mitochondrion Gene Set

Dataset LOCATE Curated Protein Localization Annotations
Category proteomics
Type cellular component
Description A semiautonomous, self replicating organelle that occurs in varying numbers, shapes, and sizes in the cytoplasm of virtually all eukaryotic cells. It is notably the site of tissue respiration. (Gene Ontology, GO_0005739)
External Link http://locate.imb.uq.edu.au/searchpages/HumanGO:0005739.shtml
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Genes

726 proteins localized to the mitochondrion cellular component in low- or high-throughput protein localization assays from the LOCATE Curated Protein Localization Annotations dataset.

Symbol Name
AADAT aminoadipate aminotransferase
AASS aminoadipate-semialdehyde synthase
ABAT 4-aminobutyrate aminotransferase
ABCB10 ATP-binding cassette, sub-family B (MDR/TAP), member 10
ABCB6 ATP-binding cassette, sub-family B (MDR/TAP), member 6 (Langereis blood group)
ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7
ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8
ABCC9 ATP-binding cassette, sub-family C (CFTR/MRP), member 9
ABCE1 ATP-binding cassette, sub-family E (OABP), member 1
ABCF2 ATP-binding cassette, sub-family F (GCN20), member 2
ABHD10 abhydrolase domain containing 10
ABHD11 abhydrolase domain containing 11
ABL1 ABL proto-oncogene 1, non-receptor tyrosine kinase
ACAA2 acetyl-CoA acyltransferase 2
ACACB acetyl-CoA carboxylase beta
ACAD8 acyl-CoA dehydrogenase family, member 8
ACAD9 acyl-CoA dehydrogenase family, member 9
ACADM acyl-CoA dehydrogenase, C-4 to C-12 straight chain
ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain
ACADSB acyl-CoA dehydrogenase, short/branched chain
ACADVL acyl-CoA dehydrogenase, very long chain
ACO2 aconitase 2, mitochondrial
ACOT2 acyl-CoA thioesterase 2
ACOT7 acyl-CoA thioesterase 7
ACOT9 acyl-CoA thioesterase 9
ACSBG1 acyl-CoA synthetase bubblegum family member 1
ACSL1 acyl-CoA synthetase long-chain family member 1
ACSL3 acyl-CoA synthetase long-chain family member 3
ACSL4 acyl-CoA synthetase long-chain family member 4
ACSL5 acyl-CoA synthetase long-chain family member 5
ACSL6 acyl-CoA synthetase long-chain family member 6
ACSM1 acyl-CoA synthetase medium-chain family member 1
ACSM2B acyl-CoA synthetase medium-chain family member 2B
ACSM3 acyl-CoA synthetase medium-chain family member 3
ACSM5 acyl-CoA synthetase medium-chain family member 5
ACSS1 acyl-CoA synthetase short-chain family member 1
ADCK3 aarF domain containing kinase 3
AFG3L1P AFG3-like AAA ATPase 1, pseudogene
AFG3L2 AFG3-like AAA ATPase 2
AGK acylglycerol kinase
AGMAT agmatine ureohydrolase (agmatinase)
AGPAT5 1-acylglycerol-3-phosphate O-acyltransferase 5
AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1
AIFM2 apoptosis-inducing factor, mitochondrion-associated, 2
AIFM3 apoptosis-inducing factor, mitochondrion-associated, 3
AK2 adenylate kinase 2
AK3 adenylate kinase 3
AK4 adenylate kinase 4
AKAP1 A kinase (PRKA) anchor protein 1
AKAP10 A kinase (PRKA) anchor protein 10
AKR1A1 aldo-keto reductase family 1, member A1 (aldehyde reductase)
ALAS1 5'-aminolevulinate synthase 1
ALAS2 5'-aminolevulinate synthase 2
ALDH18A1 aldehyde dehydrogenase 18 family, member A1
ALDH1B1 aldehyde dehydrogenase 1 family, member B1
ALDH2 aldehyde dehydrogenase 2 family (mitochondrial)
ALDH4A1 aldehyde dehydrogenase 4 family, member A1
ALDH5A1 aldehyde dehydrogenase 5 family, member A1
ALDH6A1 aldehyde dehydrogenase 6 family, member A1
ALOX15B arachidonate 15-lipoxygenase, type B
AMACR alpha-methylacyl-CoA racemase
AMT aminomethyltransferase
ANXA10 annexin A10
APEX1 APEX nuclease (multifunctional DNA repair enzyme) 1
APEX2 APEX nuclease (apurinic/apyrimidinic endonuclease) 2
ARAF A-Raf proto-oncogene, serine/threonine kinase
ARG2 arginase 2
ARL2BP ADP-ribosylation factor-like 2 binding protein
ARMC4 armadillo repeat containing 4
ASAH2 N-acylsphingosine amidohydrolase (non-lysosomal ceramidase) 2
ASIC3 acid sensing (proton gated) ion channel 3
ASPA aspartoacylase
ASRGL1 asparaginase like 1
ATP1A1 ATPase, Na+/K+ transporting, alpha 1 polypeptide
ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle
ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide
ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1
ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit
ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1
ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9)
ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9)
ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9)
ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E
ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6
ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2
ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G
ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit
ATP5S ATP synthase, H+ transporting, mitochondrial Fo complex, subunit s (factor B)
ATP7B ATPase, Cu++ transporting, beta polypeptide
ATPAF1 ATP synthase mitochondrial F1 complex assembly factor 1
ATPAF2 ATP synthase mitochondrial F1 complex assembly factor 2
ATPIF1 ATPase inhibitory factor 1
AUH AU RNA binding protein/enoyl-CoA hydratase
AZU1 azurocidin 1
BAAT bile acid CoA:amino acid N-acyltransferase
BAD BCL2-associated agonist of cell death
BAX BCL2-associated X protein
BBC3 BCL2 binding component 3
BCAT2 branched chain amino-acid transaminase 2, mitochondrial
BCKDHA branched chain keto acid dehydrogenase E1, alpha polypeptide
BCKDHB branched chain keto acid dehydrogenase E1, beta polypeptide
BCKDK branched chain ketoacid dehydrogenase kinase
BCL2 B-cell CLL/lymphoma 2
BCL2A1 BCL2-related protein A1
BCL2L1 BCL2-like 1
BCL2L10 BCL2-like 10 (apoptosis facilitator)
BCL2L11 BCL2-like 11 (apoptosis facilitator)
BCL2L13 BCL2-like 13 (apoptosis facilitator)
BCL2L14 BCL2-like 14 (apoptosis facilitator)
BCL2L2 BCL2-like 2
BCS1L BC1 (ubiquinol-cytochrome c reductase) synthesis-like
BID BH3 interacting domain death agonist
BIK BCL2-interacting killer (apoptosis-inducing)
BIN3 bridging integrator 3
BLK BLK proto-oncogene, Src family tyrosine kinase
BLOC1S6 biogenesis of lysosomal organelles complex-1, subunit 6, pallidin
BMF Bcl2 modifying factor
BNC1 basonuclin 1
BNIP3 BCL2/adenovirus E1B 19kDa interacting protein 3
BNIP3L BCL2/adenovirus E1B 19kDa interacting protein 3-like
BOK BCL2-related ovarian killer
BRCA1 breast cancer 1, early onset
C10ORF10 chromosome 10 open reading frame 10
C10ORF2 chromosome 10 open reading frame 2
C14ORF159 chromosome 14 open reading frame 159
C14ORF2 chromosome 14 open reading frame 2
C1QBP complement component 1, q subcomponent binding protein
C1QTNF3 C1q and tumor necrosis factor related protein 3
C21ORF2 chromosome 21 open reading frame 2
C21ORF33 chromosome 21 open reading frame 33
C7ORF55-LUC7L2 C7orf55-LUC7L2 readthrough
CA5A carbonic anhydrase VA, mitochondrial
CA5B carbonic anhydrase VB, mitochondrial
CABLES1 Cdk5 and Abl enzyme substrate 1
CAPRIN2 caprin family member 2
CASP2 caspase 2, apoptosis-related cysteine peptidase
CASP3 caspase 3, apoptosis-related cysteine peptidase
CASP4 caspase 4, apoptosis-related cysteine peptidase
CASP8 caspase 8, apoptosis-related cysteine peptidase
CASP9 caspase 9, apoptosis-related cysteine peptidase
CASQ1 calsequestrin 1 (fast-twitch, skeletal muscle)
CAT catalase
CCAR2 cell cycle and apoptosis regulator 2
CCBL1 cysteine conjugate-beta lyase, cytoplasmic
CCDC39 coiled-coil domain containing 39
CCDC90B coiled-coil domain containing 90B
CCHCR1 coiled-coil alpha-helical rod protein 1
CDS1 CDP-diacylglycerol synthase (phosphatidate cytidylyltransferase) 1
CDS2 CDP-diacylglycerol synthase (phosphatidate cytidylyltransferase) 2
CEND1 cell cycle exit and neuronal differentiation 1
CEP89 centrosomal protein 89kDa
CHKB choline kinase beta
CIDEB cell death-inducing DFFA-like effector b
CKB creatine kinase, brain
CKMT1A creatine kinase, mitochondrial 1A
CLN3 ceroid-lipofuscinosis, neuronal 3
CLPP caseinolytic mitochondrial matrix peptidase proteolytic subunit
CLPX caseinolytic mitochondrial matrix peptidase chaperone subunit
COA6 cytochrome c oxidase assembly factor 6
COQ2 coenzyme Q2 4-hydroxybenzoate polyprenyltransferase
COQ4 coenzyme Q4
COQ6 coenzyme Q6 monooxygenase
COQ7 coenzyme Q7 homolog, ubiquinone (yeast)
COX10 COX10 heme A:farnesyltransferase cytochrome c oxidase assembly factor
