| Symbol |
Name |
|
AADAT
|
aminoadipate aminotransferase
|
|
AASS
|
aminoadipate-semialdehyde synthase
|
|
ABAT
|
4-aminobutyrate aminotransferase
|
|
ABCA12
|
ATP-binding cassette, sub-family A (ABC1), member 12
|
|
ABCA8
|
ATP-binding cassette, sub-family A (ABC1), member 8
|
|
ABCB10
|
ATP-binding cassette, sub-family B (MDR/TAP), member 10
|
|
ABCB6
|
ATP-binding cassette, sub-family B (MDR/TAP), member 6 (Langereis blood group)
|
|
ABCB7
|
ATP-binding cassette, sub-family B (MDR/TAP), member 7
|
|
ABCB8
|
ATP-binding cassette, sub-family B (MDR/TAP), member 8
|
|
ABCD3
|
ATP-binding cassette, sub-family D (ALD), member 3
|
|
ABCF2
|
ATP-binding cassette, sub-family F (GCN20), member 2
|
|
ABCG2
|
ATP-binding cassette, sub-family G (WHITE), member 2 (Junior blood group)
|
|
ACAA2
|
acetyl-CoA acyltransferase 2
|
|
ACACB
|
acetyl-CoA carboxylase beta
|
|
ACAD11
|
acyl-CoA dehydrogenase family, member 11
|
|
ACAD8
|
acyl-CoA dehydrogenase family, member 8
|
|
ACADL
|
acyl-CoA dehydrogenase, long chain
|
|
ACADM
|
acyl-CoA dehydrogenase, C-4 to C-12 straight chain
|
|
ACADS
|
acyl-CoA dehydrogenase, C-2 to C-3 short chain
|
|
ACADSB
|
acyl-CoA dehydrogenase, short/branched chain
|
|
ACADVL
|
acyl-CoA dehydrogenase, very long chain
|
|
ACAT1
|
acetyl-CoA acetyltransferase 1
|
|
ACO2
|
aconitase 2, mitochondrial
|
|
ACSL1
|
acyl-CoA synthetase long-chain family member 1
|
|
ACSL3
|
acyl-CoA synthetase long-chain family member 3
|
|
ACSL4
|
acyl-CoA synthetase long-chain family member 4
|
|
ACSL5
|
acyl-CoA synthetase long-chain family member 5
|
|
ACSL6
|
acyl-CoA synthetase long-chain family member 6
|
|
ACSM1
|
acyl-CoA synthetase medium-chain family member 1
|
|
ACSM2A
|
acyl-CoA synthetase medium-chain family member 2A
|
|
ACSM2B
|
acyl-CoA synthetase medium-chain family member 2B
|
|
ACSM3
|
acyl-CoA synthetase medium-chain family member 3
|
|
ACSM4
|
acyl-CoA synthetase medium-chain family member 4
|
|
ACSM5
|
acyl-CoA synthetase medium-chain family member 5
|
|
ACSS1
|
acyl-CoA synthetase short-chain family member 1
|
|
ADAP2
|
ArfGAP with dual PH domains 2
|
|
ADCK4
|
aarF domain containing kinase 4
|
|
ADHFE1
|
alcohol dehydrogenase, iron containing, 1
|
|
ADPRHL2
|
ADP-ribosylhydrolase like 2
|
|
AFG3L2
|
AFG3-like AAA ATPase 2
|
|
AGK
|
acylglycerol kinase
|
|
AGPAT5
|
1-acylglycerol-3-phosphate O-acyltransferase 5
|
|
AGXT
|
alanine-glyoxylate aminotransferase
|
|
AGXT2
|
alanine--glyoxylate aminotransferase 2
|
|
AIFM1
|
apoptosis-inducing factor, mitochondrion-associated, 1
|
|
AIFM2
|
apoptosis-inducing factor, mitochondrion-associated, 2
|
|
AIFM3
|
apoptosis-inducing factor, mitochondrion-associated, 3
|
|
AK2
|
adenylate kinase 2
|
|
AK3
|
adenylate kinase 3
|
|
AKAP1
|
A kinase (PRKA) anchor protein 1
|
|
ALAS1
|
5'-aminolevulinate synthase 1
|
|
ALAS2
|
5'-aminolevulinate synthase 2
|
|
ALDH18A1
|
aldehyde dehydrogenase 18 family, member A1
|
|
ALDH1B1
|
aldehyde dehydrogenase 1 family, member B1
|
|
ALDH2
|
aldehyde dehydrogenase 2 family (mitochondrial)
|
|
ALDH3A2
|
aldehyde dehydrogenase 3 family, member A2
|
|
ALDH4A1
|
aldehyde dehydrogenase 4 family, member A1
|
|
ALDH5A1
|
aldehyde dehydrogenase 5 family, member A1
|
|
ALDH6A1
|
aldehyde dehydrogenase 6 family, member A1
|
|
ALDH7A1
|
aldehyde dehydrogenase 7 family, member A1
|
|
ALKBH7
|
alkB, alkylation repair homolog 7 (E. coli)
|
|
AMBRA1
|
autophagy/beclin-1 regulator 1
|
|
ANXA1
|
annexin A1
|
|
APEX2
|
APEX nuclease (apurinic/apyrimidinic endonuclease) 2
|
|
APOOL
|
apolipoprotein O-like
|
|
ARG2
|
arginase 2
|
|
ARL2
|
ADP-ribosylation factor-like 2
|
|
ARL2BP
|
ADP-ribosylation factor-like 2 binding protein
|
|
ARMCX3
|
armadillo repeat containing, X-linked 3
|
|
ASS1
|
argininosuccinate synthase 1
|
|
ATAD3A
|
ATPase family, AAA domain containing 3A
|
|
ATAD3B
|
ATPase family, AAA domain containing 3B
|
|
ATCAY
|
ataxia, cerebellar, Cayman type
|
|
ATF2
|
activating transcription factor 2
|
|
ATG14
|
autophagy related 14
|
|
ATG4D
|
autophagy related 4D, cysteine peptidase
|
|
ATG5
|
autophagy related 5
|
|
ATP5A1
|
ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle
|
|
ATP5B
|
ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide
|
|
ATP5C1
|
ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1
|
|
ATP5D
|
ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit
|
|
ATP5E
|
ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit
|
|
ATP5F1
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1
|
|
ATP5G1
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9)
|
|
ATP5G2
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9)
|
|
ATP5G3
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9)
|
|
ATP5H
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d
|
|
ATP5I
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E
|
|
ATP5J
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6
|
|
ATP5J2
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2
|
|
ATP5L
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G
|
|
ATP5L2
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G2
|
|
ATP5O
|
ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit
|
|
ATP5S
|
ATP synthase, H+ transporting, mitochondrial Fo complex, subunit s (factor B)
|
|
ATPIF1
|
ATPase inhibitory factor 1
|
|
ATXN3
|
ataxin 3
|
|
ATXN3L
|
ataxin 3-like
|
|
AUH
|
AU RNA binding protein/enoyl-CoA hydratase
|
|
AURKAIP1
|
aurora kinase A interacting protein 1
|
|
BAD
|
BCL2-associated agonist of cell death
|
|
BAK1
|
BCL2-antagonist/killer 1
|
|
BAX
|
BCL2-associated X protein
|
|
BCAT2
|
branched chain amino-acid transaminase 2, mitochondrial
|
|
BCKDHA
|
branched chain keto acid dehydrogenase E1, alpha polypeptide
|
|
BCKDHB
|
branched chain keto acid dehydrogenase E1, beta polypeptide
|
|
