mitochondrial respiratory chain complex assembly Gene Set

Dataset GO Biological Process Annotations 2023
Category structural or functional annotations
Type biological process
Description The aggregation, arrangement and bonding together of a set of components to form a mitochondrial respiratory chain complex. (Gene Ontology, GO_0033108)
External Link http://amigo.geneontology.org/amigo/term/GO_0033108
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Genes

91 genes participating in the mitochondrial respiratory chain complex assembly biological process from the curated GO Biological Process Annotations 2023 dataset.

Symbol Name
ACAD9 acyl-CoA dehydrogenase family, member 9
AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1
APOPT1 apoptogenic 1, mitochondrial
BCS1L BC1 (ubiquinol-cytochrome c reductase) synthesis-like
C12ORF73 chromosome 12 open reading frame 73
C16ORF91 chromosome 16 open reading frame 91
C17ORF89 chromosome 17 open reading frame 89
C7ORF73 chromosome 7 open reading frame 73
CHCHD4 coiled-coil-helix-coiled-coil-helix domain containing 4
CHCHD7 coiled-coil-helix-coiled-coil-helix domain containing 7
COA1 cytochrome c oxidase assembly factor 1 homolog (S. cerevisiae)
COA3 cytochrome c oxidase assembly factor 3
COA5 cytochrome c oxidase assembly factor 5
COX14 COX14 cytochrome c oxidase assembly factor
COX16 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)
COX17 COX17 cytochrome c oxidase copper chaperone
COX18 COX18 cytochrome c oxidase assembly factor
COX19 COX19 cytochrome c oxidase assembly factor
COX20 COX20 cytochrome c oxidase assembly factor
DMAC2 distal membrane arm assembly component 2
ECSIT ECSIT signalling integrator
FASTKD3 FAST kinase domains 3
FOXRED1 FAD-dependent oxidoreductase domain containing 1
LYRM2 LYR motif containing 2
LYRM7 LYR motif containing 7
NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
NDUFA11 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa
NDUFA13 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa
NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5
NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa
NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1
NDUFAF2 NADH dehydrogenase (ubiquinone) complex I, assembly factor 2
NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3
NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4
NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5
NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6
NDUFAF7 NADH dehydrogenase (ubiquinone) complex I, assembly factor 7
NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa
NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa
NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa
NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa
NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa
NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa
NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa
NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa
NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa
NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa
NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa
NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa
NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa
NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)
NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
NUBPL nucleotide binding protein-like
OMA1 OMA1 zinc metallopeptidase
OXA1L oxidase (cytochrome c) assembly 1-like
PET100 PET100 homolog (S. cerevisiae)
PET117 PET117 homolog (S. cerevisiae)
SAMM50 SAMM50 sorting and assembly machinery component
SCO1 SCO1 cytochrome c oxidase assembly protein
SCO2 SCO2 cytochrome c oxidase assembly protein
SDHAF1 succinate dehydrogenase complex assembly factor 1
SDHAF2 succinate dehydrogenase complex assembly factor 2
SDHAF3 succinate dehydrogenase complex assembly factor 3
SDHAF4 succinate dehydrogenase complex assembly factor 4
SLC25A33 solute carrier family 25 (pyrimidine nucleotide carrier), member 33
SMIM20 small integral membrane protein 20
SMIM4 small integral membrane protein 4
SURF1 surfeit 1
TAZ tafazzin
TIMM21 translocase of inner mitochondrial membrane 21 homolog (yeast)
TMEM126A transmembrane protein 126A
TMEM126B transmembrane protein 126B
TMEM186 transmembrane protein 186
TMEM223 transmembrane protein 223
TMEM261 transmembrane protein 261
TTC19 tetratricopeptide repeat domain 19
UQCC1 ubiquinol-cytochrome c reductase complex assembly factor 1
UQCC2 ubiquinol-cytochrome c reductase complex assembly factor 2
UQCC3 ubiquinol-cytochrome c reductase complex assembly factor 3
UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1