Symbol |
Name |
C10ORF2
|
chromosome 10 open reading frame 2
|
COX10
|
COX10 heme A:farnesyltransferase cytochrome c oxidase assembly factor
|
COX15
|
cytochrome c oxidase assembly homolog 15 (yeast)
|
COX6B1
|
cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous)
|
DNA2
|
DNA replication helicase/nuclease 2
|
FASTKD2
|
FAST kinase domains 2
|
FOXRED1
|
FAD-dependent oxidoreductase domain containing 1
|
LRPPRC
|
leucine-rich pentatricopeptide repeat containing
|
MGME1
|
mitochondrial genome maintenance exonuclease 1
|
MTFMT
|
mitochondrial methionyl-tRNA formyltransferase
|
NDUFA1
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
|
NDUFA10
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
|
NDUFA11
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa
|
NDUFA12
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12
|
NDUFA2
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
|
NDUFA4
|
NDUFA4, mitochondrial complex associated
|
NDUFAF2
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 2
|
NDUFAF5
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 5
|
NDUFS1
|
NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
|
NDUFS2
|
NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
|
NDUFS3
|
NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
|
NDUFS4
|
NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
|
NDUFS7
|
NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
|
NDUFS8
|
NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
|
NDUFV1
|
NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa
|
PDHA1
|
pyruvate dehydrogenase (lipoamide) alpha 1
|
PDHB
|
pyruvate dehydrogenase (lipoamide) beta
|
PDSS2
|
prenyl (decaprenyl) diphosphate synthase, subunit 2
|
POLG
|
polymerase (DNA directed), gamma
|
POLG2
|
polymerase (DNA directed), gamma 2, accessory subunit
|
RRM2B
|
ribonucleotide reductase M2 B (TP53 inducible)
|
SCO1
|
SCO1 cytochrome c oxidase assembly protein
|
SCO2
|
SCO2 cytochrome c oxidase assembly protein
|
SDHA
|
succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
|
SLC25A4
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
|
SURF1
|
surfeit 1
|
TACO1
|
translational activator of mitochondrially encoded cytochrome c oxidase I
|
TIMM8A
|
translocase of inner mitochondrial membrane 8 homolog A (yeast)
|
TYMP
|
thymidine phosphorylase
|