| Symbol |
Name |
|
ABCB7
|
ATP-binding cassette, sub-family B (MDR/TAP), member 7
|
|
ABCB8
|
ATP-binding cassette, sub-family B (MDR/TAP), member 8
|
|
ACAD11
|
acyl-CoA dehydrogenase family, member 11
|
|
ACAD9
|
acyl-CoA dehydrogenase family, member 9
|
|
ADCK1
|
aarF domain containing kinase 1
|
|
AFG3L2
|
AFG3-like AAA ATPase 2
|
|
AGK
|
acylglycerol kinase
|
|
AIFM1
|
apoptosis-inducing factor, mitochondrion-associated, 1
|
|
AIFM3
|
apoptosis-inducing factor, mitochondrion-associated, 3
|
|
ALAS2
|
5'-aminolevulinate synthase 2
|
|
ALDH18A1
|
aldehyde dehydrogenase 18 family, member A1
|
|
AMBP
|
alpha-1-microglobulin/bikunin precursor
|
|
APOO
|
apolipoprotein O
|
|
APOOL
|
apolipoprotein O-like
|
|
APP
|
amyloid beta (A4) precursor protein
|
|
AQP8
|
aquaporin 8
|
|
ATAD3A
|
ATPase family, AAA domain containing 3A
|
|
ATP5F1A
|
ATP synthase F1 subunit alpha
|
|
ATP5F1B
|
ATP synthase F1 subunit beta
|
|
ATP5F1C
|
ATP synthase F1 subunit gamma
|
|
ATP5F1D
|
ATP synthase F1 subunit delta
|
|
ATP5F1E
|
ATP synthase F1 subunit epsilon
|
|
ATP5MC1
|
ATP synthase membrane subunit c locus 1
|
|
ATP5MC2
|
ATP synthase membrane subunit c locus 2
|
|
ATP5MC3
|
ATP synthase membrane subunit c locus 3
|
|
ATP5ME
|
ATP synthase membrane subunit e
|
|
ATP5MF
|
ATP synthase membrane subunit f
|
|
ATP5MG
|
ATP synthase membrane subunit g
|
|
ATP5MGL
|
ATP synthase membrane subunit g like
|
|
ATP5MJ
|
ATP synthase membrane subunit j
|
|
ATP5MK
|
ATP synthase membrane subunit k
|
|
ATP5PB
|
ATP synthase peripheral stalk-membrane subunit b
|
|
ATP5PD
|
ATP synthase peripheral stalk subunit d
|
|
ATP5PF
|
ATP synthase peripheral stalk subunit F6
|
|
ATP5PO
|
ATP synthase peripheral stalk subunit OSCP
|
|
ATPAF1
|
ATP synthase mitochondrial F1 complex assembly factor 1
|
|
ATPAF2
|
ATP synthase mitochondrial F1 complex assembly factor 2
|
|
AURKAIP1
|
aurora kinase A interacting protein 1
|
|
BCS1L
|
BC1 (ubiquinol-cytochrome c reductase) synthesis-like
|
|
BDH1
|
3-hydroxybutyrate dehydrogenase, type 1
|
|
BOK
|
BCL2-related ovarian killer
|
|
CABS1
|
calcium-binding protein, spermatid-specific 1
|
|
CCDC51
|
coiled-coil domain containing 51
|
|
CCNI
|
cyclin I
|
|
CDS2
|
CDP-diacylglycerol synthase (phosphatidate cytidylyltransferase) 2
|
|
CHCHD1
|
coiled-coil-helix-coiled-coil-helix domain containing 1
|
|
CHCHD3
|
coiled-coil-helix-coiled-coil-helix domain containing 3
|
|
CHCHD6
|
coiled-coil-helix-coiled-coil-helix domain containing 6
|
|
CHDH
|
choline dehydrogenase
|
|
CIBAR1
|
CBY1 interacting BAR domain containing 1
|
|
CKMT1A
|
creatine kinase, mitochondrial 1A
|
|
CKMT2
|
creatine kinase, mitochondrial 2 (sarcomeric)
|
|
CLPX
|
caseinolytic mitochondrial matrix peptidase chaperone subunit
|
|
CLU
|
clusterin
|
|
COA1
|
cytochrome c oxidase assembly factor 1 homolog (S. cerevisiae)
|
|
COA3
|
cytochrome c oxidase assembly factor 3
|
|
COA5
|
cytochrome c oxidase assembly factor 5
|
|
COA8
|
cytochrome c oxidase assembly factor 8
|
|
COQ10A
|
coenzyme Q10 homolog A (S. cerevisiae)
|
|
COQ10B
|
coenzyme Q10 homolog B (S. cerevisiae)
|
|
COQ2
|
coenzyme Q2 4-hydroxybenzoate polyprenyltransferase
|
|
COQ3
|
coenzyme Q3 methyltransferase
|
|
COQ4
|
coenzyme Q4
|
|
COQ5
|
coenzyme Q5 homolog, methyltransferase (S. cerevisiae)
|
|
COQ6
|
coenzyme Q6 monooxygenase
