mitochondrial membrane Gene Set

Dataset GO Cellular Component Annotations 2025
Category structural or functional annotations
Type cellular component
Description Either of the lipid bilayers that surround the mitochondrion and form the mitochondrial envelope. (Gene Ontology, GO_0031966)
External Link http://amigo.geneontology.org/amigo/term/GO:0031966
Similar Terms
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Genes

596 proteins localized to the mitochondrial membrane cellular component from the curated GO Cellular Component Annotations 2025 dataset.

Symbol Name
ABCB10 ATP-binding cassette, sub-family B (MDR/TAP), member 10
ABCB6 ATP-binding cassette, sub-family B (MDR/TAP), member 6 (Langereis blood group)
ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7
ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8
ABCD1 ATP-binding cassette, sub-family D (ALD), member 1
ACACB acetyl-CoA carboxylase beta
ACAD11 acyl-CoA dehydrogenase family, member 11
ACAD9 acyl-CoA dehydrogenase family, member 9
ACADM acyl-CoA dehydrogenase, C-4 to C-12 straight chain
ACADVL acyl-CoA dehydrogenase, very long chain
ACSL1 acyl-CoA synthetase long-chain family member 1
ACSL3 acyl-CoA synthetase long-chain family member 3
ACSL4 acyl-CoA synthetase long-chain family member 4
ADCK1 aarF domain containing kinase 1
AFG1L AFG1 like ATPase
AFG3L2 AFG3-like AAA ATPase 2
AGK acylglycerol kinase
AGPAT4 1-acylglycerol-3-phosphate O-acyltransferase 4
AGPAT5 1-acylglycerol-3-phosphate O-acyltransferase 5
AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1
AIFM2 apoptosis-inducing factor, mitochondrion-associated, 2
AIFM3 apoptosis-inducing factor, mitochondrion-associated, 3
ALAS2 5'-aminolevulinate synthase 2
ALDH18A1 aldehyde dehydrogenase 18 family, member A1
ALPL alkaline phosphatase, liver/bone/kidney
AMBRA1 autophagy/beclin-1 regulator 1
ANGEL1 angel homolog 1 (Drosophila)
APOO apolipoprotein O
APOOL apolipoprotein O-like
APP amyloid beta (A4) precursor protein
AQP8 aquaporin 8
ARMC12 armadillo repeat containing 12
ASPNAT aspartate N-acetyltransferase
ATAD1 ATPase family, AAA domain containing 1
ATAD3A ATPase family, AAA domain containing 3A
ATCAY ataxia, cerebellar, Cayman type
ATP5F1A ATP synthase F1 subunit alpha
ATP5F1B ATP synthase F1 subunit beta
ATP5F1C ATP synthase F1 subunit gamma
ATP5F1D ATP synthase F1 subunit delta
ATP5F1E ATP synthase F1 subunit epsilon
ATP5MC1 ATP synthase membrane subunit c locus 1
ATP5MC2 ATP synthase membrane subunit c locus 2
ATP5MC3 ATP synthase membrane subunit c locus 3
ATP5ME ATP synthase membrane subunit e
ATP5MF ATP synthase membrane subunit f
ATP5MG ATP synthase membrane subunit g
ATP5MGL ATP synthase membrane subunit g like
ATP5MJ ATP synthase membrane subunit j
ATP5MK ATP synthase membrane subunit k
ATP5PB ATP synthase peripheral stalk-membrane subunit b
ATP5PD ATP synthase peripheral stalk subunit d
ATP5PF ATP synthase peripheral stalk subunit F6
ATP5PO ATP synthase peripheral stalk subunit OSCP
ATPAF1 ATP synthase mitochondrial F1 complex assembly factor 1
ATPAF2 ATP synthase mitochondrial F1 complex assembly factor 2
ATXN3 ataxin 3
AURKAIP1 aurora kinase A interacting protein 1
BAD BCL2-associated agonist of cell death
BAK1 BCL2-antagonist/killer 1
BAX BCL2-associated X protein
BBC3 BCL2 binding component 3
BCL2 B-cell CLL/lymphoma 2
BCL2A1 BCL2-related protein A1
BCL2L1 BCL2-like 1
BCL2L10 BCL2-like 10 (apoptosis facilitator)
BCL2L11 BCL2-like 11 (apoptosis facilitator)
BCL2L2 BCL2-like 2
BCS1L BC1 (ubiquinol-cytochrome c reductase) synthesis-like