COX11 COX11 cytochrome c oxidase copper chaperone
COX15 cytochrome c oxidase assembly homolog 15 (yeast)
COX16 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)
COX18 COX18 cytochrome c oxidase assembly factor
COX4I1 cytochrome c oxidase subunit IV isoform 1
COX4I2 cytochrome c oxidase subunit IV isoform 2 (lung)
COX5A cytochrome c oxidase subunit Va
COX6A2 cytochrome c oxidase subunit VIa polypeptide 2
COX6B1P3 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) pseudogene 3
COX6C cytochrome c oxidase subunit VIc
COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver)
COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like
COX7B cytochrome c oxidase subunit VIIb
COX7B2 cytochrome c oxidase subunit VIIb2
COX7C cytochrome c oxidase subunit VIIc
COX8C cytochrome c oxidase subunit VIIIC
CPT1B carnitine palmitoyltransferase 1B (muscle)
CPT1C carnitine palmitoyltransferase 1C
CPT2 carnitine palmitoyltransferase 2
CRAT carnitine O-acetyltransferase
CRY1 cryptochrome circadian clock 1
CS citrate synthase
CTSB cathepsin B
CTSH cathepsin H
CYB561 cytochrome b561
CYB5A cytochrome b5 type A (microsomal)
CYB5B cytochrome b5 type B (outer mitochondrial membrane)
CYB5R3 cytochrome b5 reductase 3
CYC1 cytochrome c-1
CYCS cytochrome c, somatic
CYP11A1 cytochrome P450, family 11, subfamily A, polypeptide 1
CYP11B1 cytochrome P450, family 11, subfamily B, polypeptide 1
CYP11B2 cytochrome P450, family 11, subfamily B, polypeptide 2
CYP24A1 cytochrome P450, family 24, subfamily A, polypeptide 1
CYP27A1 cytochrome P450, family 27, subfamily A, polypeptide 1
CYP27B1 cytochrome P450, family 27, subfamily B, polypeptide 1
DAP3 death associated protein 3
DBI diazepam binding inhibitor (GABA receptor modulator, acyl-CoA binding protein)
DBT dihydrolipoamide branched chain transacylase E2
DCTN6 dynactin 6
DDX28 DEAD (Asp-Glu-Ala-Asp) box polypeptide 28
DECR1 2,4-dienoyl CoA reductase 1, mitochondrial
DGUOK deoxyguanosine kinase
DHODH dihydroorotate dehydrogenase (quinone)
DIABLO diablo, IAP-binding mitochondrial protein
DISC1 disrupted in schizophrenia 1
DLD dihydrolipoamide dehydrogenase
DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
DMGDH dimethylglycine dehydrogenase
DNAJA3 DnaJ (Hsp40) homolog, subfamily A, member 3
DNM1 dynamin 1
DPYSL2 dihydropyrimidinase-like 2
DUT deoxyuridine triphosphatase
DYNC1H1 dynein, cytoplasmic 1, heavy chain 1
ECH1 enoyl CoA hydratase 1, peroxisomal
ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial
ECI1 enoyl-CoA delta isomerase 1
ECI2 enoyl-CoA delta isomerase 2
ECSIT ECSIT signalling integrator
ELN elastin
ELP3 elongator acetyltransferase complex subunit 3
ETF1 eukaryotic translation termination factor 1
ETFA electron-transfer-flavoprotein, alpha polypeptide
ETFB electron-transfer-flavoprotein, beta polypeptide
ETHE1 ethylmalonic encephalopathy 1
ETNPPL ethanolamine-phosphate phospho-lyase
FAHD1 fumarylacetoacetate hydrolase domain containing 1
FAM170A family with sequence similarity 170, member A
FARS2 phenylalanyl-tRNA synthetase 2, mitochondrial
FASTK Fas-activated serine/threonine kinase
FDX1 ferredoxin 1
FDXR ferredoxin reductase
FECH ferrochelatase
FH fumarate hydratase
FHL2 four and a half LIM domains 2
FHL3 four and a half LIM domains 3
FIBP fibroblast growth factor (acidic) intracellular binding protein
FIS1 fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae)
FKBP8 FK506 binding protein 8, 38kDa
FOXRED1 FAD-dependent oxidoreductase domain containing 1
FPGS folylpolyglutamate synthase
FUNDC2 FUN14 domain containing 2
FXN frataxin
GATM glycine amidinotransferase (L-arginine:glycine amidinotransferase)
GBAS glioblastoma amplified sequence
GCAT glycine C-acetyltransferase
GCDH glutaryl-CoA dehydrogenase
GCK glucokinase (hexokinase 4)
GFER growth factor, augmenter of liver regeneration
GFM1 G elongation factor, mitochondrial 1
GFM2 G elongation factor, mitochondrial 2
GHITM growth hormone inducible transmembrane protein
GIMAP5 GTPase, IMAP family member 5
GK glycerol kinase
GK2 glycerol kinase 2
GLRX2 glutaredoxin 2
GLRX5 glutaredoxin 5
GLS2 glutaminase 2 (liver, mitochondrial)
GLUD2 glutamate dehydrogenase 2
GLUL glutamate-ammonia ligase
GLYAT glycine-N-acyltransferase
GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial
GPAM glycerol-3-phosphate acyltransferase, mitochondrial
GPD2 glycerol-3-phosphate dehydrogenase 2 (mitochondrial)
GPT glutamic-pyruvate transaminase (alanine aminotransferase)
GPT2 glutamic pyruvate transaminase (alanine aminotransferase) 2
GRB10 growth factor receptor-bound protein 10
GRK4 G protein-coupled receptor kinase 4
GRPEL1 GrpE-like 1, mitochondrial (E. coli)
GRPEL2 GrpE-like 2, mitochondrial (E. coli)
GSN gelsolin
GSR glutathione reductase
GSTA4 glutathione S-transferase alpha 4
GSTK1 glutathione S-transferase kappa 1
GSTZ1 glutathione S-transferase zeta 1
GUK1 guanylate kinase 1
HADHA hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit
HAGH hydroxyacylglutathione hydrolase
HAP1 huntingtin-associated protein 1
HARS2 histidyl-tRNA synthetase 2, mitochondrial
HAX1 HCLS1 associated protein X-1
HIBADH 3-hydroxyisobutyrate dehydrogenase
HIGD1A HIG1 hypoxia inducible domain family, member 1A
HINT2 histidine triad nucleotide binding protein 2
HK2 hexokinase 2
HLCS holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)
HMGCL 3-hydroxymethyl-3-methylglutaryl-CoA lyase
HMGCS2 3-hydroxy-3-methylglutaryl-CoA synthase 2 (mitochondrial)
HMMR hyaluronan-mediated motility receptor (RHAMM)
HNRNPK heterogeneous nuclear ribonucleoprotein K
HRAS Harvey rat sarcoma viral oncogene homolog
HRSP12 heat-responsive protein 12
HSCB HscB mitochondrial iron-sulfur cluster co-chaperone
HSD17B2 hydroxysteroid (17-beta) dehydrogenase 2
HSD17B4 hydroxysteroid (17-beta) dehydrogenase 4
HSD3B1 hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 1
HSD3B2 hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 2
HSP90AB1 heat shock protein 90kDa alpha (cytosolic), class B member 1
HSPA9 heat shock 70kDa protein 9 (mortalin)
HSPD1 heat shock 60kDa protein 1 (chaperonin)
HTRA2 HtrA serine peptidase 2
IARS isoleucyl-tRNA synthetase
IARS2 isoleucyl-tRNA synthetase 2, mitochondrial
IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial
IDH3A isocitrate dehydrogenase 3 (NAD+) alpha
IDH3B isocitrate dehydrogenase 3 (NAD+) beta
IDH3G isocitrate dehydrogenase 3 (NAD+) gamma
IFI6 interferon, alpha-inducible protein 6
IMMT inner membrane protein, mitochondrial
INMT indolethylamine N-methyltransferase
INPP5B inositol polyphosphate-5-phosphatase, 75kDa
IP6K2 inositol hexakisphosphate kinase 2
IQCE IQ motif containing E
IQUB IQ motif and ubiquitin domain containing
IRAK1 interleukin-1 receptor-associated kinase 1
ISCA1 iron-sulfur cluster assembly 1
ISCU iron-sulfur cluster assembly enzyme
ISY1-RAB43 ISY1-RAB43 readthrough
IVD isovaleryl-CoA dehydrogenase
KCNJ11 potassium channel, inwardly rectifying subfamily J, member 11
KCNJ8 potassium channel, inwardly rectifying subfamily J, member 8
KIAA0101 KIAA0101
KIAA1683 KIAA1683
KIF1B kinesin family member 1B
KIF5A kinesin family member 5A
KIF5B kinesin family member 5B
KMO kynurenine 3-monooxygenase (kynurenine 3-hydroxylase)
KRAS Kirsten rat sarcoma viral oncogene homolog
KRT8 keratin 8, type II
L2HGDH L-2-hydroxyglutarate dehydrogenase
LACTB lactamase, beta
LAP3 leucine aminopeptidase 3
LCLAT1 lysocardiolipin acyltransferase 1
LDHD lactate dehydrogenase D
LETM1 leucine zipper-EF-hand containing transmembrane protein 1
LIAS lipoic acid synthetase
LIG3 ligase III, DNA, ATP-dependent
LIPT1 lipoyltransferase 1
LONP1 lon peptidase 1, mitochondrial
MAATS1 MYCBP-associated, testis expressed 1
MAL mal, T-cell differentiation protein
MAOA monoamine oxidase A
MAOB monoamine oxidase B
MARC2 mitochondrial amidoxime reducing component 2
MCAT malonyl CoA:ACP acyltransferase (mitochondrial)
MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta)
MCL1 myeloid cell leukemia 1
MDH2 malate dehydrogenase 2, NAD (mitochondrial)
ME2 malic enzyme 2, NAD(+)-dependent, mitochondrial
ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial
MECR mitochondrial trans-2-enoyl-CoA reductase
METAP1D methionyl aminopeptidase type 1D (mitochondrial)
MFN1 mitofusin 1
MFN2 mitofusin 2
MGST1 microsomal glutathione S-transferase 1
MIEF1 mitochondrial elongation factor 1
MIPEP mitochondrial intermediate peptidase
MLYCD malonyl-CoA decarboxylase