|
|
COQ7
|
coenzyme Q7 homolog, ubiquinone (yeast)
|
|
COQ9
|
coenzyme Q9
|
|
COX10
|
COX10 heme A:farnesyltransferase cytochrome c oxidase assembly factor
|
|
COX11
|
COX11 cytochrome c oxidase copper chaperone
|
|
COX14
|
COX14 cytochrome c oxidase assembly factor
|
|
COX15
|
cytochrome c oxidase assembly homolog 15 (yeast)
|
|
COX16
|
COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)
|
|
COX18
|
COX18 cytochrome c oxidase assembly factor
|
|
COX20
|
COX20 cytochrome c oxidase assembly factor
|
|
COX4I1
|
cytochrome c oxidase subunit IV isoform 1
|
|
COX4I2
|
cytochrome c oxidase subunit IV isoform 2 (lung)
|
|
COX5A
|
cytochrome c oxidase subunit Va
|
|
COX5B
|
cytochrome c oxidase subunit Vb
|
|
COX6A1
|
cytochrome c oxidase subunit VIa polypeptide 1
|
|
COX6A2
|
cytochrome c oxidase subunit VIa polypeptide 2
|
|
COX6B1
|
cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous)
|
|
COX6B2
|
cytochrome c oxidase subunit VIb polypeptide 2 (testis)
|
|
COX6C
|
cytochrome c oxidase subunit VIc
|
|
COX7A1
|
cytochrome c oxidase subunit VIIa polypeptide 1 (muscle)
|
|
COX7A2
|
cytochrome c oxidase subunit VIIa polypeptide 2 (liver)
|
|
COX7A2L
|
cytochrome c oxidase subunit VIIa polypeptide 2 like
|
|
COX7B
|
cytochrome c oxidase subunit VIIb
|
|
COX7C
|
cytochrome c oxidase subunit VIIc
|
|
COX8A
|
cytochrome c oxidase subunit VIIIA (ubiquitous)
|
|
COX8C
|
cytochrome c oxidase subunit VIIIC
|
|
CPT2
|
carnitine palmitoyltransferase 2
|
|
CRLS1
|
cardiolipin synthase 1
|
|
CYCS
|
cytochrome c, somatic
|
|
CYP11A1
|
cytochrome P450, family 11, subfamily A, polypeptide 1
|
|
CYP11B1
|
cytochrome P450, family 11, subfamily B, polypeptide 1
|
|
CYP11B2
|
cytochrome P450, family 11, subfamily B, polypeptide 2
|
|
CYP1A1
|
cytochrome P450, family 1, subfamily A, polypeptide 1
|
|
CYP24A1
|
cytochrome P450, family 24, subfamily A, polypeptide 1
|
|
CYP2E1
|
cytochrome P450, family 2, subfamily E, polypeptide 1
|
|
DELE1
|
DAP3 binding cell death enhancer 1
|
|
DHFR2
|
dihydrofolate reductase 2
|
|
DHODH
|
dihydroorotate dehydrogenase (quinone)
|
|
DLGAP3
|
discs, large (Drosophila) homolog-associated protein 3
|
|
DMAC1
|
distal membrane arm assembly component 1
|
|
DMAC2L
|
distal membrane arm assembly component 2 like
|
|
DNAJC15
|
DnaJ (Hsp40) homolog, subfamily C, member 15
|
|
DNAJC19
|
DnaJ (Hsp40) homolog, subfamily C, member 19
|
|
DNAJC30
|
DnaJ (Hsp40) homolog, subfamily C, member 30
|
|
ECSIT
|
ECSIT signalling integrator
|
|
EFHD1
|
EF-hand domain family, member D1
|
|
ENDOG
|
endonuclease G
|
|
ETFDH
|
electron-transferring-flavoprotein dehydrogenase
|
|
EXOG
|
endo/exonuclease (5'-3'), endonuclease G-like
|
|
FECH
|
ferrochelatase
|
|
FLVCR1
|
feline leukemia virus subgroup C cellular receptor 1
|
|
FOXRED1
|
FAD-dependent oxidoreductase domain containing 1
|
|
GADD45GIP1
|
growth arrest and DNA-damage-inducible, gamma interacting protein 1
|
|
GCAT
|
glycine C-acetyltransferase
|
|
GHITM
|
growth hormone inducible transmembrane protein
|
|
GPD2
|
glycerol-3-phosphate dehydrogenase 2 (mitochondrial)
|
|
GRPEL1
|
GrpE-like 1, mitochondrial (E. coli)
|
|
GRPEL2
|
GrpE-like 2, mitochondrial (E. coli)
|
|
HADHA
|
hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit
|
|
HADHB
|
hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit
|
|
HCCS
