| Symbol |
Name |
|
AADAT
|
aminoadipate aminotransferase
|
|
AASS
|
aminoadipate-semialdehyde synthase
|
|
ABAT
|
4-aminobutyrate aminotransferase
|
|
ABCE1
|
ATP-binding cassette, sub-family E (OABP), member 1
|
|
ABHD10
|
abhydrolase domain containing 10
|
|
ABHD11
|
abhydrolase domain containing 11
|
|
ACAA2
|
acetyl-CoA acyltransferase 2
|
|
ACAD10
|
acyl-CoA dehydrogenase family, member 10
|
|
ACAD8
|
acyl-CoA dehydrogenase family, member 8
|
|
ACADL
|
acyl-CoA dehydrogenase, long chain
|
|
ACADM
|
acyl-CoA dehydrogenase, C-4 to C-12 straight chain
|
|
ACADS
|
acyl-CoA dehydrogenase, C-2 to C-3 short chain
|
|
ACADSB
|
acyl-CoA dehydrogenase, short/branched chain
|
|
ACADVL
|
acyl-CoA dehydrogenase, very long chain
|
|
ACO2
|
aconitase 2, mitochondrial
|
|
ACOT11
|
acyl-CoA thioesterase 11
|
|
ACOT2
|
acyl-CoA thioesterase 2
|
|
ACOT9
|
acyl-CoA thioesterase 9
|
|
ACP6
|
acid phosphatase 6, lysophosphatidic
|
|
ACSF2
|
acyl-CoA synthetase family member 2
|
|
ACSF3
|
acyl-CoA synthetase family member 3
|
|
ACSM1
|
acyl-CoA synthetase medium-chain family member 1
|
|
ACSM2A
|
acyl-CoA synthetase medium-chain family member 2A
|
|
ACSM2B
|
acyl-CoA synthetase medium-chain family member 2B
|
|
ACSM3
|
acyl-CoA synthetase medium-chain family member 3
|
|
ACSM4
|
acyl-CoA synthetase medium-chain family member 4
|
|
ACSM5
|
acyl-CoA synthetase medium-chain family member 5
|
|
ACSM6
|
acyl-CoA synthetase medium-chain family member 6
|
|
ACSS1
|
acyl-CoA synthetase short-chain family member 1
|
|
ACSS2
|
acyl-CoA synthetase short-chain family member 2
|
|
ACSS3
|
acyl-CoA synthetase short-chain family member 3
|
|
ADHFE1
|
alcohol dehydrogenase, iron containing, 1
|
|
ADPRS
|
ADP-ribosylserine hydrolase
|
|
AGXT2
|
alanine--glyoxylate aminotransferase 2
|
|
AK3
|
adenylate kinase 3
|
|
AK4
|
adenylate kinase 4
|
|
AKR1B15
|
aldo-keto reductase family 1, member B15
|
|
ALAS1
|
5'-aminolevulinate synthase 1
|
|
ALAS2
|
5'-aminolevulinate synthase 2
|
|
ALDH18A1
|
aldehyde dehydrogenase 18 family, member A1
|
|
ALDH1B1
|
aldehyde dehydrogenase 1 family, member B1
|
|
ALDH1L2
|
aldehyde dehydrogenase 1 family, member L2
|
|
ALDH2
|
aldehyde dehydrogenase 2 family (mitochondrial)
|
|
ALDH4A1
|
aldehyde dehydrogenase 4 family, member A1
|
|
ALDH5A1
|
aldehyde dehydrogenase 5 family, member A1
|
|
ALDH6A1
|
aldehyde dehydrogenase 6 family, member A1
|
|
ALDH7A1
|
aldehyde dehydrogenase 7 family, member A1
|
|
ALKBH7
|
alkB, alkylation repair homolog 7 (E. coli)
|
|
AMT
|
aminomethyltransferase
|
|
ANGEL2
|
angel homolog 2 (Drosophila)
|
|
ARG2
|
arginase 2
|
|
ARHGAP11B
|
Rho GTPase activating protein 11B
|
|
ARL2
|
ADP-ribosylation factor-like 2
|
|
ARL2BP
|
ADP-ribosylation factor-like 2 binding protein
|
|
ASPNAT
|
aspartate N-acetyltransferase
|
|
ATP5F1A
|
ATP synthase F1 subunit alpha
|
|
ATP5F1B
|
ATP synthase F1 subunit beta
|
|
ATP5F1C
|
ATP synthase F1 subunit gamma
|
|
ATP5F1D
|
ATP synthase F1 subunit delta
