| Symbol |
Name |
|
ACAD9
|
acyl-CoA dehydrogenase family, member 9
|
|
AIFM1
|
apoptosis-inducing factor, mitochondrion-associated, 1
|
|
APOPT1
|
apoptogenic 1, mitochondrial
|
|
BCS1L
|
BC1 (ubiquinol-cytochrome c reductase) synthesis-like
|
|
C12ORF73
|
chromosome 12 open reading frame 73
|
|
C16ORF91
|
chromosome 16 open reading frame 91
|
|
C17ORF89
|
chromosome 17 open reading frame 89
|
|
C7ORF73
|
chromosome 7 open reading frame 73
|
|
CHCHD4
|
coiled-coil-helix-coiled-coil-helix domain containing 4
|
|
CHCHD7
|
coiled-coil-helix-coiled-coil-helix domain containing 7
|
|
COA1
|
cytochrome c oxidase assembly factor 1 homolog (S. cerevisiae)
|
|
COA3
|
cytochrome c oxidase assembly factor 3
|
|
COA5
|
cytochrome c oxidase assembly factor 5
|
|
COX14
|
COX14 cytochrome c oxidase assembly factor
|
|
COX16
|
COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)
|
|
COX17
|
COX17 cytochrome c oxidase copper chaperone
|
|
COX18
|
COX18 cytochrome c oxidase assembly factor
|
|
COX19
|
COX19 cytochrome c oxidase assembly factor
|
|
COX20
|
COX20 cytochrome c oxidase assembly factor
|
|
DMAC2
|
distal membrane arm assembly component 2
|
|
ECSIT
|
ECSIT signalling integrator
|
|
FASTKD3
|
FAST kinase domains 3
|
|
FOXRED1
|
FAD-dependent oxidoreductase domain containing 1
|
|
LYRM2
|
LYR motif containing 2
|
|
LYRM7
|
LYR motif containing 7
|
|
NDUFA1
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
|
|
NDUFA10
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
|
|
NDUFA11
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa
|
|
NDUFA13
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
|
|
NDUFA2
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
|
|
NDUFA3
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa
|
|
NDUFA5
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5
|
|
NDUFA6
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa
|
|
NDUFA8
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
|
|
NDUFA9
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
|
|
NDUFAB1
|
NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
|
|
NDUFAF1
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 1
|
|
NDUFAF2
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 2
|
|
NDUFAF3
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 3
|
|
NDUFAF4
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 4
|
|
NDUFAF5
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 5
|
|
NDUFAF6
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 6
|
|
NDUFAF7
|
NADH dehydrogenase (ubiquinone) complex I, assembly factor 7
|
|
NDUFB1
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa
|
|
NDUFB10
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa
|
|
NDUFB11
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa
|
|
NDUFB2
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa
|
|
NDUFB3
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa
|
|
NDUFB4
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa
|
|
NDUFB5
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa
|
|
NDUFB6
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa
|
|
NDUFB7
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa
|
|
NDUFB8
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa
|
|
NDUFB9
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa
|
|
NDUFC1
|
NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa
|
|
NDUFC2
|
NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa
|
|
NDUFS1
|
NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
|
|
NDUFS2
|
NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
|
|
NDUFS3
|
NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
|
|
NDUFS4
|
NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
|
|
NDUFS5
|
NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)
|
|
NDUFS7
|
NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
|
|
NDUFS8
|
NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
|
|
NUBPL
|
nucleotide binding protein-like
|
|
OMA1
|
OMA1 zinc metallopeptidase
|
|
OXA1L
|
oxidase (cytochrome c) assembly 1-like
|
|
PET100
|
PET100 homolog (S. cerevisiae)
|
|
PET117
|
PET117 homolog (S. cerevisiae)
|
|
SAMM50
|
SAMM50 sorting and assembly machinery component
|
|
SCO1
|
SCO1 cytochrome c oxidase assembly protein
|
|
SCO2
|
SCO2 cytochrome c oxidase assembly protein
|
|
SDHAF1
|
succinate dehydrogenase complex assembly factor 1
|
|
SDHAF2
|
succinate dehydrogenase complex assembly factor 2
|
|
SDHAF3
|
succinate dehydrogenase complex assembly factor 3
|
|
SDHAF4
|
succinate dehydrogenase complex assembly factor 4
|
|
SLC25A33
|
solute carrier family 25 (pyrimidine nucleotide carrier), member 33
|
|
SMIM20
|
small integral membrane protein 20
|
|
SMIM4
|
small integral membrane protein 4
|
|
SURF1
|
surfeit 1
|
|
TAZ
|
tafazzin
|
|
TIMM21
|
translocase of inner mitochondrial membrane 21 homolog (yeast)
|
|
TMEM126A
|
transmembrane protein 126A
|
|
TMEM126B
|
transmembrane protein 126B
|
|
TMEM186
|
transmembrane protein 186
|
|
TMEM223
|
transmembrane protein 223
|
|
TMEM261
|
transmembrane protein 261
|
|
TTC19
|
tetratricopeptide repeat domain 19
|
|
UQCC1
|
ubiquinol-cytochrome c reductase complex assembly factor 1
|
|
UQCC2
|
ubiquinol-cytochrome c reductase complex assembly factor 2
|
|
UQCC3
|
ubiquinol-cytochrome c reductase complex assembly factor 3
|
|
UQCRFS1
|
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
|