Name

IVD Gene

isovaleryl-CoA dehydrogenase

Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Aug 2017]

Isovaleryl-CoA Gene Set

From HMDB Metabolites of Enzymes

interacting proteins for the Isovaleryl-CoA metabolite from the curated HMDB Metabolites of Enzymes dataset.