Symbol |
Name |
ABCB10
|
ATP-binding cassette, sub-family B (MDR/TAP), member 10
|
ABCB7
|
ATP-binding cassette, sub-family B (MDR/TAP), member 7
|
ABCB8
|
ATP-binding cassette, sub-family B (MDR/TAP), member 8
|
ACAA2
|
acetyl-CoA acyltransferase 2
|
ACADVL
|
acyl-CoA dehydrogenase, very long chain
|
ALDH18A1
|
aldehyde dehydrogenase 18 family, member A1
|
COX4I1
|
cytochrome c oxidase subunit IV isoform 1
|
COX6A2
|
cytochrome c oxidase subunit VIa polypeptide 2
|
COX6C
|
cytochrome c oxidase subunit VIc
|
COX7A2
|
cytochrome c oxidase subunit VIIa polypeptide 2 (liver)
|
CRAT
|
carnitine O-acetyltransferase
|
DHODH
|
dihydroorotate dehydrogenase (quinone)
|
ECI1
|
enoyl-CoA delta isomerase 1
|
FECH
|
ferrochelatase
|
GCAT
|
glycine C-acetyltransferase
|
LETM1
|
leucine zipper-EF-hand containing transmembrane protein 1
|
NDUFA11
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa
|
NDUFA5
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5
|
NDUFA6
|
NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa
|
NDUFB1
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa
|
NDUFB5
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa
|
NDUFB7
|
NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa
|
NDUFV3
|
NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa
|
OPA1
|
optic atrophy 1 (autosomal dominant)
|
PDE3A
|
phosphodiesterase 3A, cGMP-inhibited
|
PHB
|
prohibitin
|
SDHC
|
succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa
|
SLC25A16
|
solute carrier family 25 (mitochondrial carrier), member 16
|
SLC25A2
|
solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 2
|
SLC25A20
|
solute carrier family 25 (carnitine/acylcarnitine translocase), member 20
|
SLC25A21
|
solute carrier family 25 (mitochondrial oxoadipate carrier), member 21
|
SLC25A29
|
solute carrier family 25 (mitochondrial carnitine/acylcarnitine carrier), member 29
|
SLC25A3
|
solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3
|
SLC25A30
|
solute carrier family 25, member 30
|
SLC25A35
|
solute carrier family 25, member 35
|
SLC25A38P1
|
solute carrier family 25, member 38 pseudogene 1
|
SLC25A4
|
solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
|
SLC25A46
|
solute carrier family 25, member 46
|
SLC25A47
|
solute carrier family 25, member 47
|
SLC25A53
|
solute carrier family 25, member 53
|
SPATA5
|
spermatogenesis associated 5
|
SQRDL
|
sulfide quinone reductase-like (yeast)
|
TIMM13
|
translocase of inner mitochondrial membrane 13 homolog (yeast)
|
TIMM17A
|
translocase of inner mitochondrial membrane 17 homolog A (yeast)
|
UCP3
|
uncoupling protein 3 (mitochondrial, proton carrier)
|
UQCRFS1
|
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
|