BID BH3 interacting domain death agonist
BMF Bcl2 modifying factor
BNIP1 BCL2/adenovirus E1B 19kDa interacting protein 1
BNIP3 BCL2/adenovirus E1B 19kDa interacting protein 3
BNIP3L BCL2/adenovirus E1B 19kDa interacting protein 3-like
BOK BCL2-related ovarian killer
BPHL biphenyl hydrolase-like (serine hydrolase)
C11ORF65 chromosome 11 open reading frame 65
C19ORF12 chromosome 19 open reading frame 12
CABS1 calcium-binding protein, spermatid-specific 1
CASP8 caspase 8, apoptosis-related cysteine peptidase
CCDC51 coiled-coil domain containing 51
CCNI cyclin I
CDS2 CDP-diacylglycerol synthase (phosphatidate cytidylyltransferase) 2
CHCHD1 coiled-coil-helix-coiled-coil-helix domain containing 1
CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3
CHCHD6 coiled-coil-helix-coiled-coil-helix domain containing 6
CHDH choline dehydrogenase
CIBAR1 CBY1 interacting BAR domain containing 1
CISD1 CDGSH iron sulfur domain 1
CISD2 CDGSH iron sulfur domain 2
CKMT1A creatine kinase, mitochondrial 1A
CKMT2 creatine kinase, mitochondrial 2 (sarcomeric)
CLPX caseinolytic mitochondrial matrix peptidase chaperone subunit
CLU clusterin
COA1 cytochrome c oxidase assembly factor 1 homolog (S. cerevisiae)
COA3 cytochrome c oxidase assembly factor 3
COA5 cytochrome c oxidase assembly factor 5
COASY CoA synthase
COQ10A coenzyme Q10 homolog A (S. cerevisiae)
COQ10B coenzyme Q10 homolog B (S. cerevisiae)
COQ2 coenzyme Q2 4-hydroxybenzoate polyprenyltransferase
COQ3 coenzyme Q3 methyltransferase
COQ4 coenzyme Q4
COQ5 coenzyme Q5 homolog, methyltransferase (S. cerevisiae)
COQ6 coenzyme Q6 monooxygenase
COQ7 coenzyme Q7 homolog, ubiquinone (yeast)
COQ9 coenzyme Q9
COX10 COX10 heme A:farnesyltransferase cytochrome c oxidase assembly factor
COX11 COX11 cytochrome c oxidase copper chaperone
COX14 COX14 cytochrome c oxidase assembly factor
COX15 cytochrome c oxidase assembly homolog 15 (yeast)
COX16 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)
COX18 COX18 cytochrome c oxidase assembly factor
COX20 COX20 cytochrome c oxidase assembly factor
COX4I1 cytochrome c oxidase subunit IV isoform 1
COX4I2 cytochrome c oxidase subunit IV isoform 2 (lung)
COX5A cytochrome c oxidase subunit Va
COX5B cytochrome c oxidase subunit Vb
COX6A1 cytochrome c oxidase subunit VIa polypeptide 1
COX6A2 cytochrome c oxidase subunit VIa polypeptide 2
COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous)
COX6B2 cytochrome c oxidase subunit VIb polypeptide 2 (testis)
COX6C cytochrome c oxidase subunit VIc
COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle)
COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver)
COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like
COX7B cytochrome c oxidase subunit VIIb
COX7C cytochrome c oxidase subunit VIIc
COX8A cytochrome c oxidase subunit VIIIA (ubiquitous)
COX8C cytochrome c oxidase subunit VIIIC
CPT1A carnitine palmitoyltransferase 1A (liver)
CPT1B carnitine palmitoyltransferase 1B (muscle)
CPT2 carnitine palmitoyltransferase 2
CRLS1 cardiolipin synthase 1
CYB5A cytochrome b5 type A (microsomal)
CYB5B cytochrome b5 type B (outer mitochondrial membrane)
CYB5R3 cytochrome b5 reductase 3
CYCS cytochrome c, somatic
CYP11A1 cytochrome P450, family 11, subfamily A, polypeptide 1
CYP11B1 cytochrome P450, family 11, subfamily B, polypeptide 1
CYP11B2 cytochrome P450, family 11, subfamily B, polypeptide 2
CYP1A1 cytochrome P450, family 1, subfamily A, polypeptide 1
CYP24A1 cytochrome P450, family 24, subfamily A, polypeptide 1