BCKDK
|
branched chain ketoacid dehydrogenase kinase
|
|
BCL2
|
B-cell CLL/lymphoma 2
|
|
BCL2A1
|
BCL2-related protein A1
|
|
BCL2L1
|
BCL2-like 1
|
|
BCL2L10
|
BCL2-like 10 (apoptosis facilitator)
|
|
BCL2L11
|
BCL2-like 11 (apoptosis facilitator)
|
|
BCL2L13
|
BCL2-like 13 (apoptosis facilitator)
|
|
BCL2L2
|
BCL2-like 2
|
|
BCO2
|
beta-carotene oxygenase 2
|
|
BCS1L
|
BC1 (ubiquinol-cytochrome c reductase) synthesis-like
|
|
BDH1
|
3-hydroxybutyrate dehydrogenase, type 1
|
|
BDNF
|
brain-derived neurotrophic factor
|
|
BID
|
BH3 interacting domain death agonist
|
|
BIK
|
BCL2-interacting killer (apoptosis-inducing)
|
|
BLOC1S1
|
biogenesis of lysosomal organelles complex-1, subunit 1
|
|
BMF
|
Bcl2 modifying factor
|
|
BNIP3
|
BCL2/adenovirus E1B 19kDa interacting protein 3
|
|
BNIP3L
|
BCL2/adenovirus E1B 19kDa interacting protein 3-like
|
|
BOK
|
BCL2-related ovarian killer
|
|
BRI3BP
|
BRI3 binding protein
|
|
BTD
|
biotinidase
|
|
C10ORF2
|
chromosome 10 open reading frame 2
|
|
C14ORF2
|
chromosome 14 open reading frame 2
|
|
C19ORF12
|
chromosome 19 open reading frame 12
|
|
C1QBP
|
complement component 1, q subcomponent binding protein
|
|
C9ORF89
|
chromosome 9 open reading frame 89
|
|
CA5A
|
carbonic anhydrase VA, mitochondrial
|
|
CA5B
|
carbonic anhydrase VB, mitochondrial
|
|
CABS1
|
calcium-binding protein, spermatid-specific 1
|
|
CANX
|
calnexin
|
|
CARS2
|
cysteinyl-tRNA synthetase 2, mitochondrial (putative)
|
|
CASP8
|
caspase 8, apoptosis-related cysteine peptidase
|
|
CASQ1
|
calsequestrin 1 (fast-twitch, skeletal muscle)
|
|
CAT
|
catalase
|
|
CBR4
|
carbonyl reductase 4
|
|
CCAR2
|
cell cycle and apoptosis regulator 2
|
|
CCDC109B
|
coiled-coil domain containing 109B
|
|
CDS2
|
CDP-diacylglycerol synthase (phosphatidate cytidylyltransferase) 2
|
|
CEP89
|
centrosomal protein 89kDa
|
|
CHCHD1
|
coiled-coil-helix-coiled-coil-helix domain containing 1
|
|
CHCHD10
|
coiled-coil-helix-coiled-coil-helix domain containing 10
|
|
CHCHD3
|
coiled-coil-helix-coiled-coil-helix domain containing 3
|
|
CHCHD4
|
coiled-coil-helix-coiled-coil-helix domain containing 4
|
|
CHCHD5
|
coiled-coil-helix-coiled-coil-helix domain containing 5
|
|
CHCHD6
|
coiled-coil-helix-coiled-coil-helix domain containing 6
|
|
CHCHD7
|
coiled-coil-helix-coiled-coil-helix domain containing 7
|
|
CHDH
|
choline dehydrogenase
|
|
CHPF
|
chondroitin polymerizing factor
|
|
CIAPIN1
|
cytokine induced apoptosis inhibitor 1
|
|
CIDEA
|
cell death-inducing DFFA-like effector a
|
|
CISD1
|
CDGSH iron sulfur domain 1
|
|
CISD2
|
CDGSH iron sulfur domain 2
|
|
CKMT2
|
creatine kinase, mitochondrial 2 (sarcomeric)
|
|
CLPP
|
caseinolytic mitochondrial matrix peptidase proteolytic subunit
|
|
CLPX
|
caseinolytic mitochondrial matrix peptidase chaperone subunit
|
|
CLU
|
clusterin
|
|
CNP
|
2',3'-cyclic nucleotide 3' phosphodiesterase
|
|
COA1
|
cytochrome c oxidase assembly factor 1 homolog (S. cerevisiae)
|
|
COA3
|
cytochrome c oxidase assembly factor 3
|
|
COA7
|
cytochrome c oxidase assembly factor 7 (putative)
|
|
COASY
|
CoA synthase
|
|
COQ10A
|
coenzyme Q10 homolog A (S. cerevisiae)
|
|
COQ10B
|
coenzyme Q10 homolog B (S. cerevisiae)
|
|
COQ2
|
coenzyme Q2 4-hydroxybenzoate polyprenyltransferase
|
|
COQ3
|
coenzyme Q3 methyltransferase
|
|
COQ4
|
coenzyme Q4
|
|
COQ7
|
coenzyme Q7 homolog, ubiquinone (yeast)
|
|
COX1
|
|
|
COX10
|
COX10 heme A:farnesyltransferase cytochrome c oxidase assembly factor
|
|
COX11
|
COX11 cytochrome c oxidase copper chaperone
|
|
COX14
|
COX14 cytochrome c oxidase assembly factor
|
|
COX15
|
cytochrome c oxidase assembly homolog 15 (yeast)
|
|
COX16
|
COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)
|
|
COX17
|
COX17 cytochrome c oxidase copper chaperone
|
|
COX18
|
COX18 cytochrome c oxidase assembly factor
|
|
COX19
|
COX19 cytochrome c oxidase assembly factor
|
|
COX2
|
|
|
COX20
|
COX20 cytochrome c oxidase assembly factor
|
|
COX3
|
|
|
COX4I1
|
cytochrome c oxidase subunit IV isoform 1
|
|
COX4I2
|
cytochrome c oxidase subunit IV isoform 2 (lung)
|
|
COX5A
|
cytochrome c oxidase subunit Va
|
|
COX5B
|
cytochrome c oxidase subunit Vb
|
|
COX6A1
|
cytochrome c oxidase subunit VIa polypeptide 1
|
|
COX6A2
|
cytochrome c oxidase subunit VIa polypeptide 2
|
|
COX6B1
|
cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous)
|
|
COX6B2
|
cytochrome c oxidase subunit VIb polypeptide 2 (testis)
|
|
COX6C
|
cytochrome c oxidase subunit VIc
|
|
COX7A1
|
cytochrome c oxidase subunit VIIa polypeptide 1 (muscle)
|
|
COX7A2
|
cytochrome c oxidase subunit VIIa polypeptide 2 (liver)
|
|
COX7A2L
|
cytochrome c oxidase subunit VIIa polypeptide 2 like
|
|
COX7B
|
cytochrome c oxidase subunit VIIb
|
|
COX7B2
|
cytochrome c oxidase subunit VIIb2
|
|
COX7C
|
cytochrome c oxidase subunit VIIc
|
|
COX8A
|
cytochrome c oxidase subunit VIIIA (ubiquitous)
|
|
COX8C
|
cytochrome c oxidase subunit VIIIC
|
|
CPOX
|
coproporphyrinogen oxidase
|
|
CPS1
|
carbamoyl-phosphate synthase 1, mitochondrial
|
|
CPT1A
|
carnitine palmitoyltransferase 1A (liver)
|
|
CPT1B
|
carnitine palmitoyltransferase 1B (muscle)
|
|
CPT1C
|
carnitine palmitoyltransferase 1C
|
|
CPT2
|
carnitine palmitoyltransferase 2
|
|
CRAT
|
carnitine O-acetyltransferase
|
|
CRLS1
|
cardiolipin synthase 1
|
|
CS
|
citrate synthase
|
|
CSDE1
|
cold shock domain containing E1, RNA-binding
|
|
CYB5A
|
cytochrome b5 type A (microsomal)
|
|
CYB5B
|
cytochrome b5 type B (outer mitochondrial membrane)
|
|
CYB5R3
|
cytochrome b5 reductase 3
|
|
CYC1
|
cytochrome c-1
|
|
CYCS
|
cytochrome c, somatic
|
|
CYP11A1
|
cytochrome P450, family 11, subfamily A, polypeptide 1
|
|
CYP11B1
|
cytochrome P450, family 11, subfamily B, polypeptide 1
|
|
CYP11B2
|
cytochrome P450, family 11, subfamily B, polypeptide 2
