| Name | Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial |
| Description | Biotin-attachment subunit of the 3-methylcrotonyl-CoA carboxylase, an enzyme that catalyzes the conversion of 3-methylcrotonyl-CoA to 3-methylglutaconyl-CoA, a critical step for leucine and isovaleric acid catabolism. |
| UniProt ID | Q96RQ3 |
| Gene | MCCC1 |