CYP27B1 cytochrome P450, family 27, subfamily B, polypeptide 1
CYP2E1 cytochrome P450, family 2, subfamily E, polypeptide 1
DAO D-amino-acid oxidase
DARS2 aspartyl-tRNA synthetase 2, mitochondrial
DCAKD dephospho-CoA kinase domain containing
DELE1 DAP3 binding cell death enhancer 1
DHFR2 dihydrofolate reductase 2
DHODH dihydroorotate dehydrogenase (quinone)
DLGAP3 discs, large (Drosophila) homolog-associated protein 3
DMAC1 distal membrane arm assembly component 1
DMAC2L distal membrane arm assembly component 2 like
DMPK dystrophia myotonica-protein kinase
DNAJC11 DnaJ (Hsp40) homolog, subfamily C, member 11
DNAJC15 DnaJ (Hsp40) homolog, subfamily C, member 15
DNAJC19 DnaJ (Hsp40) homolog, subfamily C, member 19
DNAJC30 DnaJ (Hsp40) homolog, subfamily C, member 30
DNM1L dynamin 1-like
ECSIT ECSIT signalling integrator
EFHD1 EF-hand domain family, member D1
ENDOG endonuclease G
ETFDH electron-transferring-flavoprotein dehydrogenase
EXD2 exonuclease 3'-5' domain containing 2
EXOG endo/exonuclease (5'-3'), endonuclease G-like
FAM210B family with sequence similarity 210, member B
FATE1 fetal and adult testis expressed 1
FBXL4 F-box and leucine-rich repeat protein 4
FECH ferrochelatase
FIS1 fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae)
FLVCR1 feline leukemia virus subgroup C cellular receptor 1
FLVCR2 feline leukemia virus subgroup C cellular receptor family, member 2
FOXO3 forkhead box O3
FOXRED1 FAD-dependent oxidoreductase domain containing 1
FUNDC1 FUN14 domain containing 1
FUNDC2 FUN14 domain containing 2
FZD9 frizzled class receptor 9
GADD45GIP1 growth arrest and DNA-damage-inducible, gamma interacting protein 1
GCAT glycine C-acetyltransferase
GDAP1 ganglioside induced differentiation associated protein 1
GDNF glial cell derived neurotrophic factor
GHITM growth hormone inducible transmembrane protein
GK2 glycerol kinase 2
GPAM glycerol-3-phosphate acyltransferase, mitochondrial
GPAT2 glycerol-3-phosphate acyltransferase 2, mitochondrial
GPD2 glycerol-3-phosphate dehydrogenase 2 (mitochondrial)
GPER1 G protein-coupled estrogen receptor 1
GRPEL1 GrpE-like 1, mitochondrial (E. coli)
GRPEL2 GrpE-like 2, mitochondrial (E. coli)
GSDMD gasdermin D
HADHA hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit
HADHB hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit
HAX1 HCLS1 associated protein X-1
HCCS holocytochrome c synthase
HIGD1A HIG1 hypoxia inducible domain family, member 1A
HINT2 histidine triad nucleotide binding protein 2
HMOX1 heme oxygenase 1
HOOK2 hook microtubule-tethering protein 2
HSD3B1 hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 1
HSD3B2 hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 2
HSPA9 heat shock 70kDa protein 9 (mortalin)
HSPD1 heat shock 60kDa protein 1 (chaperonin)
IFI27 interferon, alpha-inducible protein 27
IFI27L1 interferon, alpha-inducible protein 27-like 1
IFI27L2 interferon, alpha-inducible protein 27-like 2
IFI6 interferon, alpha-inducible protein 6
IKBKE inhibitor of kappa light polypeptide gene enhancer in B-cells, kinase epsilon
IMMP1L IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae)
IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae)
IMMT inner membrane protein, mitochondrial
IRGM immunity-related GTPase family, M
KCNK9 potassium channel, two pore domain subfamily K, member 9
KMO kynurenine 3-monooxygenase (kynurenine 3-hydroxylase)
L2HGDH L-2-hydroxyglutarate dehydrogenase
LDHB lactate dehydrogenase B
LDHD lactate dehydrogenase D
LETM1 leucine zipper-EF-hand containing transmembrane protein 1
