (mitochondrial iron transporter), member 28
SLC25A33 solute carrier family 25 (pyrimidine nucleotide carrier), member 33
SLC25A37 solute carrier family 25 (mitochondrial iron transporter), member 37
SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
SLC30A9 solute carrier family 30 (zinc transporter), member 9
SLC39A9 solute carrier family 39, member 9
SLC8B1 solute carrier family 8 (sodium/lithium/calcium exchanger), member B1
SLC9B2 solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2
SLMO1 slowmo homolog 1 (Drosophila)
SOD1 superoxide dismutase 1, soluble
STOML2 stomatin (EPB72)-like 2
TAZ tafazzin
THOP1 thimet oligopeptidase 1
TIMM10 translocase of inner mitochondrial membrane 10 homolog (yeast)
TIMM10B translocase of inner mitochondrial membrane 10 homolog B (yeast)
TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast)
TIMM23 translocase of inner mitochondrial membrane 23 homolog (yeast)
TIMM29 translocase of inner mitochondrial membrane 29
TIMM8A translocase of inner mitochondrial membrane 8 homolog A (yeast)
TIMM8B translocase of inner mitochondrial membrane 8 homolog B (yeast)
TIMM9 translocase of inner mitochondrial membrane 9 homolog (yeast)
TMBIM6 transmembrane BAX inhibitor motif containing 6
TMEM14A transmembrane protein 14A
TMEM14B transmembrane protein 14B
TMEM14C transmembrane protein 14C
TMEM14D transmembrane protein 14D (pseudogene)
TMEM14E transmembrane protein 14E
TMEM70 transmembrane protein 70
TOMM70 translocase of outer mitochondrial membrane 70
TRIAP1 TP53 regulated inhibitor of apoptosis 1
UQCC2 ubiquinol-cytochrome c reductase complex assembly factor 2
VDAC1 voltage-dependent anion channel 1
VDAC2 voltage-dependent anion channel 2
VPS13A vacuolar protein sorting 13 homolog A (S. cerevisiae)
VRK2 vaccinia related kinase 2