|
|
ATP5F1E
|
ATP synthase F1 subunit epsilon
|
|
ATP5PB
|
ATP synthase peripheral stalk-membrane subunit b
|
|
ATXN3
|
ataxin 3
|
|
AUH
|
AU RNA binding protein/enoyl-CoA hydratase
|
|
AURKAIP1
|
aurora kinase A interacting protein 1
|
|
BCAT2
|
branched chain amino-acid transaminase 2, mitochondrial
|
|
BCKDHA
|
branched chain keto acid dehydrogenase E1, alpha polypeptide
|
|
BCKDHB
|
branched chain keto acid dehydrogenase E1, beta polypeptide
|
|
BCKDK
|
branched chain ketoacid dehydrogenase kinase
|
|
BCO2
|
beta-carotene oxygenase 2
|
|
BDH1
|
3-hydroxybutyrate dehydrogenase, type 1
|
|
BLOC1S1
|
biogenesis of lysosomal organelles complex-1, subunit 1
|
|
BOLA3
|
bolA family member 3
|
|
C1QBP
|
complement component 1, q subcomponent binding protein
|
|
CA5A
|
carbonic anhydrase VA, mitochondrial
|
|
CA5B
|
carbonic anhydrase VB, mitochondrial
|
|
CASQ1
|
calsequestrin 1 (fast-twitch, skeletal muscle)
|
|
CBR4
|
carbonyl reductase 4
|
|
CCAR2
|
cell cycle and apoptosis regulator 2
|
|
CCNB1
|
cyclin B1
|
|
CD163L1
|
CD163 molecule-like 1
|
|
CDK1
|
cyclin-dependent kinase 1
|
|
CDK5RAP1
|
CDK5 regulatory subunit associated protein 1
|
|
CDKN2A
|
cyclin-dependent kinase inhibitor 2A
|
|
CLPP
|
caseinolytic mitochondrial matrix peptidase proteolytic subunit
|
|
CLPX
|
caseinolytic mitochondrial matrix peptidase chaperone subunit
|
|
CMC1
|
C-x(9)-C motif containing 1
|
|
COASY
|
CoA synthase
|
|
COQ5
|
coenzyme Q5 homolog, methyltransferase (S. cerevisiae)
|
|
CS
|
citrate synthase
|
|
CSKMT
|
citrate synthase lysine methyltransferase
|
|
CYP11A1
|
cytochrome P450, family 11, subfamily A, polypeptide 1
|
|
CYP27A1
|
cytochrome P450, family 27, subfamily A, polypeptide 1
|
|
D2HGDH
|
D-2-hydroxyglutarate dehydrogenase
|
|
DARS2
|
aspartyl-tRNA synthetase 2, mitochondrial
|
|
DBT
|
dihydrolipoamide branched chain transacylase E2
|
|
DECR1
|
2,4-dienoyl CoA reductase 1, mitochondrial
|
|
DGLUCY
|
D-glutamate cyclase
|
|
DGUOK
|
deoxyguanosine kinase
|
|
DHFR2
|
dihydrofolate reductase 2
|
|
DHTKD1
|
dehydrogenase E1 and transketolase domain containing 1
|
|
DHX30
|
DEAH (Asp-Glu-Ala-His) box helicase 30
|
|
DLAT
|
dihydrolipoamide S-acetyltransferase
|
|
DLST
|
dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
|
|
DMGDH
|
dimethylglycine dehydrogenase
|
|
DNAJA3
|
DnaJ (Hsp40) homolog, subfamily A, member 3
|
|
DNAJC15
|
DnaJ (Hsp40) homolog, subfamily C, member 15
|
|
DNAJC19
|
DnaJ (Hsp40) homolog, subfamily C, member 19
|
|
DTD1
|
D-tyrosyl-tRNA deacylase 1
|
|
ECH1
|
enoyl CoA hydratase 1, peroxisomal
|
|
ECHS1
|
enoyl CoA hydratase, short chain, 1, mitochondrial
|
|
ECI1
|
enoyl-CoA delta isomerase 1
|
|
ELAC2
|
elaC ribonuclease Z 2
|
|
ERAL1
|
Era-like 12S mitochondrial rRNA chaperone 1
|
|
ERBB4
|
erb-b2 receptor tyrosine kinase 4
|
|
ETFA
|
electron-transfer-flavoprotein, alpha polypeptide
|
|
ETFB
|
electron-transfer-flavoprotein, beta polypeptide
|
|
ETFBKMT
|