MMADHC methylmalonic aciduria (cobalamin deficiency) cblD type, with homocystinuria
MPC2 mitochondrial pyruvate carrier 2
MRPL1 mitochondrial ribosomal protein L1
MRPL10 mitochondrial ribosomal protein L10
MRPL11 mitochondrial ribosomal protein L11
MRPL12 mitochondrial ribosomal protein L12
MRPL13 mitochondrial ribosomal protein L13
MRPL14 mitochondrial ribosomal protein L14
MRPL15 mitochondrial ribosomal protein L15
MRPL16 mitochondrial ribosomal protein L16
MRPL17 mitochondrial ribosomal protein L17
MRPL18 mitochondrial ribosomal protein L18
MRPL2 mitochondrial ribosomal protein L2
MRPL21 mitochondrial ribosomal protein L21
MRPL22 mitochondrial ribosomal protein L22
MRPL24 mitochondrial ribosomal protein L24
MRPL27 mitochondrial ribosomal protein L27
MRPL28 mitochondrial ribosomal protein L28
MRPL3 mitochondrial ribosomal protein L3
MRPL30 mitochondrial ribosomal protein L30
MRPL32 mitochondrial ribosomal protein L32
MRPL34 mitochondrial ribosomal protein L34
MRPL35 mitochondrial ribosomal protein L35
MRPL36 mitochondrial ribosomal protein L36
MRPL37 mitochondrial ribosomal protein L37
MRPL38 mitochondrial ribosomal protein L38
MRPL39 mitochondrial ribosomal protein L39
MRPL4 mitochondrial ribosomal protein L4
MRPL40 mitochondrial ribosomal protein L40
MRPL41 mitochondrial ribosomal protein L41
MRPL42 mitochondrial ribosomal protein L42
MRPL43 mitochondrial ribosomal protein L43
MRPL44 mitochondrial ribosomal protein L44
MRPL45 mitochondrial ribosomal protein L45
MRPL46 mitochondrial ribosomal protein L46
MRPL47 mitochondrial ribosomal protein L47
MRPL48 mitochondrial ribosomal protein L48
MRPL49 mitochondrial ribosomal protein L49
MRPL50 mitochondrial ribosomal protein L50
MRPL51 mitochondrial ribosomal protein L51
MRPL52 mitochondrial ribosomal protein L52
MRPL53 mitochondrial ribosomal protein L53
MRPL54 mitochondrial ribosomal protein L54
MRPL55 mitochondrial ribosomal protein L55
MRPL57 mitochondrial ribosomal protein L57
MRPL9 mitochondrial ribosomal protein L9
MRPS11 mitochondrial ribosomal protein S11
MRPS12 mitochondrial ribosomal protein S12
MRPS14 mitochondrial ribosomal protein S14
MRPS15 mitochondrial ribosomal protein S15
MRPS16 mitochondrial ribosomal protein S16
MRPS17 mitochondrial ribosomal protein S17
MRPS18C mitochondrial ribosomal protein S18C
MRPS2 mitochondrial ribosomal protein S2
MRPS21 mitochondrial ribosomal protein S21
MRPS23 mitochondrial ribosomal protein S23
MRPS24 mitochondrial ribosomal protein S24
MRPS25 mitochondrial ribosomal protein S25
MRPS26 mitochondrial ribosomal protein S26
MRPS27 mitochondrial ribosomal protein S27
MRPS30 mitochondrial ribosomal protein S30
MRPS31 mitochondrial ribosomal protein S31
MRPS33 mitochondrial ribosomal protein S33
MRPS34 mitochondrial ribosomal protein S34
MRPS35 mitochondrial ribosomal protein S35
MRPS36 mitochondrial ribosomal protein S36
MRPS5 mitochondrial ribosomal protein S5
MRPS6 mitochondrial ribosomal protein S6
MRPS9 mitochondrial ribosomal protein S9
MRRF mitochondrial ribosome recycling factor
MRS2 MRS2 magnesium transporter
MSRA methionine sulfoxide reductase A
MSRB3 methionine sulfoxide reductase B3
MT-ND4L NADH dehydrogenase, subunit 4L (complex I)
MT1A metallothionein 1A
MT3 metallothionein 3
MTCH1 mitochondrial carrier 1
MTCP1 mature T-cell proliferation 1
MTERF1 mitochondrial transcription termination factor 1
MTFMT mitochondrial methionyl-tRNA formyltransferase
MTFP1 mitochondrial fission process 1
MTFR1 mitochondrial fission regulator 1
MTG2 mitochondrial ribosome-associated GTPase 2
MTHFD1L methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like
MTHFD2 methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase
MTHFS 5,10-methenyltetrahydrofolate synthetase (5-formyltetrahydrofolate cyclo-ligase)
MTIF2 mitochondrial translational initiation factor 2
MTIF3 mitochondrial translational initiation factor 3
MTO1 mitochondrial tRNA translation optimization 1
MTOR mechanistic target of rapamycin (serine/threonine kinase)
MTPAP mitochondrial poly(A) polymerase
MTRF1 mitochondrial translational release factor 1
MTRF1L mitochondrial translational release factor 1-like
MTX1 metaxin 1
MTX2 metaxin 2