|
|
CYP24A1
|
cytochrome P450, family 24, subfamily A, polypeptide 1
|
|
CYP27A1
|
cytochrome P450, family 27, subfamily A, polypeptide 1
|
|
CYP27B1
|
cytochrome P450, family 27, subfamily B, polypeptide 1
|
|
D2HGDH
|
D-2-hydroxyglutarate dehydrogenase
|
|
DAO
|
D-amino-acid oxidase
|
|
DAP3
|
death associated protein 3
|
|
DARS2
|
aspartyl-tRNA synthetase 2, mitochondrial
|
|
DBT
|
dihydrolipoamide branched chain transacylase E2
|
|
DDX28
|
DEAD (Asp-Glu-Ala-Asp) box polypeptide 28
|
|
DDX3X
|
DEAD (Asp-Glu-Ala-Asp) box helicase 3, X-linked
|
|
DECR1
|
2,4-dienoyl CoA reductase 1, mitochondrial
|
|
DGUOK
|
deoxyguanosine kinase
|
|
DHFRL1
|
dihydrofolate reductase-like 1
|
|
DHODH
|
dihydroorotate dehydrogenase (quinone)
|
|
DHRS1
|
dehydrogenase/reductase (SDR family) member 1
|
|
DHRS2
|
dehydrogenase/reductase (SDR family) member 2
|
|
DHX30
|
DEAH (Asp-Glu-Ala-His) box helicase 30
|
|
DIABLO
|
diablo, IAP-binding mitochondrial protein
|
|
DLAT
|
dihydrolipoamide S-acetyltransferase
|
|
DLD
|
dihydrolipoamide dehydrogenase
|
|
DLST
|
dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
|
|
DMGDH
|
dimethylglycine dehydrogenase
|
|
DMPK
|
dystrophia myotonica-protein kinase
|
|
DNA2
|
DNA replication helicase/nuclease 2
|
|
DNAJA3
|
DnaJ (Hsp40) homolog, subfamily A, member 3
|
|
DNAJC11
|
DnaJ (Hsp40) homolog, subfamily C, member 11
|
|
DNAJC15
|
DnaJ (Hsp40) homolog, subfamily C, member 15
|
|
DNAJC19
|
DnaJ (Hsp40) homolog, subfamily C, member 19
|
|
DNM1L
|
dynamin 1-like
|
|
DTYMK
|
deoxythymidylate kinase (thymidylate kinase)
|
|
DUSP21
|
dual specificity phosphatase 21
|
|
EARS2
|
glutamyl-tRNA synthetase 2, mitochondrial
|
|
ECHS1
|
enoyl CoA hydratase, short chain, 1, mitochondrial
|
|
ECI1
|
enoyl-CoA delta isomerase 1
|
|
EFHD1
|
EF-hand domain family, member D1
|
|
EPHA4
|
EPH receptor A4
|
|
ERAL1
|
Era-like 12S mitochondrial rRNA chaperone 1
|
|
ERBB4
|
erb-b2 receptor tyrosine kinase 4
|
|
ETFA
|
electron-transfer-flavoprotein, alpha polypeptide
|
|
ETFB
|
electron-transfer-flavoprotein, beta polypeptide
|
|
ETFDH
|
electron-transferring-flavoprotein dehydrogenase
|
|
ETHE1
|
ethylmalonic encephalopathy 1
|
|
EXOG
|
endo/exonuclease (5'-3'), endonuclease G-like
|
|
FAHD1
|
fumarylacetoacetate hydrolase domain containing 1
|
|
FARS2
|
phenylalanyl-tRNA synthetase 2, mitochondrial
|
|
FBXL4
|
F-box and leucine-rich repeat protein 4
|
|
FDX1
|
ferredoxin 1
|
|
FDX1L
|
ferredoxin 1-like
|
|
FDXR
|
ferredoxin reductase
|
|
FECH
|
ferrochelatase
|
|
FGR
|
FGR proto-oncogene, Src family tyrosine kinase
|
|
FH
|
fumarate hydratase
|
|
FIS1
|
fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae)
|
|
FKBP8
|
FK506 binding protein 8, 38kDa
|
|
FLAD1
|
flavin adenine dinucleotide synthetase 1
|
|
FLVCR1
|
feline leukemia virus subgroup C cellular receptor 1
|
|
FNDC1
|
fibronectin type III domain containing 1
|
|
FPGS
|
folylpolyglutamate synthase
|
|
FUNDC1
|
FUN14 domain containing 1
|
|
FUNDC2
|
FUN14 domain containing 2
|
|
FXN
|
frataxin
|
|
GADD45GIP1
|
growth arrest and DNA-damage-inducible, gamma interacting protein 1
|
|
GARS
|
glycyl-tRNA synthetase
|
|
GATM
|
glycine amidinotransferase (L-arginine:glycine amidinotransferase)
|
|
GCDH
|
glutaryl-CoA dehydrogenase
|
|
GDAP1
|
ganglioside induced differentiation associated protein 1
|
|
GFER
|
growth factor, augmenter of liver regeneration
|
|
GFM1
|
G elongation factor, mitochondrial 1
|
|
GFM2
|
G elongation factor, mitochondrial 2
|
|
GHITM
|
growth hormone inducible transmembrane protein
|
|
GIMAP5
|
GTPase, IMAP family member 5
|
|
GJA1
|
gap junction protein, alpha 1, 43kDa
|
|
GK
|
glycerol kinase
|
|
GK2
|
glycerol kinase 2
|
|
GLS
|
glutaminase
|
|
GLS2
|
glutaminase 2 (liver, mitochondrial)
|
|
GLUD1
|
glutamate dehydrogenase 1
|
|
GLYAT
|
glycine-N-acyltransferase
|
|
GOLPH3
|
golgi phosphoprotein 3 (coat-protein)
|
|
GOT2
|
glutamic-oxaloacetic transaminase 2, mitochondrial
|
|
GPAM
|
glycerol-3-phosphate acyltransferase, mitochondrial
|
|
GPAT2
|
glycerol-3-phosphate acyltransferase 2, mitochondrial
|
|
GPD2
|
glycerol-3-phosphate dehydrogenase 2 (mitochondrial)
|
|
GPER1
|
G protein-coupled estrogen receptor 1
|
|
GPT2
|
glutamic pyruvate transaminase (alanine aminotransferase) 2
|
|
GPX1
|
glutathione peroxidase 1
|
|
GRAMD4
|
GRAM domain containing 4
|
|
GRPEL1
|
GrpE-like 1, mitochondrial (E. coli)
|
|
GRPEL2
|
GrpE-like 2, mitochondrial (E. coli)
|
|
GRSF1
|
G-rich RNA sequence binding factor 1
|
|
GSR
|
glutathione reductase
|
|
GSTK1
|
glutathione S-transferase kappa 1
|
|
GUF1
|
GUF1 GTPase homolog (S. cerevisiae)
|
|
HAAO
|
3-hydroxyanthranilate 3,4-dioxygenase
|
|
HADH
|
hydroxyacyl-CoA dehydrogenase
|
|
HADHA
|
hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit
|
|
HADHB
|
hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit
|
|
HAGH
|
hydroxyacylglutathione hydrolase
|
|
HARS2
|
histidyl-tRNA synthetase 2, mitochondrial
|
|
HCCS
|
holocytochrome c synthase
|
|
HERC2
|
HECT and RLD domain containing E3 ubiquitin protein ligase 2
|
|
HIBADH
|
3-hydroxyisobutyrate dehydrogenase
|
|
HIBCH
|
3-hydroxyisobutyryl-CoA hydrolase
|
|
HIGD1A
|
HIG1 hypoxia inducible domain family, member 1A
|
|
HIGD2A
|
HIG1 hypoxia inducible domain family, member 2A
|
|
HK1
|
hexokinase 1
|
|
HK2
|
hexokinase 2
|
|
HMGCL
|
3-hydroxymethyl-3-methylglutaryl-CoA lyase
|
|
HMGCS2
|
3-hydroxy-3-methylglutaryl-CoA synthase 2 (mitochondrial)
|
|
HSD17B10
|
hydroxysteroid (17-beta) dehydrogenase 10
|
|
HSD17B8
|
hydroxysteroid (17-beta) dehydrogenase 8
|
|
HSD3B1
|
hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 1
|
|
HSD3B2
|
hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 2
|
|
HSPA1L
|
heat shock 70kDa protein 1-like
|
|
HSPA9
|
heat shock 70kDa protein 9 (mortalin)