electron transfer flavoprotein subunit beta lysine methyltransferase
|
|
ETHE1
|
ethylmalonic encephalopathy 1
|
|
ETNPPL
|
ethanolamine-phosphate phospho-lyase
|
|
FAHD1
|
fumarylacetoacetate hydrolase domain containing 1
|
|
FARS2
|
phenylalanyl-tRNA synthetase 2, mitochondrial
|
|
FASTK
|
Fas-activated serine/threonine kinase
|
|
FASTKD1
|
FAST kinase domains 1
|
|
FASTKD2
|
FAST kinase domains 2
|
|
FASTKD3
|
FAST kinase domains 3
|
|
FASTKD5
|
FAST kinase domains 5
|
|
FDPS
|
farnesyl diphosphate synthase
|
|
FDX1
|
ferredoxin 1
|
|
FDX2
|
ferredoxin 2
|
|
FDXR
|
ferredoxin reductase
|
|
FLAD1
|
flavin adenine dinucleotide synthetase 1
|
|
FOXO3
|
forkhead box O3
|
|
FOXO3B
|
forkhead box O3B pseudogene
|
|
FPGS
|
folylpolyglutamate synthase
|
|
FTMT
|
ferritin mitochondrial
|
|
FXN
|
frataxin
|
|
GADD45GIP1
|
growth arrest and DNA-damage-inducible, gamma interacting protein 1
|
|
GARS1
|
glycyl-tRNA synthetase 1
|
|
GCDH
|
glutaryl-CoA dehydrogenase
|
|
GCSH
|
glycine cleavage system protein H (aminomethyl carrier)
|
|
GFM1
|
G elongation factor, mitochondrial 1
|
|
GFM2
|
G elongation factor, mitochondrial 2
|
|
GLDC
|
glycine dehydrogenase (decarboxylating)
|
|
GLRX5
|
glutaredoxin 5
|
|
GLS2
|
glutaminase 2 (liver, mitochondrial)
|
|
GLYAT
|
glycine-N-acyltransferase
|
|
GOT2
|
glutamic-oxaloacetic transaminase 2, mitochondrial
|
|
GPT2
|
glutamic pyruvate transaminase (alanine aminotransferase) 2
|
|
GPX1
|
glutathione peroxidase 1
|
|
GRID1
|
glutamate receptor, ionotropic, delta 1
|
|
GRPEL1
|
GrpE-like 1, mitochondrial (E. coli)
|
|
GRPEL2
|
GrpE-like 2, mitochondrial (E. coli)
|
|
GRSF1
|
G-rich RNA sequence binding factor 1
|
|
GSR
|
glutathione reductase
|
|
GSTK1
|
glutathione S-transferase kappa 1
|
|
GSTZ1
|
glutathione S-transferase zeta 1
|
|
HADH
|
hydroxyacyl-CoA dehydrogenase
|
|
HAGH
|
hydroxyacylglutathione hydrolase
|
|
HIBADH
|
3-hydroxyisobutyrate dehydrogenase
|
|
HIBCH
|
3-hydroxyisobutyryl-CoA hydrolase
|
|
HMGCL
|
3-hydroxymethyl-3-methylglutaryl-CoA lyase
|
|
HMGCS2
|
3-hydroxy-3-methylglutaryl-CoA synthase 2 (mitochondrial)
|
|
HOGA1
|
4-hydroxy-2-oxoglutarate aldolase 1
|
|
HPDL
|
4-hydroxyphenylpyruvate dioxygenase-like
|
|
HSD17B10
|
hydroxysteroid (17-beta) dehydrogenase 10
|
|
HSD17B8
|
hydroxysteroid (17-beta) dehydrogenase 8
|
|
HSPA9
|
heat shock 70kDa protein 9 (mortalin)
|
|
HSPD1
|
heat shock 60kDa protein 1 (chaperonin)
|
|
HSPE1
|
heat shock 10kDa protein 1
|
|
HTD2
|
hydroxyacyl-thioester dehydratase type 2
|
|
HYKK
|
hydroxylysine kinase
|
|
IARS2
|
isoleucyl-tRNA synthetase 2, mitochondrial
|
|
IBA57
|
IBA57, iron-sulfur cluster assembly homolog (S. cerevisiae)
|
|
IDH2
|
isocitrate dehydrogenase 2 (NADP+), mitochondrial
|
|
IDH3A
|
isocitrate dehydrogenase 3 (NAD+) alpha
|
|
IDH3B
|
isocitrate dehydrogenase 3 (NAD+) beta
|
|
IDH3G
|
isocitrate dehydrogenase 3 (NAD+) gamma
|
|
ISCA1
|
iron-sulfur cluster assembly 1
|
|
ISCA2
|
iron-sulfur cluster assembly 2
|
|
ISCU