MUC1 mucin 1, cell surface associated
MUL1 mitochondrial E3 ubiquitin protein ligase 1
MUTYH mutY homolog
MYCBP MYC binding protein
MYL10 myosin, light chain 10, regulatory
NAGS N-acetylglutamate synthase
NAPG N-ethylmaleimide-sensitive factor attachment protein, gamma
NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
NDUFA11 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa
NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
NDUFA4 NDUFA4, mitochondrial complex associated
NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5
NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa
NDUFA7 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDa
NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1
NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3
NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa
NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa
NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa
NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa
NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)
NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)
NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
NDUFV2 NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa
NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa
NEIL2 nei endonuclease VIII-like 2 (E. coli)
NFKB1 nuclear factor of kappa light polypeptide gene enhancer in B-cells 1
NFKBIA nuclear factor of kappa light polypeptide gene enhancer in B-cells inhibitor, alpha
NFS1 NFS1 cysteine desulfurase
NFU1 NFU1 iron-sulfur cluster scaffold
NLN neurolysin (metallopeptidase M3 family)
NME3 NME/NM23 nucleoside diphosphate kinase 3
NME4 NME/NM23 nucleoside diphosphate kinase 4
NME8 NME/NM23 family member 8
NMNAT3 nicotinamide nucleotide adenylyltransferase 3
NNT nicotinamide nucleotide transhydrogenase
NPEPPS aminopeptidase puromycin sensitive
NQO1 NAD(P)H dehydrogenase, quinone 1
NR3C1 nuclear receptor subfamily 3, group C, member 1 (glucocorticoid receptor)
NR4A1 nuclear receptor subfamily 4, group A, member 1
NT5C3A 5'-nucleotidase, cytosolic IIIA
NT5M 5',3'-nucleotidase, mitochondrial
NTHL1 nth endonuclease III-like 1 (E. coli)
NUDT6 nudix (nucleoside diphosphate linked moiety X)-type motif 6
NUDT9 nudix (nucleoside diphosphate linked moiety X)-type motif 9
OAS1 2'-5'-oligoadenylate synthetase 1, 40/46kDa
OAS2 2'-5'-oligoadenylate synthetase 2, 69/71kDa
OAT ornithine aminotransferase
OGDH oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
OGG1 8-oxoguanine DNA glycosylase
OGT O-linked N-acetylglucosamine (GlcNAc) transferase
OPA1 optic atrophy 1 (autosomal dominant)
OPA3 optic atrophy 3 (autosomal recessive, with chorea and spastic paraplegia)
OTC ornithine carbamoyltransferase
OXA1L oxidase (cytochrome c) assembly 1-like
OXCT1 3-oxoacid CoA transferase 1
OXCT2 3-oxoacid CoA transferase 2
OXR1 oxidation resistance 1
OXSM 3-oxoacyl-ACP synthase, mitochondrial
PACS2 phosphofurin acidic cluster sorting protein 2
PAK7 p21 protein (Cdc42/Rac)-activated kinase 7
PAM16 presequence translocase-associated motor 16 homolog (S. cerevisiae)
PARK7 parkinson protein 7
PARL presenilin associated, rhomboid-like
PC pyruvate carboxylase
PCCA propionyl CoA carboxylase, alpha polypeptide
PCK2 phosphoenolpyruvate carboxykinase 2 (mitochondrial)
PDE3A phosphodiesterase 3A, cGMP-inhibited
PDHA1 pyruvate dehydrogenase (lipoamide) alpha 1
PDHA2 pyruvate dehydrogenase (lipoamide) alpha 2
PDHX pyruvate dehydrogenase complex, component X
PDK1 pyruvate dehydrogenase kinase, isozyme 1
PDK3 pyruvate dehydrogenase kinase, isozyme 3
PDK4 pyruvate dehydrogenase kinase, isozyme 4
PDP1 pyruvate dehyrogenase phosphatase catalytic subunit 1
PDP2 pyruvate dehyrogenase phosphatase catalytic subunit 2
PDPR pyruvate dehydrogenase phosphatase regulatory subunit
PDSS1 prenyl (decaprenyl) diphosphate synthase, subunit 1
PDSS2 prenyl (decaprenyl) diphosphate synthase, subunit 2
PEMT phosphatidylethanolamine N-methyltransferase
PFKFB2 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 2
PHB prohibitin
PHLPP1 PH domain and leucine rich repeat protein phosphatase 1
PHYHIPL phytanoyl-CoA 2-hydroxylase interacting protein-like