LGALS3 lectin, galactoside-binding, soluble, 3
LPIN1 lipin 1
LRRK2 leucine-rich repeat kinase 2
LYRM7 LYR motif containing 7
MAIP1 matrix AAA peptidase interacting protein 1
MAOA monoamine oxidase A
MAOB monoamine oxidase B
MAPKAP1 mitogen-activated protein kinase associated protein 1
MARCHF5 membrane associated ring-CH-type finger 5
MAVS mitochondrial antiviral signaling protein
MCL1 myeloid cell leukemia 1
MCU mitochondrial calcium uniporter
MCUB mitochondrial calcium uniporter dominant negative subunit beta
MCUR1 mitochondrial calcium uniporter regulator 1
MED12 mediator complex subunit 12
MFF mitochondrial fission factor
MFN1 mitofusin 1
MFN2 mitofusin 2
MGARP mitochondria-localized glutamic acid-rich protein
MGST3 microsomal glutathione S-transferase 3
MICOS10 mitochondrial contact site and cristae organizing system subunit 10
MICOS13 mitochondrial contact site and cristae organizing system subunit 13
MICU1 mitochondrial calcium uptake 1
MICU2 mitochondrial calcium uptake 2
MICU3 mitochondrial calcium uptake family, member 3
MIEF2 mitochondrial elongation factor 2
MIURF mitochondrial elongation factor 1 upstream open reading frame
MOAP1 modulator of apoptosis 1
MPC1 mitochondrial pyruvate carrier 1
MPC1L mitochondrial pyruvate carrier 1-like
MPC2 mitochondrial pyruvate carrier 2
MPV17 MpV17 mitochondrial inner membrane protein
MPV17L2 MPV17 mitochondrial membrane protein-like 2
MRPL1 mitochondrial ribosomal protein L1
MRPL10 mitochondrial ribosomal protein L10
MRPL11 mitochondrial ribosomal protein L11
MRPL12 mitochondrial ribosomal protein L12
MRPL13 mitochondrial ribosomal protein L13
MRPL14 mitochondrial ribosomal protein L14
MRPL15 mitochondrial ribosomal protein L15
MRPL16 mitochondrial ribosomal protein L16
MRPL17 mitochondrial ribosomal protein L17
MRPL18 mitochondrial ribosomal protein L18
MRPL19 mitochondrial ribosomal protein L19
MRPL20 mitochondrial ribosomal protein L20
MRPL21 mitochondrial ribosomal protein L21
MRPL23 mitochondrial ribosomal protein L23
MRPL24 mitochondrial ribosomal protein L24
MRPL3 mitochondrial ribosomal protein L3
MRPL30 mitochondrial ribosomal protein L30
MRPL32 mitochondrial ribosomal protein L32
MRPL33 mitochondrial ribosomal protein L33
MRPL34 mitochondrial ribosomal protein L34
MRPL35 mitochondrial ribosomal protein L35
MRPL36 mitochondrial ribosomal protein L36
MRPL37 mitochondrial ribosomal protein L37
MRPL38 mitochondrial ribosomal protein L38
MRPL39 mitochondrial ribosomal protein L39
MRPL4 mitochondrial ribosomal protein L4
MRPL40 mitochondrial ribosomal protein L40
MRPL41 mitochondrial ribosomal protein L41
MRPL42 mitochondrial ribosomal protein L42
MRPL43 mitochondrial ribosomal protein L43
MRPL44 mitochondrial ribosomal protein L44
MRPL45 mitochondrial ribosomal protein L45
MRPL46 mitochondrial ribosomal protein L46
MRPL47 mitochondrial ribosomal protein L47
MRPL48 mitochondrial ribosomal protein L48
MRPL49 mitochondrial ribosomal protein L49
MRPL50 mitochondrial ribosomal protein L50
MRPL51 mitochondrial ribosomal protein L51
MRPL52 mitochondrial ribosomal protein L52
MRPL53 mitochondrial ribosomal protein L53
MRPL54 mitochondrial ribosomal protein L54
MRPL55 mitochondrial ribosomal protein L55
MRPL57 mitochondrial ribosomal protein L57
MRPL58 mitochondrial ribosomal protein L58
MRPL9 mitochondrial ribosomal protein L9
MRPS10 mitochondrial ribosomal protein S10
MRPS11 mitochondrial ribosomal protein S11
MRPS14 mitochondrial ribosomal protein S14
MRPS15 mitochondrial ribosomal protein S15