|
iron-sulfur cluster assembly enzyme
|
|
IVD
|
isovaleryl-CoA dehydrogenase
|
|
KARS1
|
lysyl-tRNA synthetase 1
|
|
LACTB2
|
lactamase, beta 2
|
|
LARS2
|
leucyl-tRNA synthetase 2, mitochondrial
|
|
LDHAL6B
|
lactate dehydrogenase A-like 6B
|
|
LDHD
|
lactate dehydrogenase D
|
|
LDLR
|
low density lipoprotein receptor
|
|
LIAS
|
lipoic acid synthetase
|
|
LIPT1
|
lipoyltransferase 1
|
|
LIPT2
|
lipoyl(octanoyl) transferase 2 (putative)
|
|
LONP1
|
lon peptidase 1, mitochondrial
|
|
LRPPRC
|
leucine-rich pentatricopeptide repeat containing
|
|
LRRK2
|
leucine-rich repeat kinase 2
|
|
LYRM4
|
LYR motif containing 4
|
|
LYRM7
|
LYR motif containing 7
|
|
MAIP1
|
matrix AAA peptidase interacting protein 1
|
|
MARS2
|
methionyl-tRNA synthetase 2, mitochondrial
|
|
MCAT
|
malonyl CoA:ACP acyltransferase (mitochondrial)
|
|
MCCC1
|
methylcrotonoyl-CoA carboxylase 1 (alpha)
|
|
MCCC2
|
methylcrotonoyl-CoA carboxylase 2 (beta)
|
|
MCEE
|
methylmalonyl CoA epimerase
|
|
MDH2
|
malate dehydrogenase 2, NAD (mitochondrial)
|
|
MECR
|
mitochondrial trans-2-enoyl-CoA reductase
|
|
METTL15
|
methyltransferase like 15
|
|
METTL17
|
methyltransferase like 17
|
|
METTL4
|
methyltransferase like 4
|
|
METTL8
|
methyltransferase like 8
|
|
MIURF
|
mitochondrial elongation factor 1 upstream open reading frame
|
|
MLYCD
|
malonyl-CoA decarboxylase
|
|
MMAA
|
methylmalonic aciduria (cobalamin deficiency) cblA type
|
|
MMAB
|
methylmalonic aciduria (cobalamin deficiency) cblB type
|
|
MMUT
|
methylmalonyl-CoA mutase
|
|
MPST
|
mercaptopyruvate sulfurtransferase
|
|
MRM1
|
mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae)
|
|
MRM2
|
mitochondrial rRNA methyltransferase 2
|
|
MRM3
|
mitochondrial rRNA methyltransferase 3
|
|
MRPL11
|
mitochondrial ribosomal protein L11
|
|
MRPL12
|
mitochondrial ribosomal protein L12
|
|
MRPL13
|
mitochondrial ribosomal protein L13
|
|
MRPL18
|
mitochondrial ribosomal protein L18
|
|
MRPL20
|
mitochondrial ribosomal protein L20
|
|
MRPL30
|
mitochondrial ribosomal protein L30
|
|
MRPL32
|
mitochondrial ribosomal protein L32
|
|
MRPL34
|
mitochondrial ribosomal protein L34
|
|
MRPL35
|
mitochondrial ribosomal protein L35
|
|
MRPL37
|
mitochondrial ribosomal protein L37
|
|
MRPL39
|
mitochondrial ribosomal protein L39
|
|
MRPL40
|
mitochondrial ribosomal protein L40
|
|
MRPL43
|
mitochondrial ribosomal protein L43
|
|
MRPL48
|
mitochondrial ribosomal protein L48
|
|
MRPL49
|
mitochondrial ribosomal protein L49
|
|
MRPL51
|
mitochondrial ribosomal protein L51
|
|
MRPL57
|
mitochondrial ribosomal protein L57
|
|
MRPL58
|
mitochondrial ribosomal protein L58
|
|
MRPL9
|
mitochondrial ribosomal protein L9
|
|
MRPS10
|
mitochondrial ribosomal protein S10
|
|
MRPS14
|
mitochondrial ribosomal protein S14
|
|
MRPS15
|
mitochondrial ribosomal protein S15
|
|
MRPS2
|
mitochondrial ribosomal protein S2
|
|
MRPS22
|
mitochondrial ribosomal protein S22
|
|
MRPS34
|
mitochondrial ribosomal protein S34