|
holocytochrome c synthase
|
|
HIGD1A
|
HIG1 hypoxia inducible domain family, member 1A
|
|
HSD3B1
|
hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 1
|
|
HSD3B2
|
hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 2
|
|
HSPA9
|
heat shock 70kDa protein 9 (mortalin)
|
|
HSPD1
|
heat shock 60kDa protein 1 (chaperonin)
|
|
IFI6
|
interferon, alpha-inducible protein 6
|
|
IMMP1L
|
IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae)
|
|
IMMP2L
|
IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae)
|
|
IMMT
|
inner membrane protein, mitochondrial
|
|
KCNK9
|
potassium channel, two pore domain subfamily K, member 9
|
|
L2HGDH
|
L-2-hydroxyglutarate dehydrogenase
|
|
LDHB
|
lactate dehydrogenase B
|
|
LDHD
|
lactate dehydrogenase D
|
|
LETM1
|
leucine zipper-EF-hand containing transmembrane protein 1
|
|
LGALS3
|
lectin, galactoside-binding, soluble, 3
|
|
LRRK2
|
leucine-rich repeat kinase 2
|
|
MAIP1
|
matrix AAA peptidase interacting protein 1
|
|
MCU
|
mitochondrial calcium uniporter
|
|
MCUB
|
mitochondrial calcium uniporter dominant negative subunit beta
|
|
MCUR1
|
mitochondrial calcium uniporter regulator 1
|
|
MED12
|
mediator complex subunit 12
|
|
MGARP
|
mitochondria-localized glutamic acid-rich protein
|
|
MICOS10
|
mitochondrial contact site and cristae organizing system subunit 10
|
|
MICOS13
|
mitochondrial contact site and cristae organizing system subunit 13
|
|
MICU1
|
mitochondrial calcium uptake 1
|
|
MICU2
|
mitochondrial calcium uptake 2
|
|
MICU3
|
mitochondrial calcium uptake family, member 3
|
|
MPC1
|
mitochondrial pyruvate carrier 1
|
|
MPC1L
|
mitochondrial pyruvate carrier 1-like
|
|
MPC2
|
mitochondrial pyruvate carrier 2
|
|
MPV17
|
MpV17 mitochondrial inner membrane protein
|
|
MPV17L2
|
MPV17 mitochondrial membrane protein-like 2
|
|
MRPL1
|
mitochondrial ribosomal protein L1
|
|
MRPL10
|
mitochondrial ribosomal protein L10
|
|
MRPL11
|
mitochondrial ribosomal protein L11
|
|
MRPL12
|
mitochondrial ribosomal protein L12
|
|
MRPL13
|
mitochondrial ribosomal protein L13
|
|
MRPL14
|
mitochondrial ribosomal protein L14
|
|
MRPL15
|
mitochondrial ribosomal protein L15
|
|
MRPL16
|
mitochondrial ribosomal protein L16
|
|
MRPL17
|
mitochondrial ribosomal protein L17
|
|
MRPL18
|
mitochondrial ribosomal protein L18
|
|
MRPL19
|
mitochondrial ribosomal protein L19
|
|
MRPL20
|
mitochondrial ribosomal protein L20
|
|
MRPL21
|
mitochondrial ribosomal protein L21
|
|
MRPL23
|
mitochondrial ribosomal protein L23
|
|
MRPL24
|
mitochondrial ribosomal protein L24
|
|
MRPL3
|
mitochondrial ribosomal protein L3
|
|
MRPL30
|
mitochondrial ribosomal protein L30
|
|
MRPL32
|
mitochondrial ribosomal protein L32
|
|
MRPL33
|
mitochondrial ribosomal protein L33
|
|
MRPL34
|
mitochondrial ribosomal protein L34
|
|
MRPL35
|
mitochondrial ribosomal protein L35
|
|
MRPL36
|
mitochondrial ribosomal protein L36
|
|
MRPL37
|
mitochondrial ribosomal protein L37
|
|
MRPL38
|
mitochondrial ribosomal protein L38
|
|
MRPL39
|
mitochondrial ribosomal protein L39
|
|
MRPL4
|
mitochondrial ribosomal protein L4
|
|
MRPL40
|
mitochondrial ribosomal protein L40
|
|
MRPL41
|
mitochondrial ribosomal protein L41
|
|
MRPL42
|
mitochondrial ribosomal protein L42
|
|
MRPL43
|
mitochondrial ribosomal protein L43
|
|
MRPL44
|
mitochondrial ribosomal protein L44
