Name | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial |
Description | The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). |
UniProt ID | P21953 |
Gene | BCKDHB |