|
|
MRRF
|
mitochondrial ribosome recycling factor
|
|
MTERF1
|
mitochondrial transcription termination factor 1
|
|
MTERF2
|
mitochondrial transcription termination factor 2
|
|
MTERF3
|
mitochondrial transcription termination factor 3
|
|
MTERF4
|
mitochondrial transcription termination factor 4
|
|
MTG1
|
mitochondrial ribosome-associated GTPase 1
|
|
MTG2
|
mitochondrial ribosome-associated GTPase 2
|
|
MTHFD1L
|
methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like
|
|
MTHFD2
|
methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase
|
|
MTHFD2L
|
methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2-like
|
|
MTRES1
|
mitochondrial transcription rescue factor 1
|
|
MTRF1L
|
mitochondrial translational release factor 1-like
|
|
MTRFR
|
mitochondrial translation release factor in rescue
|
|
MYG1
|
MYG1 exonuclease
|
|
NADK2
|
NAD kinase 2, mitochondrial
|
|
NAGS
|
N-acetylglutamate synthase
|
|
NAXD
|
NAD(P)HX dehydratase
|
|
NAXE
|
NAD(P)HX epimerase
|
|
NDUFA9
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
|
|
NDUFAB1
|
NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
|
|
NDUFAF7
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 7
|
|
NDUFAF8
|
NADH:ubiquinone oxidoreductase complex assembly factor 8
|
|
NDUFB8
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa
|
|
NDUFS1
|
NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
|
|
NDUFS2
|
NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
|
|
NDUFS3
|
NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
|
|
NDUFS7
|
NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
|
|
NDUFS8
|
NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
|
|
NFS1
|
NFS1 cysteine desulfurase
|
|
NFU1
|
NFU1 iron-sulfur cluster scaffold
|
|
NGRN
|
neugrin, neurite outgrowth associated
|
|
NIPSNAP1
|
nipsnap homolog 1 (C. elegans)
|
|
NIPSNAP2
|
nipsnap homolog 2
|
|
NME6
|
NME/NM23 nucleoside diphosphate kinase 6
|
|
NMNAT3
|
nicotinamide nucleotide adenylyltransferase 3
|
|
NR3C1
|
nuclear receptor subfamily 3, group C, member 1 (glucocorticoid receptor)
|
|
NRDC
|
nardilysin convertase
|
|
NSUN3
|
NOP2/Sun domain family, member 3
|
|
NSUN4
|
NOP2/Sun domain family, member 4
|
|
NT5M
|
5',3'-nucleotidase, mitochondrial
|
|
NUBPL
|
nucleotide binding protein-like
|
|
NUDT1
|
nudix (nucleoside diphosphate linked moiety X)-type motif 1
|
|
NUDT13
|
nudix (nucleoside diphosphate linked moiety X)-type motif 13
|
|
NUDT2
|
nudix (nucleoside diphosphate linked moiety X)-type motif 2
|
|
NUDT9
|
nudix (nucleoside diphosphate linked moiety X)-type motif 9
|
|
OAT
|
ornithine aminotransferase
|
|
OGDH
|
oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
|
|
OGDHL
|
oxoglutarate dehydrogenase-like
|
|
OGG1
|
8-oxoguanine DNA glycosylase
|
|
OTC
|
ornithine carbamoyltransferase
|
|
OXA1L
|
oxidase (cytochrome c) assembly 1-like
|
|
OXCT1
|
3-oxoacid CoA transferase 1
|
|
OXCT2
|
3-oxoacid CoA transferase 2
|
|
OXSM
|