|
|
MRPL45
|
mitochondrial ribosomal protein L45
|
|
MRPL46
|
mitochondrial ribosomal protein L46
|
|
MRPL47
|
mitochondrial ribosomal protein L47
|
|
MRPL48
|
mitochondrial ribosomal protein L48
|
|
MRPL49
|
mitochondrial ribosomal protein L49
|
|
MRPL50
|
mitochondrial ribosomal protein L50
|
|
MRPL51
|
mitochondrial ribosomal protein L51
|
|
MRPL52
|
mitochondrial ribosomal protein L52
|
|
MRPL53
|
mitochondrial ribosomal protein L53
|
|
MRPL54
|
mitochondrial ribosomal protein L54
|
|
MRPL55
|
mitochondrial ribosomal protein L55
|
|
MRPL57
|
mitochondrial ribosomal protein L57
|
|
MRPL58
|
mitochondrial ribosomal protein L58
|
|
MRPL9
|
mitochondrial ribosomal protein L9
|
|
MRPS10
|
mitochondrial ribosomal protein S10
|
|
MRPS11
|
mitochondrial ribosomal protein S11
|
|
MRPS14
|
mitochondrial ribosomal protein S14
|
|
MRPS15
|
mitochondrial ribosomal protein S15
|
|
MRPS16
|
mitochondrial ribosomal protein S16
|
|
MRPS17
|
mitochondrial ribosomal protein S17
|
|
MRPS18A
|
mitochondrial ribosomal protein S18A
|
|
MRPS18B
|
mitochondrial ribosomal protein S18B
|
|
MRPS18C
|
mitochondrial ribosomal protein S18C
|
|
MRPS2
|
mitochondrial ribosomal protein S2
|
|
MRPS21
|
mitochondrial ribosomal protein S21
|
|
MRPS22
|
mitochondrial ribosomal protein S22
|
|
MRPS23
|
mitochondrial ribosomal protein S23
|
|
MRPS24
|
mitochondrial ribosomal protein S24
|
|
MRPS25
|
mitochondrial ribosomal protein S25
|
|
MRPS26
|
mitochondrial ribosomal protein S26
|
|
MRPS27
|
mitochondrial ribosomal protein S27
|
|
MRPS30
|
mitochondrial ribosomal protein S30
|
|
MRPS31
|
mitochondrial ribosomal protein S31
|
|
MRPS33
|
mitochondrial ribosomal protein S33
|
|
MRPS34
|
mitochondrial ribosomal protein S34
|
|
MRPS35
|
mitochondrial ribosomal protein S35
|
|
MRPS36
|
mitochondrial ribosomal protein S36
|
|
MRPS5
|
mitochondrial ribosomal protein S5
|
|
MRPS6
|
mitochondrial ribosomal protein S6
|
|
MRPS7
|
mitochondrial ribosomal protein S7
|
|
MRPS9
|
mitochondrial ribosomal protein S9
|
|
MRS2
|
MRS2 magnesium transporter
|
|
MTFP1
|
mitochondrial fission process 1
|
|
MTG1
|
mitochondrial ribosome-associated GTPase 1
|
|
MTG2
|
mitochondrial ribosome-associated GTPase 2
|
|
MTLN
|
mitoregulin
|
|
MYOC
|
myocilin, trabecular meshwork inducible glucocorticoid response
|
|
NDUFA1
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
|
|
NDUFA10
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
|
|
NDUFA11
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa
|
|
NDUFA12
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12
|
|
NDUFA13
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
|
|
NDUFA2
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
|
|
NDUFA3
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa
|
|
NDUFA4
|
NDUFA4, mitochondrial complex associated
|
|
NDUFA5
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5
|
|
NDUFA6
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa
|
|
NDUFA7
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDa
|
|
NDUFA8
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
|
|
NDUFA9
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
|
|
NDUFAB1
|
NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
|
|
NDUFAF1
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 1
|
|
NDUFAF2