|
|
HSPD1
|
heat shock 60kDa protein 1 (chaperonin)
|
|
HSPE1
|
heat shock 10kDa protein 1
|
|
HTRA2
|
HtrA serine peptidase 2
|
|
IARS2
|
isoleucyl-tRNA synthetase 2, mitochondrial
|
|
IBA57
|
IBA57, iron-sulfur cluster assembly homolog (S. cerevisiae)
|
|
ICT1
|
immature colon carcinoma transcript 1
|
|
IDH2
|
isocitrate dehydrogenase 2 (NADP+), mitochondrial
|
|
IDH3A
|
isocitrate dehydrogenase 3 (NAD+) alpha
|
|
IDH3B
|
isocitrate dehydrogenase 3 (NAD+) beta
|
|
IDH3G
|
isocitrate dehydrogenase 3 (NAD+) gamma
|
|
IFI27
|
interferon, alpha-inducible protein 27
|
|
IKBKE
|
inhibitor of kappa light polypeptide gene enhancer in B-cells, kinase epsilon
|
|
IMMP1L
|
IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae)
|
|
IMMP2L
|
IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae)
|
|
IMMT
|
inner membrane protein, mitochondrial
|
|
ISCU
|
iron-sulfur cluster assembly enzyme
|
|
IVD
|
isovaleryl-CoA dehydrogenase
|
|
KARS
|
lysyl-tRNA synthetase
|
|
KMO
|
kynurenine 3-monooxygenase (kynurenine 3-hydroxylase)
|
|
L2HGDH
|
L-2-hydroxyglutarate dehydrogenase
|
|
LARS2
|
leucyl-tRNA synthetase 2, mitochondrial
|
|
LDHD
|
lactate dehydrogenase D
|
|
LETM1
|
leucine zipper-EF-hand containing transmembrane protein 1
|
|
LETM2
|
leucine zipper-EF-hand containing transmembrane protein 2
|
|
LETMD1
|
LETM1 domain containing 1
|
|
LGALS3
|
lectin, galactoside-binding, soluble, 3
|
|
LONP1
|
lon peptidase 1, mitochondrial
|
|
LPIN1
|
lipin 1
|
|
LRPPRC
|
leucine-rich pentatricopeptide repeat containing
|
|
LRRC59
|
leucine rich repeat containing 59
|
|
LRRK2
|
leucine-rich repeat kinase 2
|
|
LYN
|
LYN proto-oncogene, Src family tyrosine kinase
|
|
LYRM4
|
LYR motif containing 4
|
|
LYRM7
|
LYR motif containing 7
|
|
MALSU1
|
mitochondrial assembly of ribosomal large subunit 1
|
|
MAOA
|
monoamine oxidase A
|
|
MAOB
|
monoamine oxidase B
|
|
MAPK8IP1
|
mitogen-activated protein kinase 8 interacting protein 1
|
|
MARC1
|
mitochondrial amidoxime reducing component 1
|
|
MARC2
|
mitochondrial amidoxime reducing component 2
|
|
MARCH5
|
membrane-associated ring finger (C3HC4) 5
|
|
MARS2
|
methionyl-tRNA synthetase 2, mitochondrial
|
|
MAVS
|
mitochondrial antiviral signaling protein
|
|
MCCC1
|
methylcrotonoyl-CoA carboxylase 1 (alpha)
|
|
MCCC2
|
methylcrotonoyl-CoA carboxylase 2 (beta)
|
|
MCEE
|
methylmalonyl CoA epimerase
|
|
MCL1
|
myeloid cell leukemia 1
|
|
MCU
|
mitochondrial calcium uniporter
|
|
MCUR1
|
mitochondrial calcium uniporter regulator 1
|
|
MDH2
|
malate dehydrogenase 2, NAD (mitochondrial)
|
|
ME2
|
malic enzyme 2, NAD(+)-dependent, mitochondrial
|
|
ME3
|
malic enzyme 3, NADP(+)-dependent, mitochondrial
|
|
METTL20
|
methyltransferase like 20
|
|
MFF
|
mitochondrial fission factor
|
|
MFN1
|
mitofusin 1
|
|
MFN2
|
mitofusin 2
|
|
MGARP
|
mitochondria-localized glutamic acid-rich protein
|
|
MGST1
|
microsomal glutathione S-transferase 1
|
|
MICU1
|
mitochondrial calcium uptake 1
|
|
MICU2
|
mitochondrial calcium uptake 2
|
|
MIEF1
|
mitochondrial elongation factor 1
|
|
MIEF2
|
mitochondrial elongation factor 2
|
|
MINOS1
|
mitochondrial inner membrane organizing system 1
|
|
MIPEP
|
mitochondrial intermediate peptidase
|
|
MLXIP
|
MLX interacting protein
|
|
MLYCD
|
malonyl-CoA decarboxylase
|
|
MMAA
|
methylmalonic aciduria (cobalamin deficiency) cblA type
|
|
MMAB
|
methylmalonic aciduria (cobalamin deficiency) cblB type
|
|
MOAP1
|
modulator of apoptosis 1
|
|
MPC1
|
mitochondrial pyruvate carrier 1
|
|
MPC1L
|
mitochondrial pyruvate carrier 1-like
|
|
MPC2
|
mitochondrial pyruvate carrier 2
|
|
MPG
|
N-methylpurine-DNA glycosylase
|
|
MPST
|
mercaptopyruvate sulfurtransferase
|
|
MPV17
|
MpV17 mitochondrial inner membrane protein
|
|
MPV17L2
|
MPV17 mitochondrial membrane protein-like 2
|
|
MRPL1
|
mitochondrial ribosomal protein L1
|
|
MRPL10
|
mitochondrial ribosomal protein L10
|
|
MRPL11
|
mitochondrial ribosomal protein L11
|
|
MRPL12
|
mitochondrial ribosomal protein L12
|
|
MRPL13
|
mitochondrial ribosomal protein L13
|
|
MRPL14
|
mitochondrial ribosomal protein L14
|
|
MRPL15
|
mitochondrial ribosomal protein L15
|
|
MRPL16
|
mitochondrial ribosomal protein L16
|
|
MRPL17
|
mitochondrial ribosomal protein L17
|
|
MRPL18
|
mitochondrial ribosomal protein L18
|
|
MRPL19
|
mitochondrial ribosomal protein L19
|
|
MRPL2
|
mitochondrial ribosomal protein L2
|
|
MRPL20
|
mitochondrial ribosomal protein L20
|
|
MRPL21
|
mitochondrial ribosomal protein L21
|
|
MRPL22
|
mitochondrial ribosomal protein L22
|
|
MRPL23
|
mitochondrial ribosomal protein L23
|
|
MRPL24
|
mitochondrial ribosomal protein L24
|
|
MRPL27
|
mitochondrial ribosomal protein L27
|
|
MRPL28
|
mitochondrial ribosomal protein L28
|
|
MRPL3
|
mitochondrial ribosomal protein L3
|
|
MRPL30
|
mitochondrial ribosomal protein L30
|
|
MRPL32
|
mitochondrial ribosomal protein L32
|
|
MRPL33
|
mitochondrial ribosomal protein L33
|
|
MRPL34
|
mitochondrial ribosomal protein L34
|
|
MRPL35
|
mitochondrial ribosomal protein L35
|
|
MRPL36
|
mitochondrial ribosomal protein L36
|
|
MRPL37
|
mitochondrial ribosomal protein L37
|
|
MRPL38
|
mitochondrial ribosomal protein L38
|
|
MRPL39
|
mitochondrial ribosomal protein L39
|
|
MRPL4
|
mitochondrial ribosomal protein L4
|
|
MRPL40
|
mitochondrial ribosomal protein L40
|
|
MRPL41
|
mitochondrial ribosomal protein L41
|
|
MRPL42
|
mitochondrial ribosomal protein L42
|
|
MRPL43
|
mitochondrial ribosomal protein L43
|
|
MRPL44
|
mitochondrial ribosomal protein L44
|
|
MRPL46
|
mitochondrial ribosomal protein L46
|
|
MRPL47
|
mitochondrial ribosomal protein L47
|
|
MRPL48
|
mitochondrial ribosomal protein L48
|
|
MRPL49
|
mitochondrial ribosomal protein L49
|
|
MRPL50
|
mitochondrial ribosomal protein L50
|
|
MRPL51
|