3-oxoacyl-ACP synthase, mitochondrial
|
|
PABPC5
|
poly(A) binding protein, cytoplasmic 5
|
|
PAM16
|
presequence translocase-associated motor 16 homolog (S. cerevisiae)
|
|
PCCA
|
propionyl CoA carboxylase, alpha polypeptide
|
|
PCCB
|
propionyl CoA carboxylase, beta polypeptide
|
|
PCDHB11
|
protocadherin beta 11
|
|
PCDHGA5
|
protocadherin gamma subfamily A, 5
|
|
PCK2
|
phosphoenolpyruvate carboxykinase 2 (mitochondrial)
|
|
PDE12
|
phosphodiesterase 12
|
|
PDE2A
|
phosphodiesterase 2A, cGMP-stimulated
|
|
PDHA1
|
pyruvate dehydrogenase (lipoamide) alpha 1
|
|
PDHA2
|
pyruvate dehydrogenase (lipoamide) alpha 2
|
|
PDHB
|
pyruvate dehydrogenase (lipoamide) beta
|
|
PDHX
|
pyruvate dehydrogenase complex, component X
|
|
PDK2
|
pyruvate dehydrogenase kinase, isozyme 2
|
|
PDK3
|
pyruvate dehydrogenase kinase, isozyme 3
|
|
PDK4
|
pyruvate dehydrogenase kinase, isozyme 4
|
|
PDP2
|
pyruvate dehyrogenase phosphatase catalytic subunit 2
|
|
PDPK1
|
3-phosphoinositide dependent protein kinase 1
|
|
PDPR
|
pyruvate dehydrogenase phosphatase regulatory subunit
|
|
PDSS1
|
prenyl (decaprenyl) diphosphate synthase, subunit 1
|
|
PDSS2
|
prenyl (decaprenyl) diphosphate synthase, subunit 2
|
|
PGK1
|
phosphoglycerate kinase 1
|
|
PHYKPL
|
5-phosphohydroxy-L-lysine phospho-lyase
|
|
PIN4
|
peptidylprolyl cis/trans isomerase, NIMA-interacting 4
|
|
PITRM1
|
pitrilysin metallopeptidase 1
|
|
PLPP6
|
phospholipid phosphatase 6
|
|
PM20D1
|
peptidase M20 domain containing 1
|
|
PMPCA
|
peptidase (mitochondrial processing) alpha
|
|
PMPCB
|
peptidase (mitochondrial processing) beta
|
|
PNPT1
|
polyribonucleotide nucleotidyltransferase 1
|
|
POLDIP2
|
polymerase (DNA-directed), delta interacting protein 2
|
|
POLG2
|
polymerase (DNA directed), gamma 2, accessory subunit
|
|
POLGARF
|
POLG alternative reading frame
|
|
POLRMT
|
polymerase (RNA) mitochondrial (DNA directed)
|
|
PPA2
|
pyrophosphatase (inorganic) 2
|
|
PPM1K
|
protein phosphatase, Mg2+/Mn2+ dependent, 1K
|
|
PPTC7
|
PTC7 protein phosphatase homolog (S. cerevisiae)
|
|
PRDX3
|
peroxiredoxin 3
|
|
PRDX5
|
peroxiredoxin 5
|
|
PRIMPOL
|
primase and polymerase (DNA-directed)
|
|
PRKCA
|
protein kinase C, alpha
|
|
PROC
|
protein C (inactivator of coagulation factors Va and VIIIa)
|
|
PRORP
|
protein only RNase P catalytic subunit
|
|
PTCD1
|
pentatricopeptide repeat domain 1
|
|
PTCD3
|
pentatricopeptide repeat domain 3
|
|
PUS1
|
pseudouridylate synthase 1
|
|
PYCR1
|
pyrroline-5-carboxylate reductase 1
|
|
PYCR2
|
pyrroline-5-carboxylate reductase family, member 2
|
|
PYROXD2
|
pyridine nucleotide-disulphide oxidoreductase domain 2
|
|
QARS1
|
glutaminyl-tRNA synthetase 1
|
|
RARS2
|
arginyl-tRNA synthetase 2, mitochondrial
|
|
RCC1L
|
RCC1 like
|
|
REXO2
|
RNA exonuclease 2
|
|
RIDA
|
reactive intermediate imine deaminase A homolog
|
|
RNASEL
|
ribonuclease L (2',5'-oligoisoadenylate synthetase-dependent)
|
|
RPS3
|
ribosomal protein S3
|
|
RPUSD3
|