PHYKPL 5-phosphohydroxy-L-lysine phospho-lyase
PI4KB phosphatidylinositol 4-kinase, catalytic, beta
PIN4 peptidylprolyl cis/trans isomerase, NIMA-interacting 4
PISD phosphatidylserine decarboxylase
PLA2G15 phospholipase A2, group XV
PLSCR3 phospholipid scramblase 3
PMAIP1 phorbol-12-myristate-13-acetate-induced protein 1
PMPCA peptidase (mitochondrial processing) alpha
PNPLA6 patatin-like phospholipase domain containing 6
POLDIP2 polymerase (DNA-directed), delta interacting protein 2
POLG polymerase (DNA directed), gamma
POLG2 polymerase (DNA directed), gamma 2, accessory subunit
POLRMT polymerase (RNA) mitochondrial (DNA directed)
PPA1 pyrophosphatase (inorganic) 1
PPA2 pyrophosphatase (inorganic) 2
PPIF peptidylprolyl isomerase F
PPL periplakin
PPM1K protein phosphatase, Mg2+/Mn2+ dependent, 1K
PRDX3 peroxiredoxin 3
PRDX5 peroxiredoxin 5
PREP prolyl endopeptidase
PRKCD protein kinase C, delta
PRKD1 protein kinase D1
PTDSS2 phosphatidylserine synthase 2
PTGES2 prostaglandin E synthase 2
PTPN21 protein tyrosine phosphatase, non-receptor type 21
PTRH2 peptidyl-tRNA hydrolase 2
PTS 6-pyruvoyltetrahydropterin synthase
PUS1 pseudouridylate synthase 1
PYCR1 pyrroline-5-carboxylate reductase 1
RAB11FIP5 RAB11 family interacting protein 5 (class I)
RAB31 RAB31, member RAS oncogene family
RAB3GAP2 RAB3 GTPase activating protein subunit 2 (non-catalytic)
RAB43 RAB43, member RAS oncogene family
RAN RAN, member RAS oncogene family
RAPGEF3 Rap guanine nucleotide exchange factor (GEF) 3
RBM12 RNA binding motif protein 12
RBP2 retinol binding protein 2, cellular
RD3 retinal degeneration 3
RGL4 ral guanine nucleotide dissociation stimulator-like 4
RHOT1 ras homolog family member T1
RHOT2 ras homolog family member T2
RIPK3 receptor-interacting serine-threonine kinase 3
RNASEH1 ribonuclease H1
RNF130 ring finger protein 130
RTN4IP1 reticulon 4 interacting protein 1
SARS seryl-tRNA synthetase
SCD stearoyl-CoA desaturase (delta-9-desaturase)
SCO2 SCO2 cytochrome c oxidase assembly protein
SCP2 sterol carrier protein 2
SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa
SECISBP2 SECIS binding protein 2
SEPT4 septin 4
SFXN1 sideroflexin 1
SFXN3 sideroflexin 3
SH3BP5 SH3-domain binding protein 5 (BTK-associated)
SIRT3 sirtuin 3
SIRT5 sirtuin 5
SIVA1 SIVA1, apoptosis-inducing factor
SLC16A1 solute carrier family 16 (monocarboxylate transporter), member 1
SLC25A1 solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1
SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11
SLC25A13 solute carrier family 25 (aspartate/glutamate carrier), member 13
SLC25A14 solute carrier family 25 (mitochondrial carrier, brain), member 14
SLC25A15 solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15
SLC25A16 solute carrier family 25 (mitochondrial carrier), member 16
SLC25A18 solute carrier family 25 (glutamate carrier), member 18
SLC25A2 solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 2
SLC25A20 solute carrier family 25 (carnitine/acylcarnitine translocase), member 20
SLC25A21 solute carrier family 25 (mitochondrial oxoadipate carrier), member 21
SLC25A22 solute carrier family 25 (mitochondrial carrier: glutamate), member 22
SLC25A23 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 23
SLC25A25 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 25
SLC25A29 solute carrier family 25 (mitochondrial carnitine/acylcarnitine carrier), member 29
SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3
SLC25A30 solute carrier family 25, member 30
SLC25A31 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 31
SLC25A35 solute carrier family 25, member 35
SLC25A37 solute carrier family 25 (mitochondrial iron transporter), member 37
SLC25A38P1 solute carrier family 25, member 38 pseudogene 1
SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
SLC25A40 solute carrier family 25, member 40
SLC25A46 solute carrier family 25, member 46
SLC25A47 solute carrier family 25, member 47
SLC25A5 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5
SLC25A52 solute carrier family 25, member 52
SLC25A53 solute carrier family 25, member 53
SLC9A6 solute carrier family 9, subfamily A (NHE6, cation proton antiporter 6), member 6
SLIT3 slit homolog 3 (Drosophila)