MRPS16 mitochondrial ribosomal protein S16
MRPS17 mitochondrial ribosomal protein S17
MRPS18A mitochondrial ribosomal protein S18A
MRPS18B mitochondrial ribosomal protein S18B
MRPS18C mitochondrial ribosomal protein S18C
MRPS2 mitochondrial ribosomal protein S2
MRPS21 mitochondrial ribosomal protein S21
MRPS22 mitochondrial ribosomal protein S22
MRPS23 mitochondrial ribosomal protein S23
MRPS24 mitochondrial ribosomal protein S24
MRPS25 mitochondrial ribosomal protein S25
MRPS26 mitochondrial ribosomal protein S26
MRPS27 mitochondrial ribosomal protein S27
MRPS30 mitochondrial ribosomal protein S30
MRPS31 mitochondrial ribosomal protein S31
MRPS33 mitochondrial ribosomal protein S33
MRPS34 mitochondrial ribosomal protein S34
MRPS35 mitochondrial ribosomal protein S35
MRPS36 mitochondrial ribosomal protein S36
MRPS5 mitochondrial ribosomal protein S5
MRPS6 mitochondrial ribosomal protein S6
MRPS7 mitochondrial ribosomal protein S7
MRPS9 mitochondrial ribosomal protein S9
MRS2 MRS2 magnesium transporter
MSTO1 misato 1, mitochondrial distribution and morphology regulator
MTARC1 mitochondrial amidoxime reducing component 1
MTARC2 mitochondrial amidoxime reducing component 2
MTCH2 mitochondrial carrier 2
MTERF3 mitochondrial transcription termination factor 3
MTFP1 mitochondrial fission process 1
MTG1 mitochondrial ribosome-associated GTPase 1
MTG2 mitochondrial ribosome-associated GTPase 2
MTLN mitoregulin
MTX1 metaxin 1
MTX2 metaxin 2
MUL1 mitochondrial E3 ubiquitin protein ligase 1
MYO19 myosin XIX
MYOC myocilin, trabecular meshwork inducible glucocorticoid response
NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
NDUFA11 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa
NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12
NDUFA13 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa
NDUFA4 NDUFA4, mitochondrial complex associated
NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5
NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa
NDUFA7 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDa
NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1
NDUFAF2 NADH dehydrogenase (ubiquinone) complex I, assembly factor 2
NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3
NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4
NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5
NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6
NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa
NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa
NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa
NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa
NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa
NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa
NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa
NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa
NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa
NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa
NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa
NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa
NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa
NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)
NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)
NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa
NDUFV2 NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa
NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa
NEU4 sialidase 4
NGRN neugrin, neurite outgrowth associated
NIPSNAP2 nipsnap homolog 2