RNA pseudouridylate synthase domain containing 3
|
|
RPUSD4
|
RNA pseudouridylate synthase domain containing 4
|
|
RTN4IP1
|
reticulon 4 interacting protein 1
|
|
SARDH
|
sarcosine dehydrogenase
|
|
SARS2
|
seryl-tRNA synthetase 2, mitochondrial
|
|
SDHA
|
succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
|
|
SDHAF1
|
succinate dehydrogenase complex assembly factor 1
|
|
SDHAF3
|
succinate dehydrogenase complex assembly factor 3
|
|
SDHAF4
|
succinate dehydrogenase complex assembly factor 4
|
|
SDHB
|
succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
|
|
SHMT2
|
serine hydroxymethyltransferase 2 (mitochondrial)
|
|
SIRT3
|
sirtuin 3
|
|
SIRT4
|
sirtuin 4
|
|
SIRT5
|
sirtuin 5
|
|
SLIRP
|
SRA stem-loop interacting RNA binding protein
|
|
SMDT1
|
single-pass membrane protein with aspartate-rich tail 1
|
|
SOAT1
|
sterol O-acyltransferase 1
|
|
SOD1
|
superoxide dismutase 1, soluble
|
|
SOD2
|
superoxide dismutase 2, mitochondrial
|
|
SP8
|
Sp8 transcription factor
|
|
SPATA18
|
spermatogenesis associated 18
|
|
SSBP1
|
single-stranded DNA binding protein 1, mitochondrial
|
|
ST20-MTHFS
|
ST20-MTHFS readthrough
|
|
SUCLA2
|
succinate-CoA ligase, ADP-forming, beta subunit
|
|
SUCLG1
|
succinate-CoA ligase, alpha subunit
|
|
SUCLG2
|
succinate-CoA ligase, GDP-forming, beta subunit
|
|
SUOX
|
sulfite oxidase
|
|
SUPV3L1
|
suppressor of var1, 3-like 1 (S. cerevisiae)
|
|
TBRG4
|
transforming growth factor beta regulator 4
|
|
TEFM
|
transcription elongation factor, mitochondrial
|
|
TFAM
|
transcription factor A, mitochondrial
|
|
TFB1M
|
transcription factor B1, mitochondrial
|
|
TFB2M
|
transcription factor B2, mitochondrial
|
|
THEM4
|
thioesterase superfamily member 4
|
|
THEM5
|
thioesterase superfamily member 5
|
|
TIMM44
|
translocase of inner mitochondrial membrane 44 homolog (yeast)
|
|
TK2
|
thymidine kinase 2, mitochondrial
|
|
TMLHE
|
trimethyllysine hydroxylase, epsilon
|
|
TP53AIP1
|
tumor protein p53 regulated apoptosis inducing protein 1
|
|
TRAP1
|
TNF receptor-associated protein 1
|
|
TRIT1
|
tRNA isopentenyltransferase 1
|
|
TRMT10C
|
tRNA methyltransferase 10 homolog C (S. cerevisiae)
|
|
TRMT2B
|
tRNA methyltransferase 2 homolog B (S. cerevisiae)
|
|
TRMT5
|
tRNA methyltransferase 5
|
|
TRMT61B
|
tRNA methyltransferase 61B
|
|
TRNT1
|
tRNA nucleotidyl transferase, CCA-adding, 1
|
|
TRUB2
|
TruB pseudouridine (psi) synthase family member 2
|
|
TSTD1
|
thiosulfate sulfurtransferase (rhodanese)-like domain containing 1
|
|
TWNK
|
twinkle mtDNA helicase
|
|
TXN2
|
thioredoxin 2
|
|
TXNRD2
|
thioredoxin reductase 2
|
|
TYMS
|
thymidylate synthetase
|
|
UQCC2
|
ubiquinol-cytochrome c reductase complex assembly factor 2
|
|
UQCRFS1
|
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
|
|
WARS2
|
tryptophanyl tRNA synthetase 2, mitochondrial
|
|
YARS2
|
tyrosyl-tRNA synthetase 2, mitochondrial
|
|
YWHAG
|
tyrosine 3-monooxygenase/tryptophan 5-monooxygenase activation protein, gamma
|