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 2
|
|
NDUFAF3
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 3
|
|
NDUFAF4
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 4
|
|
NDUFAF5
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 5
|
|
NDUFAF6
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 6
|
|
NDUFB1
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa
|
|
NDUFB10
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa
|
|
NDUFB11
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa
|
|
NDUFB2
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa
|
|
NDUFB3
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa
|
|
NDUFB4
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa
|
|
NDUFB5
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa
|
|
NDUFB6
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa
|
|
NDUFB7
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa
|
|
NDUFB8
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa
|
|
NDUFB9
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa
|
|
NDUFC1
|
NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa
|
|
NDUFC2
|
NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa
|
|
NDUFS1
|
NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
|
|
NDUFS2
|
NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
|
|
NDUFS3
|
NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
|
|
NDUFS4
|
NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
|
|
NDUFS5
|
NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)
|
|
NDUFS6
|
NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)
|
|
NDUFS7
|
NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
|
|
NDUFS8
|
NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
|
|
NDUFV1
|
NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa
|
|
NDUFV2
|
NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa
|
|
NDUFV3
|
NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa
|
|
NEU4
|
sialidase 4
|
|
NME4
|
NME/NM23 nucleoside diphosphate kinase 4
|
|
NME6
|
NME/NM23 nucleoside diphosphate kinase 6
|
|
NNT
|
nicotinamide nucleotide transhydrogenase
|
|
NOA1
|
nitric oxide associated 1
|
|
OMA1
|
OMA1 zinc metallopeptidase
|
|
OXA1L
|
oxidase (cytochrome c) assembly 1-like
|
|
PAM16
|
presequence translocase-associated motor 16 homolog (S. cerevisiae)
|
|
PARL
|
presenilin associated, rhomboid-like
|
|
PDE2A
|
phosphodiesterase 2A, cGMP-stimulated
|
|
PET100
|
PET100 homolog (S. cerevisiae)
|
|
PGAM5
|
phosphoglycerate mutase family member 5
|
|
PHB1
|
prohibitin 1
|
|
PHB2
|
prohibitin 2
|
|
PINK1
|
PTEN induced putative kinase 1
|
|
PLA2G4A
|
phospholipase A2, group IVA (cytosolic, calcium-dependent)
|
|
PLA2G4B
|
phospholipase A2, group IVB (cytosolic)
|
|
PLSCR3
|
phospholipid scramblase 3
|
|
PMPCA
|
peptidase (mitochondrial processing) alpha
|
|
PPOX
|
protoporphyrinogen oxidase
|
|
PRODH
|
proline dehydrogenase (oxidase) 1
|
|
PRODH2
|
proline dehydrogenase (oxidase) 2
|
|
PTCD3
|
pentatricopeptide repeat domain 3
|
|
RCC1L
|
RCC1 like
|
|
RDH13
|
retinol dehydrogenase 13 (all-trans/9-cis)
|
|
ROMO1
|
reactive oxygen species modulator 1
|
|
RPS3
|
ribosomal protein S3
|
|
RSAD2
|
radical S-adenosyl methionine domain containing 2
|
|
SCO1
|
SCO1 cytochrome c oxidase assembly protein
|
|
SCO2
|
SCO2 cytochrome c oxidase assembly protein
