Name

TRN-GTT8-1 Gene

transfer RNA-Asn (GTT) 8-1

TRN-GTT17-1 Gene

transfer RNA-Asn (GTT) 17-1

TRN-GTT14-1 Gene

transfer RNA-Asn (GTT) 14-1

TRN-GTT9-2 Gene

transfer RNA-Asn (GTT) 9-2

TRN-GTT11-2 Gene

transfer RNA-Asn (GTT) 11-2

TRN-GTT11-1 Gene

transfer RNA-Asn (GTT) 11-1

TRN-GTT10-1 Gene

transfer RNA-Asn (GTT) 10-1

TRN-GTT6-1 Gene

transfer RNA-Asn (GTT) 6-1

TRN-GTT7-1 Gene

transfer RNA-Asn (GTT) 7-1

TRN-GTT22-1 Gene

transfer RNA-Asn (GTT) 22-1

TRN-GTT16-1 Gene

transfer RNA-Asn (GTT) 16-1

TRN-GTT16-3 Gene

transfer RNA-Asn (GTT) 16-3

TRN-GTT16-2 Gene

transfer RNA-Asn (GTT) 16-2

TRN-GTT16-5 Gene

transfer RNA-Asn (GTT) 16-5

TRN-GTT16-4 Gene

transfer RNA-Asn (GTT) 16-4

TRN-ATT1-2 Gene

transfer RNA-Asn (ATT) 1-2

TRN-GTT20-1 Gene

transfer RNA-Asn (GTT) 20-1

TRN-GTT21-1 Gene

transfer RNA-Asn (GTT) 21-1

TRN-ATT1-1 Gene

transfer RNA-Asn (ATT) 1-1

TRN-GTT2-6 Gene

transfer RNA-Asn (GTT) 2-6

TRN-GTT2-5 Gene

transfer RNA-Asn (GTT) 2-5

TRN-GTT2-4 Gene

transfer RNA-Asn (GTT) 2-4

TRN-GTT2-3 Gene

transfer RNA-Asn (GTT) 2-3

TRN-GTT2-2 Gene

transfer RNA-Asn (GTT) 2-2

TRN-GTT2-1 Gene

transfer RNA-Asn (GTT) 2-1

The saturation hybridization studies of Hatlen and Attardi (1971) [PubMed 4929578] indicated a copy number of tRNA genes of 1,300 for the haploid human genome--an average of 65 gene copies for each tRNA species. These genes tend to be clustered, an arrangement that would facilitate the exchange of sequence information and enable them to evolve together.[supplied by OMIM, Sep 2009]