mitochondrial ribosomal protein L51
|
|
MRPL52
|
mitochondrial ribosomal protein L52
|
|
MRPL53
|
mitochondrial ribosomal protein L53
|
|
MRPL54
|
mitochondrial ribosomal protein L54
|
|
MRPL55
|
mitochondrial ribosomal protein L55
|
|
MRPL57
|
mitochondrial ribosomal protein L57
|
|
MRPL9
|
mitochondrial ribosomal protein L9
|
|
MRPS10
|
mitochondrial ribosomal protein S10
|
|
MRPS11
|
mitochondrial ribosomal protein S11
|
|
MRPS12
|
mitochondrial ribosomal protein S12
|
|
MRPS14
|
mitochondrial ribosomal protein S14
|
|
MRPS15
|
mitochondrial ribosomal protein S15
|
|
MRPS16
|
mitochondrial ribosomal protein S16
|
|
MRPS17
|
mitochondrial ribosomal protein S17
|
|
MRPS18A
|
mitochondrial ribosomal protein S18A
|
|
MRPS18B
|
mitochondrial ribosomal protein S18B
|
|
MRPS18C
|
mitochondrial ribosomal protein S18C
|
|
MRPS2
|
mitochondrial ribosomal protein S2
|
|
MRPS21
|
mitochondrial ribosomal protein S21
|
|
MRPS22
|
mitochondrial ribosomal protein S22
|
|
MRPS23
|
mitochondrial ribosomal protein S23
|
|
MRPS24
|
mitochondrial ribosomal protein S24
|
|
MRPS25
|
mitochondrial ribosomal protein S25
|
|
MRPS26
|
mitochondrial ribosomal protein S26
|
|
MRPS27
|
mitochondrial ribosomal protein S27
|
|
MRPS28
|
mitochondrial ribosomal protein S28
|
|
MRPS30
|
mitochondrial ribosomal protein S30
|
|
MRPS31
|
mitochondrial ribosomal protein S31
|
|
MRPS33
|
mitochondrial ribosomal protein S33
|
|
MRPS34
|
mitochondrial ribosomal protein S34
|
|
MRPS35
|
mitochondrial ribosomal protein S35
|
|
MRPS36
|
mitochondrial ribosomal protein S36
|
|
MRPS5
|
mitochondrial ribosomal protein S5
|
|
MRPS6
|
mitochondrial ribosomal protein S6
|
|
MRPS7
|
mitochondrial ribosomal protein S7
|
|
MRPS9
|
mitochondrial ribosomal protein S9
|
|
MRRF
|
mitochondrial ribosome recycling factor
|
|
MRS2
|
MRS2 magnesium transporter
|
|
MSTO1
|
misato 1, mitochondrial distribution and morphology regulator
|
|
MT-ATP6
|
ATP synthase F0 subunit 6
|
|
MT-ATP8
|
ATP synthase F0 subunit 8
|
|
MT-CYB
|
cytochrome b
|
|
MT-ND2
|
MTND2
|
|
MT-ND3
|
NADH dehydrogenase, subunit 3 (complex I)
|
|
MT-ND4
|
NADH dehydrogenase, subunit 4 (complex I)
|
|
MT-ND4L
|
NADH dehydrogenase, subunit 4L (complex I)
|
|
MT-ND5
|
NADH dehydrogenase, subunit 5 (complex I)
|
|
MT-ND6
|
NADH dehydrogenase, subunit 6 (complex I)
|
|
MTCH1
|
mitochondrial carrier 1
|
|
MTCH2
|
mitochondrial carrier 2
|
|
MTERF1
|
mitochondrial transcription termination factor 1
|
|
MTERF2
|
mitochondrial transcription termination factor 2
|
|
MTERF4
|
mitochondrial transcription termination factor 4
|
|
MTFP1
|
mitochondrial fission process 1
|
|
MTG1
|
mitochondrial ribosome-associated GTPase 1
|
|
MTG2
|
mitochondrial ribosome-associated GTPase 2
|
|
MTHFD2L
|
methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2-like
|
|
MTOR
|
mechanistic target of rapamycin (serine/threonine kinase)
|
|
MTRF1L
|
mitochondrial translational release factor 1-like
|
|
MTX1
|
metaxin 1
|
|
MTX2
|
metaxin 2
|
|
MTX3
|
metaxin 3
|
|
MUL1
|
mitochondrial E3 ubiquitin protein ligase 1
|
|
MUT
|
methylmalonyl CoA mutase
|
|
MYO19
|
myosin XIX
|
|
MYOC
|
myocilin, trabecular meshwork inducible glucocorticoid response
|
|
NAGS
|
N-acetylglutamate synthase
|
|
NARS2
|
asparaginyl-tRNA synthetase 2, mitochondrial (putative)
|
|
NAT8L
|
N-acetyltransferase 8-like (GCN5-related, putative)
|
|
ND1
|
|
|
NDUFA1
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
|
|
NDUFA10
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
|
|
NDUFA11
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa
|
|
NDUFA12
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12
|
|
NDUFA13
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
|
|
NDUFA2
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
|
|
NDUFA3
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa
|
|
NDUFA4
|
NDUFA4, mitochondrial complex associated
|
|
NDUFA5
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5
|
|
NDUFA6
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa
|
|
NDUFA7
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDa
|
|
NDUFA8
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
|
|
NDUFA9
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
|
|
NDUFAB1
|
NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
|
|
NDUFAF1
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 1
|
|
NDUFAF3
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 3
|
|
NDUFAF4
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 4
|
|
NDUFAF5
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 5
|
|
NDUFAF6
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 6
|
|
NDUFB1
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa
|
|
NDUFB10
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa
|
|
NDUFB11
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa
|
|
NDUFB2
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa
|
|
NDUFB3
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa
|
|
NDUFB4
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa
|
|
NDUFB5
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa
|
|
NDUFB6
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa
|
|
NDUFB7
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa
|
|
NDUFB8
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa
|
|
NDUFB9
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa
|
|
NDUFC1
|
NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa
|
|
NDUFC2
|
NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa
|
|
NDUFC2-KCTD14
|
NDUFC2-KCTD14 readthrough
|
|
NDUFS1
|
NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
|
|
NDUFS2
|
NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
|
|
NDUFS3
|
NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
|
|
NDUFS4
|
NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