NLRX1 NLR family member X1
NME3 NME/NM23 nucleoside diphosphate kinase 3
NME4 NME/NM23 nucleoside diphosphate kinase 4
NME6 NME/NM23 nucleoside diphosphate kinase 6
NNT nicotinamide nucleotide transhydrogenase
NRAS neuroblastoma RAS viral (v-ras) oncogene homolog
OGDH oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
OMA1 OMA1 zinc metallopeptidase
OXA1L oxidase (cytochrome c) assembly 1-like
PAM16 presequence translocase-associated motor 16 homolog (S. cerevisiae)
PARL presenilin associated, rhomboid-like
PDE2A phosphodiesterase 2A, cGMP-stimulated
PET100 PET100 homolog (S. cerevisiae)
PGAM5 phosphoglycerate mutase family member 5
PGRMC1 progesterone receptor membrane component 1
PHB1 prohibitin 1
PHB2 prohibitin 2
PIGBOS1 PIGB opposite strand 1
PINK1 PTEN induced putative kinase 1
PLA2G4A phospholipase A2, group IVA (cytosolic, calcium-dependent)
PLA2G4B phospholipase A2, group IVB (cytosolic)
PLA2G4C phospholipase A2, group IVC (cytosolic, calcium-independent)
PLD6 phospholipase D family, member 6
PLEKHN1 pleckstrin homology domain containing, family N member 1
PLSCR3 phospholipid scramblase 3
PMAIP1 phorbol-12-myristate-13-acetate-induced protein 1
PMPCA peptidase (mitochondrial processing) alpha
PPOX protoporphyrinogen oxidase
PPP2R2B protein phosphatase 2, regulatory subunit B, beta
PPTC7 PTC7 protein phosphatase homolog (S. cerevisiae)
PRNP prion protein
PRODH proline dehydrogenase (oxidase) 1
PRODH2 proline dehydrogenase (oxidase) 2
PTCD3 pentatricopeptide repeat domain 3
PTRH2 peptidyl-tRNA hydrolase 2
QTRT1 queuine tRNA-ribosyltransferase 1
QTRT2 queuine tRNA-ribosyltransferase accessory subunit 2
RAB11FIP5 RAB11 family interacting protein 5 (class I)
RAB32 RAB32, member RAS oncogene family
RAC2 ras-related C3 botulinum toxin substrate 2 (rho family, small GTP binding protein Rac2)
RARS2 arginyl-tRNA synthetase 2, mitochondrial
RCC1L RCC1 like
RDH13 retinol dehydrogenase 13 (all-trans/9-cis)
RHOD ras homolog family member D
RHOT1 ras homolog family member T1
RHOT2 ras homolog family member T2
RMDN3 regulator of microtubule dynamics 3
RNASE3 ribonuclease, RNase A family, 3
RNF144B ring finger protein 144B
ROMO1 reactive oxygen species modulator 1
RPS27A ribosomal protein S27a
RPS3 ribosomal protein S3
RSAD2 radical S-adenosyl methionine domain containing 2
RTN4IP1 reticulon 4 interacting protein 1
SAMM50 SAMM50 sorting and assembly machinery component
SCO1 SCO1 cytochrome c oxidase assembly protein
SCO2 SCO2 cytochrome c oxidase assembly protein
SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa
SDHD succinate dehydrogenase complex, subunit D, integral membrane protein
SDSL serine dehydratase-like
SEPTIN4 septin 4
SFXN1 sideroflexin 1
SFXN2 sideroflexin 2
SFXN3 sideroflexin 3
SFXN4 sideroflexin 4
SFXN5 sideroflexin 5
SHMT2 serine hydroxymethyltransferase 2 (mitochondrial)
SLC22A14 solute carrier family 22, member 14
SLC22A3 solute carrier family 22 (organic cation transporter), member 3
SLC22A4 solute carrier family 22 (organic cation/zwitterion transporter), member 4
SLC25A1 solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1
SLC25A10 solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10
SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11
SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12
SLC25A13 solute carrier family 25 (aspartate/glutamate carrier), member 13
SLC25A14 solute carrier family 25 (mitochondrial carrier, brain), member 14
SLC25A15 solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15