TRN-GTT3-2 Gene

transfer RNA-Asn (GTT) 3-2

TRN-GTT3-1 Gene

transfer RNA-Asn (GTT) 3-1

TRN-GTT9-1 Gene

transfer RNA-Asn (GTT) 9-1

TRN-GTT13-1 Gene

transfer RNA-Asn (GTT) 13-1

TRN-GTT12-1 Gene

transfer RNA-Asn (GTT) 12-1

TRN-GTT4-1 Gene

transfer RNA-Asn (GTT) 4-1

TRN-GTT19-1 Gene

transfer RNA-Asn (GTT) 19-1

TRN-GTT18-1 Gene

transfer RNA-Asn (GTT) 18-1

TRN-GTT1-1 Gene

transfer RNA-Asn (GTT) 1-1

TRN-GTT5-1 Gene

transfer RNA-Asn (GTT) 5-1

TRN-GTT15-1 Gene

transfer RNA-Asn (GTT) 15-1

TRN-GTT23-1 Gene

transfer RNA-Asn (GTT) 23-1

TRQ-CTG8-2 Gene

transfer RNA-Gln (CTG) 8-2

TRQ-CTG18-1 Gene

transfer RNA-Gln (CTG) 18-1

TRQ-CTG1-5 Gene

transfer RNA-Gln (CTG) 1-5

TRQ-CTG9-1 Gene

transfer RNA-Gln (CTG) 9-1

TRQ-CTG15-1 Gene

transfer RNA-Gln (CTG) 15-1

NMTRQ-TTG8-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 8-1

TRQ-CTG14-1 Gene

transfer RNA-Gln (CTG) 14-1

NMTRQ-TTG2-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 2-1

NMTRQ-TTG3-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 3-1

NMTRQ-TTG12-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 12-1

TRQ-TTG8-1 Gene

transfer RNA-Gln (TTG) 8-1

NMTRQ-TTG6-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 6-1

NMTRQ-TTG13-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 13-1

TRQ-CTG4-1 Gene

transfer RNA-Gln (CTG) 4-1

TRQ-CTG4-2 Gene

transfer RNA-Gln (CTG) 4-2

NMTRQ-TTG7-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 7-1

TRQ-CTG3-2 Gene

transfer RNA-Gln (CTG) 3-2

TRQ-CTG1-4 Gene

transfer RNA-Gln (CTG) 1-4

TRQ-CTG1-1 Gene

transfer RNA-Gln (CTG) 1-1

TRQ-CTG1-2 Gene

transfer RNA-Gln (CTG) 1-2

TRQ-CTG1-3 Gene

transfer RNA-Gln (CTG) 1-3

TRQ-TTG3-3 Gene

transfer RNA-Gln (TTG) 3-3

TRQ-TTG3-2 Gene

transfer RNA-Gln (TTG) 3-2

TRQ-TTG3-1 Gene

transfer RNA-Gln (TTG) 3-1

TRQ-TTG2-1 Gene

transfer RNA-Gln (TTG) 2-1

TRQ-CTG5-1 Gene

transfer RNA-Gln (CTG) 5-1

GATB Gene

glutamyl-tRNA(Gln) amidotransferase, subunit B

Contributes to glutaminyl-tRNA synthase (glutamine-hydrolyzing) activity. Involved in glutaminyl-tRNAGln biosynthesis via transamidation and mitochondrial translation. Located in mitochondrion. Part of glutamyl-tRNA(Gln) amidotransferase complex. Implicated in combined oxidative phosphorylation deficiency 41. [provided by Alliance of Genome Resources, Mar 2025]

GATC Gene

glutamyl-tRNA(Gln) amidotransferase, subunit C

Predicted to enable ATP binding activity and glutaminyl-tRNA synthase (glutamine-hydrolyzing) activity. Involved in glutaminyl-tRNAGln biosynthesis via transamidation and mitochondrial translation. Located in mitochondrion. Part of glutamyl-tRNA(Gln) amidotransferase complex. Implicated in combined oxidative phosphorylation deficiency 42. [provided by Alliance of Genome Resources, Mar 2025]

NMTRQ-TTG11-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 11-1

NMTRQ-TTG10-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 10-1

TRQ-CTG17-1 Gene

transfer RNA-Gln (CTG) 17-1

NMTRQ-TTG9-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 9-1

TRQ-CTG16-1 Gene

transfer RNA-Gln (CTG) 16-1

TRQ-TTG7-1 Gene

transfer RNA-Gln (TTG) 7-1

TRQ-TTG6-1 Gene

transfer RNA-Gln (TTG) 6-1

TRQ-CTG13-1 Gene

transfer RNA-Gln (CTG) 13-1

TRQ-CTG11-1 Gene

transfer RNA-Gln (CTG) 11-1

TRQ-CTG10-1 Gene

transfer RNA-Gln (CTG) 10-1

TRQ-CTG12-1 Gene

transfer RNA-Gln (CTG) 12-1

TRQ-CTG8-1 Gene

transfer RNA-Gln (CTG) 8-1

NMTRQ-TTG1-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 1-1

NMTRQ-TTG15-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 15-1

TRQ-CTG7-1 Gene

transfer RNA-Gln (CTG) 7-1

TRQ-TTG1-1 Gene

transfer RNA-Gln (TTG) 1-1

Mammalian cells contain at least 2 species of glutamine tRNA, the Gln(CUG) form (TRQ1; MIM 189919) and the Gln(UUG) form. Nemoto et al. (1991) [PubMed 2041751] reported the nucleotide sequence of the human tRNA(Gln/UUG) gene. In a correction, Nemoto et al. (1991) [PubMed 2041751] stated that the gene involved should have been designated tRNA-GLN/U*UG, where U* is a derivative of U.[supplied by OMIM, Sep 2009]

NMTRQ-TTG14-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 14-1

TRQ-CTG2-1 Gene

transfer RNA-Gln (CTG) 2-1

TRQ-CTG3-1 Gene

transfer RNA-Gln (CTG) 3-1

TRQ-TTG5-1 Gene

transfer RNA-Gln (TTG) 5-1

TRQ-CTG6-1 Gene

transfer RNA-Gln (CTG) 6-1

TRQ-TTG9-1 Gene

transfer RNA-Gln (TTG) 9-1

TRQ-TTG4-1 Gene

transfer RNA-Gln (TTG) 4-1

NMTRQ-CTG1-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (CTG) 1-1

TRQ-TTG10-1 Gene

transfer RNA-Gln (TTG) 10-1

NMTRQ-TTG4-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 4-1

NMTRQ-TTG5-1 Gene

nuclear-encoded mitochondrial transfer RNA-Gln (TTG) 5-1