|
|
NDUFS5
|
NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)
|
|
NDUFS6
|
NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)
|
|
NDUFS7
|
NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
|
|
NDUFS8
|
NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
|
|
NDUFV1
|
NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa
|
|
NDUFV2
|
NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa
|
|
NDUFV3
|
NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa
|
|
NFS1
|
NFS1 cysteine desulfurase
|
|
NIPSNAP1
|
nipsnap homolog 1 (C. elegans)
|
|
NLN
|
neurolysin (metallopeptidase M3 family)
|
|
NLRX1
|
NLR family member X1
|
|
NME4
|
NME/NM23 nucleoside diphosphate kinase 4
|
|
NNT
|
nicotinamide nucleotide transhydrogenase
|
|
NOA1
|
nitric oxide associated 1
|
|
NR3C1
|
nuclear receptor subfamily 3, group C, member 1 (glucocorticoid receptor)
|
|
NSUN4
|
NOP2/Sun domain family, member 4
|
|
NT5M
|
5',3'-nucleotidase, mitochondrial
|
|
NUDT1
|
nudix (nucleoside diphosphate linked moiety X)-type motif 1
|
|
NUDT9
|
nudix (nucleoside diphosphate linked moiety X)-type motif 9
|
|
OAT
|
ornithine aminotransferase
|
|
OCIAD2
|
OCIA domain containing 2
|
|
OGDH
|
oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
|
|
OGDHL
|
oxoglutarate dehydrogenase-like
|
|
OMA1
|
OMA1 zinc metallopeptidase
|
|
OPA1
|
optic atrophy 1 (autosomal dominant)
|
|
OTC
|
ornithine carbamoyltransferase
|
|
OXA1L
|
oxidase (cytochrome c) assembly 1-like
|
|
OXCT1
|
3-oxoacid CoA transferase 1
|
|
PABPC5
|
poly(A) binding protein, cytoplasmic 5
|
|
PAM16
|
presequence translocase-associated motor 16 homolog (S. cerevisiae)
|
|
PANK2
|
pantothenate kinase 2
|
|
PARG
|
poly (ADP-ribose) glycohydrolase
|
|
PARK7
|
parkinson protein 7
|
|
PARL
|
presenilin associated, rhomboid-like
|
|
PARS2
|
prolyl-tRNA synthetase 2, mitochondrial (putative)
|
|
PC
|
pyruvate carboxylase
|
|
PCCA
|
propionyl CoA carboxylase, alpha polypeptide
|
|
PCCB
|
propionyl CoA carboxylase, beta polypeptide
|
|
PCK2
|
phosphoenolpyruvate carboxykinase 2 (mitochondrial)
|
|
PDE12
|
phosphodiesterase 12
|
|
PDE2A
|
phosphodiesterase 2A, cGMP-stimulated
|
|
PDHA1
|
pyruvate dehydrogenase (lipoamide) alpha 1
|
|
PDHA2
|
pyruvate dehydrogenase (lipoamide) alpha 2
|
|
PDHB
|
pyruvate dehydrogenase (lipoamide) beta
|
|
PDHX
|
pyruvate dehydrogenase complex, component X
|
|
PDK1
|
pyruvate dehydrogenase kinase, isozyme 1
|
|
PDK2
|
pyruvate dehydrogenase kinase, isozyme 2
|
|
PDK3
|
pyruvate dehydrogenase kinase, isozyme 3
|
|
PDK4
|
pyruvate dehydrogenase kinase, isozyme 4
|
|
PDP1
|
pyruvate dehyrogenase phosphatase catalytic subunit 1
|
|
PDP2
|
pyruvate dehyrogenase phosphatase catalytic subunit 2
|
|
PDPR
|
pyruvate dehydrogenase phosphatase regulatory subunit
|
|
PDSS1
|
prenyl (decaprenyl) diphosphate synthase, subunit 1
|
|
PDSS2
|
prenyl (decaprenyl) diphosphate synthase, subunit 2
|
|
PEMT
|
phosphatidylethanolamine N-methyltransferase
|
|
PGAM5
|
phosphoglycerate mutase family member 5
|
|
PGR
|
progesterone receptor
|
|
PGS1
|
phosphatidylglycerophosphate synthase 1
|
|
PHB
|
prohibitin
|
|
PHB2
|
prohibitin 2
|
|
PI4KB
|
phosphatidylinositol 4-kinase, catalytic, beta
|
|
PIN4
|
peptidylprolyl cis/trans isomerase, NIMA-interacting 4
|
|
PINK1
|
PTEN induced putative kinase 1
|
|
PITRM1
|
pitrilysin metallopeptidase 1
|
|
PLA2G4A
|
phospholipase A2, group IVA (cytosolic, calcium-dependent)
|
|
PLD6
|
phospholipase D family, member 6
|
|
PLN
|
phospholamban
|
|
PLSCR3
|
phospholipid scramblase 3
|
|
PMAIP1
|
phorbol-12-myristate-13-acetate-induced protein 1
|
|
PMPCA
|
peptidase (mitochondrial processing) alpha
|
|
PMPCB
|
peptidase (mitochondrial processing) beta
|
|
PNPLA7
|
patatin-like phospholipase domain containing 7
|
|
PNPT1
|
polyribonucleotide nucleotidyltransferase 1
|
|
POLDIP2
|
polymerase (DNA-directed), delta interacting protein 2
|
|
POLG
|
polymerase (DNA directed), gamma
|
|
POLG2
|
polymerase (DNA directed), gamma 2, accessory subunit
|
|
POLRMT
|
polymerase (RNA) mitochondrial (DNA directed)
|
|
POP7
|
processing of precursor 7, ribonuclease P/MRP subunit (S. cerevisiae)
|
|
PPA2
|
pyrophosphatase (inorganic) 2
|
|
PPIF
|
peptidylprolyl isomerase F
|
|
PPM1K
|
protein phosphatase, Mg2+/Mn2+ dependent, 1K
|
|
PPOX
|
protoporphyrinogen oxidase
|
|
PPP1R15A
|
protein phosphatase 1, regulatory subunit 15A
|
|
PPP2R2B
|
protein phosphatase 2, regulatory subunit B, beta
|
|
PRDX1
|
peroxiredoxin 1
|
|
PRDX3
|
peroxiredoxin 3
|
|
PRDX5
|
peroxiredoxin 5
|
|
PRELID1
|
PRELI domain containing 1
|
|
PRELID2
|
PRELI domain containing 2
|
|
PRIMPOL
|
primase and polymerase (DNA-directed)
|
|
PRKCA
|
protein kinase C, alpha
|
|
PRODH
|
proline dehydrogenase (oxidase) 1
|
|
PRODH2
|
proline dehydrogenase (oxidase) 2
|
|
PSEN1
|
presenilin 1
|
|
PSEN2
|
presenilin 2
|
|
PTCD1
|
pentatricopeptide repeat domain 1
|
|
PTCD3
|
pentatricopeptide repeat domain 3
|
|
PTPMT1
|
protein tyrosine phosphatase, mitochondrial 1
|
|
PYCR1
|
pyrroline-5-carboxylate reductase 1
|
|
QARS
|
glutaminyl-tRNA synthetase
|
|
RAB11FIP5
|
RAB11 family interacting protein 5 (class I)
|
|
RAD51
|
RAD51 recombinase
|
|
RAF1
|
Raf-1 proto-oncogene, serine/threonine kinase
|
|
RARS2
|
arginyl-tRNA synthetase 2, mitochondrial
|
|
RDH13
|
retinol dehydrogenase 13 (all-trans/9-cis)
|
|
REEP1
|
receptor accessory protein 1
|
|
REXO2
|
RNA exonuclease 2
|
|
RHOT1
|
ras homolog family member T1
|
|
RHOT2
|
ras homolog family member T2
|
|
RMDN3
|
regulator of microtubule dynamics 3
|
|
RNF144B
|
ring finger protein 144B
|
|
RNF185
|
ring finger protein 185
|
|
RNF5
|
ring finger protein 5, E3 ubiquitin protein ligase
|
|
ROMO1
|
reactive oxygen species modulator 1
|
|
RPS3
|
ribosomal protein S3