|
|
SDHA
|
succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
|
|
SDHB
|
succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
|
|
SDHC
|
succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa
|
|
SDHD
|
succinate dehydrogenase complex, subunit D, integral membrane protein
|
|
SDSL
|
serine dehydratase-like
|
|
SFXN1
|
sideroflexin 1
|
|
SFXN2
|
sideroflexin 2
|
|
SFXN3
|
sideroflexin 3
|
|
SFXN4
|
sideroflexin 4
|
|
SFXN5
|
sideroflexin 5
|
|
SHMT2
|
serine hydroxymethyltransferase 2 (mitochondrial)
|
|
SLC22A14
|
solute carrier family 22, member 14
|
|
SLC25A1
|
solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1
|
|
SLC25A10
|
solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10
|
|
SLC25A11
|
solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11
|
|
SLC25A12
|
solute carrier family 25 (aspartate/glutamate carrier), member 12
|
|
SLC25A13
|
solute carrier family 25 (aspartate/glutamate carrier), member 13
|
|
SLC25A14
|
solute carrier family 25 (mitochondrial carrier, brain), member 14
|
|
SLC25A15
|
solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15
|
|
SLC25A16
|
solute carrier family 25 (mitochondrial carrier), member 16
|
|
SLC25A18
|
solute carrier family 25 (glutamate carrier), member 18
|
|
SLC25A19
|
solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19
|
|
SLC25A2
|
solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 2
|
|
SLC25A20
|
solute carrier family 25 (carnitine/acylcarnitine translocase), member 20
|
|
SLC25A21
|
solute carrier family 25 (mitochondrial oxoadipate carrier), member 21
|
|
SLC25A22
|
solute carrier family 25 (mitochondrial carrier: glutamate), member 22
|
|
SLC25A26
|
solute carrier family 25 (S-adenosylmethionine carrier), member 26
|
|
SLC25A27
|
solute carrier family 25, member 27
|
|
SLC25A29
|
solute carrier family 25 (mitochondrial carnitine/acylcarnitine carrier), member 29
|
|
SLC25A3
|
solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3
|
|
SLC25A32
|
solute carrier family 25 (mitochondrial folate carrier), member 32
|
|
SLC25A38
|
solute carrier family 25, member 38
|
|
SLC25A39
|
solute carrier family 25, member 39
|
|
SLC25A4
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
|
|
SLC25A42
|
solute carrier family 25, member 42
|
|
SLC25A47
|
solute carrier family 25, member 47
|
|
SLC25A5
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5
|
|
SLC25A51
|
solute carrier family 25, member 51
|
|
SLC25A6
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 6
|
|
SLC30A2
|
solute carrier family 30 (zinc transporter), member 2
|
|
SLC35A4
|
solute carrier family 35, member A4
|
|
SLC41A3
|
solute carrier family 41, member 3
|
|
SLC8B1
|
solute carrier family 8 (sodium/lithium/calcium exchanger), member B1
|
|
SLC9B2
|
solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2
|
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SMDT1
|
single-pass membrane protein with aspartate-rich tail 1
|
|
SMIM20
|
small integral membrane protein 20
|
|
SPG7
|
spastic paraplegia 7 (pure and complicated autosomal recessive)
|
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SQOR
|
sulfide quinone oxidoreductase
|
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SRC
|
SRC proto-oncogene, non-receptor tyrosine kinase
|
|
STMP1
|
short transmembrane mitochondrial protein 1