SLC25A16 solute carrier family 25 (mitochondrial carrier), member 16
SLC25A18 solute carrier family 25 (glutamate carrier), member 18
SLC25A19 solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19
SLC25A2 solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 2
SLC25A20 solute carrier family 25 (carnitine/acylcarnitine translocase), member 20
SLC25A21 solute carrier family 25 (mitochondrial oxoadipate carrier), member 21
SLC25A22 solute carrier family 25 (mitochondrial carrier: glutamate), member 22
SLC25A26 solute carrier family 25 (S-adenosylmethionine carrier), member 26
SLC25A27 solute carrier family 25, member 27
SLC25A28 solute carrier family 25 (mitochondrial iron transporter), member 28
SLC25A29 solute carrier family 25 (mitochondrial carnitine/acylcarnitine carrier), member 29
SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3
SLC25A32 solute carrier family 25 (mitochondrial folate carrier), member 32
SLC25A33 solute carrier family 25 (pyrimidine nucleotide carrier), member 33
SLC25A37 solute carrier family 25 (mitochondrial iron transporter), member 37
SLC25A38 solute carrier family 25, member 38
SLC25A39 solute carrier family 25, member 39
SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
SLC25A42 solute carrier family 25, member 42
SLC25A46 solute carrier family 25, member 46
SLC25A47 solute carrier family 25, member 47
SLC25A5 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5
SLC25A51 solute carrier family 25, member 51
SLC25A6 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 6
SLC29A3 solute carrier family 29 (equilibrative nucleoside transporter), member 3
SLC30A2 solute carrier family 30 (zinc transporter), member 2
SLC30A9 solute carrier family 30 (zinc transporter), member 9
SLC35A4 solute carrier family 35, member A4
SLC39A9 solute carrier family 39, member 9
SLC41A3 solute carrier family 41, member 3
SLC44A1 solute carrier family 44 (choline transporter), member 1
SLC44A2 solute carrier family 44 (choline transporter), member 2
SLC8A3 solute carrier family 8 (sodium/calcium exchanger), member 3
SLC8B1 solute carrier family 8 (sodium/lithium/calcium exchanger), member B1
SLC9B2 solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2
SMDT1 single-pass membrane protein with aspartate-rich tail 1
SMIM20 small integral membrane protein 20
SMIM26 small integral membrane protein 26
SMIM30 small integral membrane protein 30
SPART spartin
SPATA18 spermatogenesis associated 18
SPATA19 spermatogenesis associated 19
SPG7 spastic paraplegia 7 (pure and complicated autosomal recessive)
SPIRE1 spire-type actin nucleation factor 1
SQOR sulfide quinone oxidoreductase
SRC SRC proto-oncogene, non-receptor tyrosine kinase
STARD7 StAR-related lipid transfer (START) domain containing 7
STING1 stimulator of interferon response cGAMP interactor 1
STMP1 short transmembrane mitochondrial protein 1
STOML2 stomatin (EPB72)-like 2
SURF1 surfeit 1
SYNJ2BP synaptojanin 2 binding protein
TAFAZZIN tafazzin, phospholipid-lysophospholipid transacylase
TAMM41 TAM41, mitochondrial translocator assembly and maintenance protein, homolog (S. cerevisiae)
TIGAR TP53 induced glycolysis regulatory phosphatase
TIMM10 translocase of inner mitochondrial membrane 10 homolog (yeast)
TIMM10B translocase of inner mitochondrial membrane 10 homolog B (yeast)
TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast)
TIMM17A translocase of inner mitochondrial membrane 17 homolog A (yeast)
TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast)