|
|
RPS6KB1
|
ribosomal protein S6 kinase, 70kDa, polypeptide 1
|
|
RSAD2
|
radical S-adenosyl methionine domain containing 2
|
|
SAMM50
|
SAMM50 sorting and assembly machinery component
|
|
SARDH
|
sarcosine dehydrogenase
|
|
SARM1
|
sterile alpha and TIR motif containing 1
|
|
SARS2
|
seryl-tRNA synthetase 2, mitochondrial
|
|
SCO1
|
SCO1 cytochrome c oxidase assembly protein
|
|
SCO2
|
SCO2 cytochrome c oxidase assembly protein
|
|
SDHA
|
succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
|
|
SDHAF1
|
succinate dehydrogenase complex assembly factor 1
|
|
SDHAF2
|
succinate dehydrogenase complex assembly factor 2
|
|
SDHAF3
|
succinate dehydrogenase complex assembly factor 3
|
|
SDHAF4
|
succinate dehydrogenase complex assembly factor 4
|
|
SDHB
|
succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
|
|
SDHC
|
succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa
|
|
SDHD
|
succinate dehydrogenase complex, subunit D, integral membrane protein
|
|
SFXN1
|
sideroflexin 1
|
|
SFXN2
|
sideroflexin 2
|
|
SFXN3
|
sideroflexin 3
|
|
SFXN4
|
sideroflexin 4
|
|
SFXN5
|
sideroflexin 5
|
|
SH3GLB1
|
SH3-domain GRB2-like endophilin B1
|
|
SHC1
|
SHC (Src homology 2 domain containing) transforming protein 1
|
|
SHMT2
|
serine hydroxymethyltransferase 2 (mitochondrial)
|
|
SIRT3
|
sirtuin 3
|
|
SIRT4
|
sirtuin 4
|
|
SIRT5
|
sirtuin 5
|
|
SLC11A2
|
solute carrier family 11 (proton-coupled divalent metal ion transporter), member 2
|
|
SLC25A1
|
solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1
|
|
SLC25A10
|
solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10
|
|
SLC25A11
|
solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11
|
|
SLC25A12
|
solute carrier family 25 (aspartate/glutamate carrier), member 12
|
|
SLC25A13
|
solute carrier family 25 (aspartate/glutamate carrier), member 13
|
|
SLC25A14
|
solute carrier family 25 (mitochondrial carrier, brain), member 14
|
|
SLC25A15
|
solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15
|
|
SLC25A16
|
solute carrier family 25 (mitochondrial carrier), member 16
|
|
SLC25A18
|
solute carrier family 25 (glutamate carrier), member 18
|
|
SLC25A19
|
solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19
|
|
SLC25A2
|
solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 2
|
|
SLC25A20
|
solute carrier family 25 (carnitine/acylcarnitine translocase), member 20
|
|
SLC25A21
|
solute carrier family 25 (mitochondrial oxoadipate carrier), member 21
|
|
SLC25A22
|
solute carrier family 25 (mitochondrial carrier: glutamate), member 22
|
|
SLC25A23
|
solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 23
|
|
SLC25A24
|
solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 24
|
|
SLC25A25
|
solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 25
|
|
SLC25A26
|
solute carrier family 25 (S-adenosylmethionine carrier), member 26
|
|
SLC25A27
|
solute carrier family 25, member 27
|
|
SLC25A28
|
solute carrier family 25 (mitochondrial iron transporter), member 28
|
|
SLC25A29
|
solute carrier family 25 (mitochondrial carnitine/acylcarnitine carrier), member 29
|
|
SLC25A3
|
solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3
|
|
SLC25A30
|
solute carrier family 25, member 30
|
|
SLC25A31
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 31
|
|
SLC25A32
|
solute carrier family 25 (mitochondrial folate carrier), member 32
|
|
SLC25A33
|
solute carrier family 25 (pyrimidine nucleotide carrier), member 33
|
|
SLC25A34
|
solute carrier family 25, member 34
|
|
SLC25A35
|
solute carrier family 25, member 35
|
|
SLC25A36
|
solute carrier family 25 (pyrimidine nucleotide carrier), member 36
|
|
SLC25A37
|
solute carrier family 25 (mitochondrial iron transporter), member 37
|
|
SLC25A38
|
solute carrier family 25, member 38
|
|
SLC25A39
|
solute carrier family 25, member 39
|
|
SLC25A4
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
|
|
SLC25A40
|
solute carrier family 25, member 40
|
|
SLC25A41
|
solute carrier family 25, member 41
|
|
SLC25A42
|
solute carrier family 25, member 42
|
|
SLC25A43
|
solute carrier family 25, member 43
|
|
SLC25A44
|
solute carrier family 25, member 44
|
|
SLC25A45
|
solute carrier family 25, member 45
|
|
SLC25A46
|
solute carrier family 25, member 46
|
|
SLC25A47
|
solute carrier family 25, member 47
|
|
SLC25A48
|
solute carrier family 25, member 48
|
|
SLC25A5
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5
|
|
SLC25A51
|
solute carrier family 25, member 51
|
|
SLC25A52
|
solute carrier family 25, member 52
|
|
SLC25A53
|
solute carrier family 25, member 53
|
|
SLC25A6
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 6
|
|
SLC27A3
|
solute carrier family 27 (fatty acid transporter), member 3
|
|
SLC3A1
|
solute carrier family 3 (amino acid transporter heavy chain), member 1
|
|
SLC44A1
|
solute carrier family 44 (choline transporter), member 1
|
|
SLC8B1
|
solute carrier family 8 (sodium/lithium/calcium exchanger), member B1
|
|
SLC9B2
|
solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2
|
|
SLMO1
|
slowmo homolog 1 (Drosophila)
|
|
SLMO2
|
slowmo homolog 2 (Drosophila)
|
|
SMCP
|
sperm mitochondria-associated cysteine-rich protein
|
|
SMDT1
|
single-pass membrane protein with aspartate-rich tail 1
|
|
SNCA
|
synuclein, alpha (non A4 component of amyloid precursor)
|
|
SNN
|
stannin
|
|
SNPH
|
syntaphilin
|
|
SOD1
|
superoxide dismutase 1, soluble
|
|
SOD2
|
superoxide dismutase 2, mitochondrial
|
|
SORD
|
sorbitol dehydrogenase
|
|
SOX10
|
SRY (sex determining region Y)-box 10
|
|
SPATA18
|
spermatogenesis associated 18
|
|
SPATA19
|
spermatogenesis associated 19
|
|
SPG20
|
spastic paraplegia 20 (Troyer syndrome)
|
|
SPG7
|
spastic paraplegia 7 (pure and complicated autosomal recessive)
|
|
SPNS1
|
spinster homolog 1 (Drosophila)