|
|
STOML2
|
stomatin (EPB72)-like 2
|
|
SURF1
|
surfeit 1
|
|
TAFAZZIN
|
tafazzin, phospholipid-lysophospholipid transacylase
|
|
TAMM41
|
TAM41, mitochondrial translocator assembly and maintenance protein, homolog (S. cerevisiae)
|
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TIMM10
|
translocase of inner mitochondrial membrane 10 homolog (yeast)
|
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TIMM10B
|
translocase of inner mitochondrial membrane 10 homolog B (yeast)
|
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TIMM13
|
translocase of inner mitochondrial membrane 13 homolog (yeast)
|
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TIMM17A
|
translocase of inner mitochondrial membrane 17 homolog A (yeast)
|
|
TIMM17B
|
translocase of inner mitochondrial membrane 17 homolog B (yeast)
|
|
TIMM21
|
translocase of inner mitochondrial membrane 21 homolog (yeast)
|
|
TIMM22
|
translocase of inner mitochondrial membrane 22 homolog (yeast)
|
|
TIMM23
|
translocase of inner mitochondrial membrane 23 homolog (yeast)
|
|
TIMM29
|
translocase of inner mitochondrial membrane 29
|
|
TIMM44
|
translocase of inner mitochondrial membrane 44 homolog (yeast)
|
|
TIMM50
|
translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae)
|
|
TIMM9
|
translocase of inner mitochondrial membrane 9 homolog (yeast)
|
|
TIMMDC1
|
translocase of inner mitochondrial membrane domain containing 1
|
|
TMEM11
|
transmembrane protein 11
|
|
TMEM126A
|
transmembrane protein 126A
|
|
TMEM126B
|
transmembrane protein 126B
|
|
TMEM160
|
transmembrane protein 160
|
|
TMEM177
|
transmembrane protein 177
|
|
TMEM186
|
transmembrane protein 186
|
|
TMEM223
|
transmembrane protein 223
|
|
TMEM242
|
transmembrane protein 242
|
|
TMEM65
|
transmembrane protein 65
|
|
TMEM70
|
transmembrane protein 70
|
|
TOMM40
|
translocase of outer mitochondrial membrane 40 homolog (yeast)
|
|
TPGS1
|
tubulin polyglutamylase complex subunit 1
|
|
TRAP1
|
TNF receptor-associated protein 1
|
|
TRMT10B
|
tRNA methyltransferase 10 homolog B (S. cerevisiae)
|
|
TTC19
|
tetratricopeptide repeat domain 19
|
|
TYMS
|
thymidylate synthetase
|
|
UCP1
|
uncoupling protein 1 (mitochondrial, proton carrier)
|
|
UCP2
|
uncoupling protein 2 (mitochondrial, proton carrier)
|
|
UCP3
|
uncoupling protein 3 (mitochondrial, proton carrier)
|
|
UQCC1
|
ubiquinol-cytochrome c reductase complex assembly factor 1
|
|
UQCC2
|
ubiquinol-cytochrome c reductase complex assembly factor 2
|
|
UQCC3
|
ubiquinol-cytochrome c reductase complex assembly factor 3
|
|
UQCC4
|
ubiquinol-cytochrome c reductase complex assembly factor 4
|
|
UQCC5
|
ubiquinol-cytochrome c reductase complex assembly factor 5
|
|
UQCC6
|
ubiquinol-cytochrome c reductase complex assembly factor 6
|
|
UQCR10
|
ubiquinol-cytochrome c reductase, complex III subunit X
|
|
UQCR11
|
ubiquinol-cytochrome c reductase, complex III subunit XI
|
|
UQCRB
|
ubiquinol-cytochrome c reductase binding protein
|
|
UQCRC1
|
ubiquinol-cytochrome c reductase core protein I
|
|
UQCRC2
|
ubiquinol-cytochrome c reductase core protein II
|
|
UQCRFS1
|
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
|
|
UQCRH
|
ubiquinol-cytochrome c reductase hinge protein
|
|
UQCRQ
|
ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa
|
|
YME1L1
|
YME1-like 1 ATPase
|