TIMM21 translocase of inner mitochondrial membrane 21 homolog (yeast)
TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast)
TIMM23 translocase of inner mitochondrial membrane 23 homolog (yeast)
TIMM29 translocase of inner mitochondrial membrane 29
TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast)
TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae)
TIMM9 translocase of inner mitochondrial membrane 9 homolog (yeast)
TIMMDC1 translocase of inner mitochondrial membrane domain containing 1
TMEM11 transmembrane protein 11
TMEM126A transmembrane protein 126A
TMEM126B transmembrane protein 126B
TMEM14A transmembrane protein 14A
TMEM14B transmembrane protein 14B
TMEM14C transmembrane protein 14C
TMEM160 transmembrane protein 160
TMEM177 transmembrane protein 177
TMEM186 transmembrane protein 186
TMEM223 transmembrane protein 223
TMEM242 transmembrane protein 242
TMEM65 transmembrane protein 65
TMEM70 transmembrane protein 70
TOMM20 translocase of outer mitochondrial membrane 20 homolog (yeast)
TOMM22 translocase of outer mitochondrial membrane 22 homolog (yeast)
TOMM34 translocase of outer mitochondrial membrane 34
TOMM40 translocase of outer mitochondrial membrane 40 homolog (yeast)
TOMM5 translocase of outer mitochondrial membrane 5 homolog (yeast)
TOMM6 translocase of outer mitochondrial membrane 6 homolog (yeast)
TOMM7 translocase of outer mitochondrial membrane 7 homolog (yeast)
TOMM70 translocase of outer mitochondrial membrane 70
TPGS1 tubulin polyglutamylase complex subunit 1
TRABD TraB domain containing
TRAF3IP3 TRAF3 interacting protein 3
TRAP1 TNF receptor-associated protein 1
TRMT10B tRNA methyltransferase 10 homolog B (S. cerevisiae)
TSPO translocator protein (18kDa)
TSPO2 translocator protein 2
TTC19 tetratricopeptide repeat domain 19
TUFM Tu translation elongation factor, mitochondrial
TYMS thymidylate synthetase
UBA52 ubiquitin A-52 residue ribosomal protein fusion product 1
UBB ubiquitin B
UBC ubiquitin C
UCP1 uncoupling protein 1 (mitochondrial, proton carrier)
UCP2 uncoupling protein 2 (mitochondrial, proton carrier)
UCP3 uncoupling protein 3 (mitochondrial, proton carrier)
UFL1 UFM1-specific ligase 1
ULK1 unc-51 like autophagy activating kinase 1
UQCC1 ubiquinol-cytochrome c reductase complex assembly factor 1
UQCC2 ubiquinol-cytochrome c reductase complex assembly factor 2
UQCC3 ubiquinol-cytochrome c reductase complex assembly factor 3
UQCC4 ubiquinol-cytochrome c reductase complex assembly factor 4
UQCC5 ubiquinol-cytochrome c reductase complex assembly factor 5
UQCC6 ubiquinol-cytochrome c reductase complex assembly factor 6
UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X
UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI
UQCRB ubiquinol-cytochrome c reductase binding protein
UQCRC1 ubiquinol-cytochrome c reductase core protein I
UQCRC2 ubiquinol-cytochrome c reductase core protein II
UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
UQCRH ubiquinol-cytochrome c reductase hinge protein
UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa
USP30 ubiquitin specific peptidase 30
VAT1 vesicle amine transport 1
VDAC1 voltage-dependent anion channel 1
VDAC2 voltage-dependent anion channel 2
VDAC3 voltage-dependent anion channel 3
VPS13A vacuolar protein sorting 13 homolog A (S. cerevisiae)
VPS13C vacuolar protein sorting 13 homolog C (S. cerevisiae)
VRK2 vaccinia related kinase 2
YME1L1 YME1-like 1 ATPase
YWHAE tyrosine 3-monooxygenase/tryptophan 5-monooxygenase activation protein, epsilon
ZNFX1 zinc finger, NFX1-type containing 1