SMAD5 SMAD family member 5
SNN stannin
SOD2 superoxide dismutase 2, mitochondrial
SPATA5 spermatogenesis associated 5
SPG7 spastic paraplegia 7 (pure and complicated autosomal recessive)
SPNS1 spinster homolog 1 (Drosophila)
SQRDL sulfide quinone reductase-like (yeast)
SSBP1 single-stranded DNA binding protein 1, mitochondrial
STAM signal transducing adaptor molecule (SH3 domain and ITAM motif) 1
STAR steroidogenic acute regulatory protein
STAT3 signal transducer and activator of transcription 3 (acute-phase response factor)
STK11 serine/threonine kinase 11
SUOX sulfite oxidase
SURF1 surfeit 1
SYNJ2 synaptojanin 2
SYNJ2BP synaptojanin 2 binding protein
TAZ tafazzin
TBRG4 transforming growth factor beta regulator 4
TCAIM T cell activation inhibitor, mitochondrial
TDRD7 tudor domain containing 7
TERT telomerase reverse transcriptase
TFAM transcription factor A, mitochondrial
TFB1M transcription factor B1, mitochondrial
TFB2M transcription factor B2, mitochondrial
THG1L tRNA-histidine guanylyltransferase 1-like (S. cerevisiae)
TIMM10B translocase of inner mitochondrial membrane 10 homolog B (yeast)
TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast)
TIMM17A translocase of inner mitochondrial membrane 17 homolog A (yeast)
TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast)
TIMM21 translocase of inner mitochondrial membrane 21 homolog (yeast)
TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast)
TIMM23 translocase of inner mitochondrial membrane 23 homolog (yeast)
TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast)
TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae)
TIMM8A translocase of inner mitochondrial membrane 8 homolog A (yeast)
TIMM9 translocase of inner mitochondrial membrane 9 homolog (yeast)
TIMMDC1 translocase of inner mitochondrial membrane domain containing 1
TK2 thymidine kinase 2, mitochondrial
TMEM126A transmembrane protein 126A
TMEM143 transmembrane protein 143
TMEM14B transmembrane protein 14B
TMEM14D transmembrane protein 14D (pseudogene)
TMEM186 transmembrane protein 186
TMEM243 transmembrane protein 243, mitochondrial
TMEM91 transmembrane protein 91
TMLHE trimethyllysine hydroxylase, epsilon
TOMM20 translocase of outer mitochondrial membrane 20 homolog (yeast)
TOMM22 translocase of outer mitochondrial membrane 22 homolog (yeast)
TOMM34 translocase of outer mitochondrial membrane 34
TOMM7 translocase of outer mitochondrial membrane 7 homolog (yeast)
TOMM70A translocase of outer mitochondrial membrane 70 homolog A (S. cerevisiae)
TOP1MT topoisomerase (DNA) I, mitochondrial
TOP3A topoisomerase (DNA) III alpha
TP53 tumor protein p53
TRAP1 TNF receptor-associated protein 1
TRMT1 tRNA methyltransferase 1 homolog (S. cerevisiae)
TRMU tRNA 5-methylaminomethyl-2-thiouridylate methyltransferase
TRNT1 tRNA nucleotidyl transferase, CCA-adding, 1
TSFM Ts translation elongation factor, mitochondrial
TSHZ3 teashirt zinc finger homeobox 3
TSPO translocator protein (18kDa)
TST thiosulfate sulfurtransferase (rhodanese)
TUBA1B tubulin, alpha 1b
TUFM Tu translation elongation factor, mitochondrial
TXN thioredoxin
TXN2 thioredoxin 2
TXNRD2 thioredoxin reductase 2
TYMS thymidylate synthetase
UCP1 uncoupling protein 1 (mitochondrial, proton carrier)
UCP2 uncoupling protein 2 (mitochondrial, proton carrier)
UCP3 uncoupling protein 3 (mitochondrial, proton carrier)
UNG uracil-DNA glycosylase
UQCC1 ubiquinol-cytochrome c reductase complex assembly factor 1
UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI
UQCRC2 ubiquinol-cytochrome c reductase core protein II
UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
VAMP1 vesicle-associated membrane protein 1 (synaptobrevin 1)
VDAC1 voltage-dependent anion channel 1
VDAC2 voltage-dependent anion channel 2
VDAC3 voltage-dependent anion channel 3
VHL von Hippel-Lindau tumor suppressor, E3 ubiquitin protein ligase
WARS2 tryptophanyl tRNA synthetase 2, mitochondrial
WBSCR16 Williams-Beuren syndrome chromosome region 16
WWOX WW domain containing oxidoreductase
XPNPEP3 X-prolyl aminopeptidase 3, mitochondrial
YARS2 tyrosyl-tRNA synthetase 2, mitochondrial
YME1L1 YME1-like 1 ATPase
ZNF713 zinc finger protein 713