|
|
SQRDL
|
sulfide quinone reductase-like (yeast)
|
|
SRC
|
SRC proto-oncogene, non-receptor tyrosine kinase
|
|
SSBP1
|
single-stranded DNA binding protein 1, mitochondrial
|
|
ST20
|
suppressor of tumorigenicity 20
|
|
STAR
|
steroidogenic acute regulatory protein
|
|
STARD13
|
StAR-related lipid transfer (START) domain containing 13
|
|
STAT3
|
signal transducer and activator of transcription 3 (acute-phase response factor)
|
|
STOML2
|
stomatin (EPB72)-like 2
|
|
STX17
|
syntaxin 17
|
|
SUCLA2
|
succinate-CoA ligase, ADP-forming, beta subunit
|
|
SUCLG1
|
succinate-CoA ligase, alpha subunit
|
|
SUCLG2
|
succinate-CoA ligase, GDP-forming, beta subunit
|
|
SUOX
|
sulfite oxidase
|
|
SUPV3L1
|
suppressor of var1, 3-like 1 (S. cerevisiae)
|
|
SURF1
|
surfeit 1
|
|
SYNJ2BP
|
synaptojanin 2 binding protein
|
|
TAMM41
|
TAM41, mitochondrial translocator assembly and maintenance protein, homolog (S. cerevisiae)
|
|
TARS2
|
threonyl-tRNA synthetase 2, mitochondrial (putative)
|
|
TAZ
|
tafazzin
|
|
TDRD7
|
tudor domain containing 7
|
|
TEFM
|
transcription elongation factor, mitochondrial
|
|
TERT
|
telomerase reverse transcriptase
|
|
TFAM
|
transcription factor A, mitochondrial
|
|
TFB1M
|
transcription factor B1, mitochondrial
|
|
TFB2M
|
transcription factor B2, mitochondrial
|
|
THEM4
|
thioesterase superfamily member 4
|
|
THEM5
|
thioesterase superfamily member 5
|
|
TIMM10
|
translocase of inner mitochondrial membrane 10 homolog (yeast)
|
|
TIMM10B
|
translocase of inner mitochondrial membrane 10 homolog B (yeast)
|
|
TIMM13
|
translocase of inner mitochondrial membrane 13 homolog (yeast)
|
|
TIMM17A
|
translocase of inner mitochondrial membrane 17 homolog A (yeast)
|
|
TIMM17B
|
translocase of inner mitochondrial membrane 17 homolog B (yeast)
|
|
TIMM21
|
translocase of inner mitochondrial membrane 21 homolog (yeast)
|
|
TIMM22
|
translocase of inner mitochondrial membrane 22 homolog (yeast)
|
|
TIMM23
|
translocase of inner mitochondrial membrane 23 homolog (yeast)
|
|
TIMM44
|
translocase of inner mitochondrial membrane 44 homolog (yeast)
|
|
TIMM50
|
translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae)
|
|
TIMM8A
|
translocase of inner mitochondrial membrane 8 homolog A (yeast)
|
|
TIMM8B
|
translocase of inner mitochondrial membrane 8 homolog B (yeast)
|
|
TIMM9
|
translocase of inner mitochondrial membrane 9 homolog (yeast)
|
|
TIMMDC1
|
translocase of inner mitochondrial membrane domain containing 1
|
|
TK2
|
thymidine kinase 2, mitochondrial
|
|
TMEM11
|
transmembrane protein 11
|
|
TMEM126A
|
transmembrane protein 126A
|
|
TMEM126B
|
transmembrane protein 126B
|
|
TMEM14C
|
transmembrane protein 14C
|
|
TMEM173
|
transmembrane protein 173
|
|
TMEM70
|
transmembrane protein 70
|
|
TMLHE
|
trimethyllysine hydroxylase, epsilon
|
|
TOMM20
|
translocase of outer mitochondrial membrane 20 homolog (yeast)
|
|
TOMM20L
|
translocase of outer mitochondrial membrane 20 homolog (yeast)-like
|
|
TOMM22
|
translocase of outer mitochondrial membrane 22 homolog (yeast)
|
|
TOMM34
|
translocase of outer mitochondrial membrane 34
|
|
TOMM40
|
translocase of outer mitochondrial membrane 40 homolog (yeast)
|
|
TOMM40L
|
translocase of outer mitochondrial membrane 40 homolog (yeast)-like
|
|
TOMM5
|
translocase of outer mitochondrial membrane 5 homolog (yeast)
|
|
TOMM6
|
translocase of outer mitochondrial membrane 6 homolog (yeast)
|
|
TOMM7
|
translocase of outer mitochondrial membrane 7 homolog (yeast)
|
|
TOMM70A
|
translocase of outer mitochondrial membrane 70 homolog A (S. cerevisiae)
|
|
TOP1MT
|
topoisomerase (DNA) I, mitochondrial
|
|
TP53
|
tumor protein p53
|
|
TRAP1
|
TNF receptor-associated protein 1
|
|
TRIAP1
|
TP53 regulated inhibitor of apoptosis 1
|
|
TRMT10C
|
tRNA methyltransferase 10 homolog C (S. cerevisiae)
|
|
TRMT5
|
tRNA methyltransferase 5
|
|
TSPO
|
translocator protein (18kDa)
|
|
TST
|
thiosulfate sulfurtransferase (rhodanese)
|
|
TTC19
|
tetratricopeptide repeat domain 19
|
|
TUFM
|
Tu translation elongation factor, mitochondrial
|
|
TXN2
|
thioredoxin 2
|
|
TXNIP
|
thioredoxin interacting protein
|
|
TXNRD2
|
thioredoxin reductase 2
|
|
TYMS
|
thymidylate synthetase
|
|
UBIAD1
|
UbiA prenyltransferase domain containing 1
|
|
UCP1
|
uncoupling protein 1 (mitochondrial, proton carrier)
|
|
UCP2
|
uncoupling protein 2 (mitochondrial, proton carrier)
|
|
UCP3
|
uncoupling protein 3 (mitochondrial, proton carrier)
|
|
UQCC1
|
ubiquinol-cytochrome c reductase complex assembly factor 1
|
|
UQCC2
|
ubiquinol-cytochrome c reductase complex assembly factor 2
|
|
UQCC3
|
ubiquinol-cytochrome c reductase complex assembly factor 3
|
|
UQCR10
|
ubiquinol-cytochrome c reductase, complex III subunit X
|
|
UQCR11
|
ubiquinol-cytochrome c reductase, complex III subunit XI
|
|
UQCRB
|
ubiquinol-cytochrome c reductase binding protein
|
|
UQCRC1
|
ubiquinol-cytochrome c reductase core protein I
|
|
UQCRC2
|
ubiquinol-cytochrome c reductase core protein II
|
|
UQCRFS1
|
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
|
|
UQCRH
|
ubiquinol-cytochrome c reductase hinge protein
|
|
UQCRQ
|
ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa
|
|
USMG5
|
up-regulated during skeletal muscle growth 5 homolog (mouse)
|
|
USP30
|
ubiquitin specific peptidase 30
|
|
VAMP1
|
vesicle-associated membrane protein 1 (synaptobrevin 1)
|
|
VAT1
|
vesicle amine transport 1
|
|
VDAC1
|
voltage-dependent anion channel 1
|
|
VDAC2
|
voltage-dependent anion channel 2
|
|
VDAC3
|
voltage-dependent anion channel 3
|
|
VRK2
|
vaccinia related kinase 2
|
|
WARS2
|
tryptophanyl tRNA synthetase 2, mitochondrial
|
|
YARS2
|
tyrosyl-tRNA synthetase 2, mitochondrial
|
|
YME1L1
|
YME1-like 1 ATPase
|
|
ZFYVE1
|
zinc finger, FYVE domain containing 1
|
